A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum

Bibliographic Details
Main Author: Teixeira, Joaquim Cruz
Publication Date: 2019
Other Authors: Simão, Diogo Cardoso, Pimentel, José, Livraghi, Sérgio
Format: Article
Language: eng
Source: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Download full: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331
Summary: Fibrous dysplasia is a bone disease characterized by an osteoblastic dysfunction resulting in a fibrous replacement of the normal medullary bone. We describe the case of a 33-year-old who presented with low back pain irradiating to her right leg. Both the computed tomography scan and magnetic resonance imaging showed an osteolytic, multicystic lesion of the right hemi-sacrum with invasion of the right S1 foramen. She underwent foraminotomy and curettage of the lesion. Histological diagnosis was fibrous dysplasia, without features of malignant transformation. Three years after surgery the patient is asymptomatic and imaging is stable. This is the fifth known case of monostotic fibrous dysplasia involving the sacrum, a rare entity that must be considered in the differential diagnosis when approaching patients with sacral lesions.
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spelling A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the SacrumUm Caso Raro de Radiculopatia: Displasia Fibrosa Monostótica do SacroFibrous DysplasiaMonostoticRadiculopathySacrumDisplasia Fibrosa MonostóticaRadiculopatiaSacroFibrous dysplasia is a bone disease characterized by an osteoblastic dysfunction resulting in a fibrous replacement of the normal medullary bone. We describe the case of a 33-year-old who presented with low back pain irradiating to her right leg. Both the computed tomography scan and magnetic resonance imaging showed an osteolytic, multicystic lesion of the right hemi-sacrum with invasion of the right S1 foramen. She underwent foraminotomy and curettage of the lesion. Histological diagnosis was fibrous dysplasia, without features of malignant transformation. Three years after surgery the patient is asymptomatic and imaging is stable. This is the fifth known case of monostotic fibrous dysplasia involving the sacrum, a rare entity that must be considered in the differential diagnosis when approaching patients with sacral lesions.A displasia fibrosa é uma doença óssea caracterizada por uma disfunção osteoblástica que resulta na substituição do osso medular normal por tecido fibroso. Descrevemos o caso de uma doente de 33 anos que se apresentou com lombalgia e ciatalgia direita. A tomografia computorizada e ressonância magnética lombares revelaram uma lesão osteolítica e multiquística no hemissacro direito com invasão do foramen de S1. A doente foi submetida a foraminotomia e curetagem da lesão. O diagnóstico histológico foi de displasia fibrosa, sem sinais de transformação maligna. Três anos após a cirurgia, a doente está assintomática e os estudos de imagem apresentam estabilidade da lesão. Este é o quinto caso conhecido na literatura de displasia fibrosa monostótica com atingimento do sacro, uma entidade rara que deve ser considerada no diagnóstico diferencial de doentes com lesões do sacro.Ordem dos Médicos2019-06-28info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfapplication/vnd.openxmlformats-officedocument.wordprocessingml.documentapplication/pdfapplication/pdfapplication/mswordapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331oai:ojs.www.actamedicaportuguesa.com:article/9331Acta Médica Portuguesa; Vol. 32 No. 6 (2019): June; 466-468Acta Médica Portuguesa; Vol. 32 N.º 6 (2019): Junho; 466-4681646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/5716https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/9549https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/9552https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10697https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10698https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10716Direitos de Autor (c) 2019 Acta Médica Portuguesainfo:eu-repo/semantics/openAccessTeixeira, Joaquim CruzSimão, Diogo CardosoPimentel, JoséLivraghi, Sérgio2022-12-20T11:05:44Zoai:ojs.www.actamedicaportuguesa.com:article/9331Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:19:42.208542Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
Um Caso Raro de Radiculopatia: Displasia Fibrosa Monostótica do Sacro
title A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
spellingShingle A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
Teixeira, Joaquim Cruz
Fibrous Dysplasia
Monostotic
Radiculopathy
Sacrum
Displasia Fibrosa Monostótica
Radiculopatia
Sacro
title_short A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
title_full A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
title_fullStr A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
title_full_unstemmed A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
title_sort A Rare Case of Radiculopathy: Monostotic Fibrous Dysplasia of the Sacrum
author Teixeira, Joaquim Cruz
author_facet Teixeira, Joaquim Cruz
Simão, Diogo Cardoso
Pimentel, José
Livraghi, Sérgio
author_role author
author2 Simão, Diogo Cardoso
Pimentel, José
Livraghi, Sérgio
author2_role author
author
author
dc.contributor.author.fl_str_mv Teixeira, Joaquim Cruz
Simão, Diogo Cardoso
Pimentel, José
Livraghi, Sérgio
dc.subject.por.fl_str_mv Fibrous Dysplasia
Monostotic
Radiculopathy
Sacrum
Displasia Fibrosa Monostótica
Radiculopatia
Sacro
topic Fibrous Dysplasia
Monostotic
Radiculopathy
Sacrum
Displasia Fibrosa Monostótica
Radiculopatia
Sacro
description Fibrous dysplasia is a bone disease characterized by an osteoblastic dysfunction resulting in a fibrous replacement of the normal medullary bone. We describe the case of a 33-year-old who presented with low back pain irradiating to her right leg. Both the computed tomography scan and magnetic resonance imaging showed an osteolytic, multicystic lesion of the right hemi-sacrum with invasion of the right S1 foramen. She underwent foraminotomy and curettage of the lesion. Histological diagnosis was fibrous dysplasia, without features of malignant transformation. Three years after surgery the patient is asymptomatic and imaging is stable. This is the fifth known case of monostotic fibrous dysplasia involving the sacrum, a rare entity that must be considered in the differential diagnosis when approaching patients with sacral lesions.
publishDate 2019
dc.date.none.fl_str_mv 2019-06-28
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331
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url https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331
identifier_str_mv oai:ojs.www.actamedicaportuguesa.com:article/9331
dc.language.iso.fl_str_mv eng
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dc.relation.none.fl_str_mv https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/5716
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/9549
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/9552
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10697
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10698
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/9331/10716
dc.rights.driver.fl_str_mv Direitos de Autor (c) 2019 Acta Médica Portuguesa
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Direitos de Autor (c) 2019 Acta Médica Portuguesa
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
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application/pdf
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application/msword
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dc.publisher.none.fl_str_mv Ordem dos Médicos
publisher.none.fl_str_mv Ordem dos Médicos
dc.source.none.fl_str_mv Acta Médica Portuguesa; Vol. 32 No. 6 (2019): June; 466-468
Acta Médica Portuguesa; Vol. 32 N.º 6 (2019): Junho; 466-468
1646-0758
0870-399X
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
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