GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.34635/rpc.709 |
Resumo: | Gastrointestinal stromal tumors are rare tumors of the gastroistestinal tract. Less than 5% of these are not associated to the gastrointestinal tract, being designated EGISTs. EGISTs of the mesocolon are extremely rare, with just a few cases reported in the literature. We present the case of an 82-year old female presenting with nausea and vomiting for a month, having had an ultra-sound(US) and CT which showed “large tumoral formation, mainly cystic, with significant contrast uptake in the solid component, measuring 16,6x11,2 cm, apparently independent from the tail of the pancreas, in the likely dependence of the gastric wall”. Endoscopic US and FNA were perfomed but the result was inconclusive. The patient underwent exploratory laparotomy with atypical gastrectomy, excision of the anterior layer of the transverse mesocolon and omentectomy en-bloc. Histopathology report revealed ephitelioid type malignant EGIST. pT4N0. By patient will no adjuvant therapy was performed. Although rare, GISTs are the most common mesenchymal tumors of the GI tract, nevertheless EGISTs of the mesocolon are extremely rare. Contrarily to what happens with GISTs, the pathogenesis, incidence and prognosis are not fully established for EGIST since there are few cases described. We present a brief review on the diagnosis and therapeutic approach to these cases. |
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GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORTEGIST GIGANTE DO MESOCÓLON TRANSVERSO: APRESENTAÇÃO DE CASO CLÍNICOGastrointestinal stromal tumors are rare tumors of the gastroistestinal tract. Less than 5% of these are not associated to the gastrointestinal tract, being designated EGISTs. EGISTs of the mesocolon are extremely rare, with just a few cases reported in the literature. We present the case of an 82-year old female presenting with nausea and vomiting for a month, having had an ultra-sound(US) and CT which showed “large tumoral formation, mainly cystic, with significant contrast uptake in the solid component, measuring 16,6x11,2 cm, apparently independent from the tail of the pancreas, in the likely dependence of the gastric wall”. Endoscopic US and FNA were perfomed but the result was inconclusive. The patient underwent exploratory laparotomy with atypical gastrectomy, excision of the anterior layer of the transverse mesocolon and omentectomy en-bloc. Histopathology report revealed ephitelioid type malignant EGIST. pT4N0. By patient will no adjuvant therapy was performed. Although rare, GISTs are the most common mesenchymal tumors of the GI tract, nevertheless EGISTs of the mesocolon are extremely rare. Contrarily to what happens with GISTs, the pathogenesis, incidence and prognosis are not fully established for EGIST since there are few cases described. We present a brief review on the diagnosis and therapeutic approach to these cases.Os Tumores do Estroma Gastro-Intestinal (GIST) são tumores raros do tracto gastro-intestinal. Menos de 5% destes não estão associados ao tracto gastro-intestinal, sendo definidos por EGISTs. Os EGISTs do mesocólon são extremamente raros, com apenas alguns casos descritos na literatura. Apresentamos o caso de uma doente de 82 anos com quadro de náuseas e vómitos com 1 mês de evolução, tendo realizado ecografia e TC que mostrou “observa-se uma volumosa formação tumoral, em grande parte quística, com significativa toma de contraste nas áreas sólidas, que mede cerca de 16,8x11,2 cm. Esta formação é aparentemente independente da cauda do pâncreas, estando na provável dependência da parede gástrica...”, realizou eco-endoscopia com PAAF que foi inconclusiva. Foi submetida a laparotomia exploradora com gastrectomia atípica e excisão parcial do folheto anterior do mesocólon transverso e omentectomia em bloco com o tumor. A anatomia patológica revelou “Tumor do estroma extragastrointestinal maligno, do tipo epitelioide. pT4N0”. Por vontade da doente não foi realizada terapêutica adjuvante. Apesar de raros, os GISTs são os tumores mesenquimatosos mais comuns do tracto gastro-intestinal, no entanto EGISTs do mesocólon são extremamente raros. Contrariamente ao que acontece nos GISTs, a patogénese, incidência e prognóstico não estão completamente estabelecidos para os EGISTs uma vez que poucos casos estão descritos. Apresentamos uma breve revisão sobre o diagnóstico e abordagem terapêutica nestes casos.Sociedade Portuguesa de Cirurgia2021-08-09info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.34635/rpc.709https://doi.org/10.34635/rpc.709Revista Portuguesa de Cirurgia; No 50 (2021): Number 50 - March 2021; 69-74Revista Portuguesa de Cirurgia; No 50 (2021): Number 50 - March 2021; 69-742183-11651646-6918reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spcir.com/index.php/spcir/article/view/709https://revista.spcir.com/index.php/spcir/article/view/709/605Copyright (c) 2021 Revista Portuguesa de Cirurgiainfo:eu-repo/semantics/openAccessMartins Jordão, Daniel FilipeMartins, RuiPereira, João SantosFerrão, HenriqueFerrão, Isabel Cristina2024-03-14T22:04:52Zoai:revista.spcir.com:article/709Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T04:00:44.989507Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT EGIST GIGANTE DO MESOCÓLON TRANSVERSO: APRESENTAÇÃO DE CASO CLÍNICO |
title |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
spellingShingle |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT Martins Jordão, Daniel Filipe |
title_short |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
title_full |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
title_fullStr |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
title_full_unstemmed |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
title_sort |
GIANT EGIST OF THE TRANSVERSE MESOCOLON: CASE REPORT |
author |
Martins Jordão, Daniel Filipe |
author_facet |
Martins Jordão, Daniel Filipe Martins, Rui Pereira, João Santos Ferrão, Henrique Ferrão, Isabel Cristina |
author_role |
author |
author2 |
Martins, Rui Pereira, João Santos Ferrão, Henrique Ferrão, Isabel Cristina |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Martins Jordão, Daniel Filipe Martins, Rui Pereira, João Santos Ferrão, Henrique Ferrão, Isabel Cristina |
description |
Gastrointestinal stromal tumors are rare tumors of the gastroistestinal tract. Less than 5% of these are not associated to the gastrointestinal tract, being designated EGISTs. EGISTs of the mesocolon are extremely rare, with just a few cases reported in the literature. We present the case of an 82-year old female presenting with nausea and vomiting for a month, having had an ultra-sound(US) and CT which showed “large tumoral formation, mainly cystic, with significant contrast uptake in the solid component, measuring 16,6x11,2 cm, apparently independent from the tail of the pancreas, in the likely dependence of the gastric wall”. Endoscopic US and FNA were perfomed but the result was inconclusive. The patient underwent exploratory laparotomy with atypical gastrectomy, excision of the anterior layer of the transverse mesocolon and omentectomy en-bloc. Histopathology report revealed ephitelioid type malignant EGIST. pT4N0. By patient will no adjuvant therapy was performed. Although rare, GISTs are the most common mesenchymal tumors of the GI tract, nevertheless EGISTs of the mesocolon are extremely rare. Contrarily to what happens with GISTs, the pathogenesis, incidence and prognosis are not fully established for EGIST since there are few cases described. We present a brief review on the diagnosis and therapeutic approach to these cases. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-08-09 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
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publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.34635/rpc.709 https://doi.org/10.34635/rpc.709 |
url |
https://doi.org/10.34635/rpc.709 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spcir.com/index.php/spcir/article/view/709 https://revista.spcir.com/index.php/spcir/article/view/709/605 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2021 Revista Portuguesa de Cirurgia info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2021 Revista Portuguesa de Cirurgia |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Cirurgia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Cirurgia |
dc.source.none.fl_str_mv |
Revista Portuguesa de Cirurgia; No 50 (2021): Number 50 - March 2021; 69-74 Revista Portuguesa de Cirurgia; No 50 (2021): Number 50 - March 2021; 69-74 2183-1165 1646-6918 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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