Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation

• Autor(a) principal: Gama, Mafalda
• Data de Publicação: 2023
• Outros Autores: Cardoso, Isabel, Palma Anselmo, Mónica, Aguiar Rosa, Sílvia, Gaspar da Costa, Pedro, Fortuna, Philip
• Tipo de documento: Artigo
• Idioma: eng
• Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
• Texto Completo: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/19624
• topic: Arrhythmogenic Left Ventricular Cardiomyopathy; Cardiopulmonary Resuscitation; Extracorporeal Membrane Oxygenation; Heart Arrest/therapy; Miocardiopatia Arritmogénica do Ventrículo Esquerdo; Oxigenação por Membrana Extracorporal; Paragem Cardíaca/tratamento; Ressuscitação Cardiopulmonar

A 24-year-old man suffered a witnessed cardiac arrest after a padel game. Basic life support was immediately provided. The pre-hospital emergency services team continued the resuscitation efforts, and the patient was accepted for extracorporeal cardiopulmonary resuscitation. The return of spontaneous circulation was achieved in 45 minutes. The initial assessment revealed a ST-segment elevation in leads V4-V6 and a dilated left ventricle with severe systolic dysfunction. Coronary angiography was normal. An improvement in left ventricular systolic function was observed and extracorporeal cardiac support was discontinued after 48 hours. Cardiovascular magnetic resonance imaging demonstrated hypokinesia and subepicardial fatty infiltration of the left ventricle lateral wall. Genetic testing detected a variant of uncertain significance in the ANK2 gene. The diagnosis of arrhythmogenic left ventricular myocardiopathy did not fulfill all the current diagnostic criteria, but it is a very likely diagnosis. An implantable cardioverter-defibrillator was placed. Thepatient was discharged without physical or cognitive impairment.