Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature

Detalhes bibliográficos
Autor(a) principal: Mesquita, RD
Data de Publicação: 2018
Outros Autores: Sousa, M, Vilaverde, F, Cardoso, R
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10400.23/1279
Resumo: The Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic portosystemic shunts are increasingly suspected and diagnosed in specialized centres, much of their clinical presentation and natural history is not fully understood. Symptoms of portosystemic shunt are mainly caused by increased levels of ammonia, which lead to signs of encephalopathy. Therapeutic options depend on the type of shunt and its clinical course, so the classification of the congenital portosystemic shunt is a key finding in these patients.
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spelling Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literatureEncefalopatia HepáticaVeia Porta/anomalias congénitasThe Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic portosystemic shunts are increasingly suspected and diagnosed in specialized centres, much of their clinical presentation and natural history is not fully understood. Symptoms of portosystemic shunt are mainly caused by increased levels of ammonia, which lead to signs of encephalopathy. Therapeutic options depend on the type of shunt and its clinical course, so the classification of the congenital portosystemic shunt is a key finding in these patients.Repositório Científico do Hospital de BragaMesquita, RDSousa, MVilaverde, FCardoso, R2018-11-09T13:43:27Z2018-01-01T00:00:00Z2018-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.23/1279engBJR Case Rep. 2017 Nov 16;4(2):20170054.10.1259/bjrcr.20170054info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2022-09-21T09:03:11Zoai:repositorio.hospitaldebraga.pt:10400.23/1279Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T15:55:48.968368Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
title Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
spellingShingle Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
Mesquita, RD
Encefalopatia Hepática
Veia Porta/anomalias congénitas
title_short Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
title_full Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
title_fullStr Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
title_full_unstemmed Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
title_sort Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults-case report and review of the relevant literature
author Mesquita, RD
author_facet Mesquita, RD
Sousa, M
Vilaverde, F
Cardoso, R
author_role author
author2 Sousa, M
Vilaverde, F
Cardoso, R
author2_role author
author
author
dc.contributor.none.fl_str_mv Repositório Científico do Hospital de Braga
dc.contributor.author.fl_str_mv Mesquita, RD
Sousa, M
Vilaverde, F
Cardoso, R
dc.subject.por.fl_str_mv Encefalopatia Hepática
Veia Porta/anomalias congénitas
topic Encefalopatia Hepática
Veia Porta/anomalias congénitas
description The Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic portosystemic shunts are increasingly suspected and diagnosed in specialized centres, much of their clinical presentation and natural history is not fully understood. Symptoms of portosystemic shunt are mainly caused by increased levels of ammonia, which lead to signs of encephalopathy. Therapeutic options depend on the type of shunt and its clinical course, so the classification of the congenital portosystemic shunt is a key finding in these patients.
publishDate 2018
dc.date.none.fl_str_mv 2018-11-09T13:43:27Z
2018-01-01T00:00:00Z
2018-01-01T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.23/1279
url http://hdl.handle.net/10400.23/1279
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv BJR Case Rep. 2017 Nov 16;4(2):20170054.
10.1259/bjrcr.20170054
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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