Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?

Detalhes bibliográficos
Autor(a) principal: Teixeira, Ana Isabel
Data de Publicação: 2016
Outros Autores: Soares-Almeida, Luís, Leal Filipe, Paulo
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.29021/spdv.74.4.683
Resumo: Spiny keratoderma is a rare dermatosis of unknown etiology that has been described with both hereditary and acquired variants. The acquired form has been associated with underlying malignancy and systemic diseases. We report a case of a 65-year- -old caucasian male presenting with multiple filiform hyperkeratotic papules in the palmar aspect of his hands which were present for the past year. Skin biopsy revealed aspects compatible with spiny keratoderma. After 10 months of follow-up, the patient developed mycosis fungoides, staged as IB according to the European Organization for Research and Treatment of Cancer and treated with PUVAtherapy with good control of both dermatosis. The authors raise the hypothesis of a new paraneoplastic association of spiny keratoderma.
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spelling Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?Spiny Keratoderma Palmar que precedeu o Diagnóstico de Micose Fungóide: Uma Nova Associação Paraneoplásica?KeratodermaPalmoplantarMycosis FungoidesSkin NeoplasmsMicose FungoideNeoplasias da PeleQueratodermia PalmoplantarSpiny keratoderma is a rare dermatosis of unknown etiology that has been described with both hereditary and acquired variants. The acquired form has been associated with underlying malignancy and systemic diseases. We report a case of a 65-year- -old caucasian male presenting with multiple filiform hyperkeratotic papules in the palmar aspect of his hands which were present for the past year. Skin biopsy revealed aspects compatible with spiny keratoderma. After 10 months of follow-up, the patient developed mycosis fungoides, staged as IB according to the European Organization for Research and Treatment of Cancer and treated with PUVAtherapy with good control of both dermatosis. The authors raise the hypothesis of a new paraneoplastic association of spiny keratoderma.Os quadros de spiny keratoderma são raros, de etiologia desconhecida e ocorrem de forma esporádica ou hereditária. A variante esporádica ocorre frequentemente em associação a neoplasias ou doenças sistémicas. Os autores relatam o caso de um doente caucasiano que recorreu à consulta de Dermatologia com multiplas pápulas hiperqueratósicas filiformes palmares presentes desde há um ano. Foi realizada uma biópsia cutânea que permitiu efectuar o diagnóstico de spiny keratoderma. Após dez meses de follow-up, o doente desenvolveu lesões cutâneas de micose fungóide, tendo sido classificado como estadio IB de acordo com a European Organization for Research and Treatment of Cancer e tratado com PUVAterapia com controlo satisfatório da dermatose. Os autores discutem a hipótese de este caso se tratar de uma nova associação paraneoplásica de um quadro de spiny keratoderma.Sociedade Portuguesa de Dermatologia e Venereologia2016-12-26T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.74.4.683oai:ojs.revista.spdv.com.pt:article/683Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 4 (2016): Outubro - Dezembro; 405-407Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 4 (2016): Outubro - Dezembro; 405-4072182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttps://revista.spdv.com.pt/index.php/spdv/article/view/683https://doi.org/10.29021/spdv.74.4.683https://revista.spdv.com.pt/index.php/spdv/article/view/683/467Teixeira, Ana IsabelSoares-Almeida, LuísLeal Filipe, Pauloinfo:eu-repo/semantics/openAccess2022-10-06T12:35:01Zoai:ojs.revista.spdv.com.pt:article/683Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:11:00.286649Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
Spiny Keratoderma Palmar que precedeu o Diagnóstico de Micose Fungóide: Uma Nova Associação Paraneoplásica?
title Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
spellingShingle Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
Teixeira, Ana Isabel
Keratoderma
Palmoplantar
Mycosis Fungoides
Skin Neoplasms
Micose Fungoide
Neoplasias da Pele
Queratodermia Palmoplantar
title_short Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
title_full Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
title_fullStr Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
title_full_unstemmed Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
title_sort Palmar Spiny Keratoderma Preceding the Diagnosis of Mycosis Fungoides: A New Paraneoplastic Association?
author Teixeira, Ana Isabel
author_facet Teixeira, Ana Isabel
Soares-Almeida, Luís
Leal Filipe, Paulo
author_role author
author2 Soares-Almeida, Luís
Leal Filipe, Paulo
author2_role author
author
dc.contributor.author.fl_str_mv Teixeira, Ana Isabel
Soares-Almeida, Luís
Leal Filipe, Paulo
dc.subject.por.fl_str_mv Keratoderma
Palmoplantar
Mycosis Fungoides
Skin Neoplasms
Micose Fungoide
Neoplasias da Pele
Queratodermia Palmoplantar
topic Keratoderma
Palmoplantar
Mycosis Fungoides
Skin Neoplasms
Micose Fungoide
Neoplasias da Pele
Queratodermia Palmoplantar
description Spiny keratoderma is a rare dermatosis of unknown etiology that has been described with both hereditary and acquired variants. The acquired form has been associated with underlying malignancy and systemic diseases. We report a case of a 65-year- -old caucasian male presenting with multiple filiform hyperkeratotic papules in the palmar aspect of his hands which were present for the past year. Skin biopsy revealed aspects compatible with spiny keratoderma. After 10 months of follow-up, the patient developed mycosis fungoides, staged as IB according to the European Organization for Research and Treatment of Cancer and treated with PUVAtherapy with good control of both dermatosis. The authors raise the hypothesis of a new paraneoplastic association of spiny keratoderma.
publishDate 2016
dc.date.none.fl_str_mv 2016-12-26T00:00:00Z
dc.type.driver.fl_str_mv journal article
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dc.identifier.uri.fl_str_mv https://doi.org/10.29021/spdv.74.4.683
oai:ojs.revista.spdv.com.pt:article/683
url https://doi.org/10.29021/spdv.74.4.683
identifier_str_mv oai:ojs.revista.spdv.com.pt:article/683
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://revista.spdv.com.pt/index.php/spdv/article/view/683
https://doi.org/10.29021/spdv.74.4.683
https://revista.spdv.com.pt/index.php/spdv/article/view/683/467
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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dc.publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
dc.source.none.fl_str_mv Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 4 (2016): Outubro - Dezembro; 405-407
Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 4 (2016): Outubro - Dezembro; 405-407
2182-2409
2182-2395
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