Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association
Autor(a) principal: | |
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Data de Publicação: | 2006 |
Outros Autores: | , , , , , , , , , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.17/419 |
Resumo: | OBJECTIVE: Since most centers' experience with Ebstein anomaly is limited, we sought to analyze the collective experience of participating institutions of the European Congenital Heart Surgeons Association with surgery for this rare malformation. METHODS: The records of all 150 patients (median age 6.4 years) who underwent surgery for Ebstein anomaly in the 13 participating Association centers between January 1992 and January 2005 were reviewed retrospectively. Patients with congenitally corrected transposition were excluded. RESULTS: Most patients (81%) had Ebstein disease type B or C and significant functional impairment (61% in New York Heart Association class III or IV) and 16% had prior operations. Surgical procedures (n = 179) included valve replacement (n = 60, 33.5%), valve repair (n = 49, 27.3%), 1(1/2) ventricle repair (n = 46, 25.6%), palliative shunt (n = 13, 7.26%), and other complex procedures (n = 11, 6.14%). There were 20 hospital deaths (operative mortality 13.3%) after valve replacement in 5 patients, valve repair in 3, 1(1/2) ventricle repair in 7, palliative procedures in 3, and miscellaneous procedures in 2. Younger age and palliative procedures were univariate risk factors for operative death, but only age was an independent predictor on multivariable analysis. CONCLUSIONS: Most patients coming to surgery presented in childhood and were significantly symptomatic. More than half underwent valve replacement or repair, but a considerable proportion had severe disease necessitating 1(1/2) ventricle repair or palliative procedures. Operative mortality did not differ significantly among repair, replacement, and 1(1/2) ventricle repair but was associated with palliative procedures for severe disease early in life, young age being the only independent predictor of operative death. |
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Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons AssociationDistribuição por IdadeAnomalia de EbsteinEuropaVálvulas CardíacasVentrículos CardíacosMortalidade HospitalarModelos LogísticosAnálise MultivariadaCuidados PaliativosEstudos RetrospectivosResultado de TratamentoOBJECTIVE: Since most centers' experience with Ebstein anomaly is limited, we sought to analyze the collective experience of participating institutions of the European Congenital Heart Surgeons Association with surgery for this rare malformation. METHODS: The records of all 150 patients (median age 6.4 years) who underwent surgery for Ebstein anomaly in the 13 participating Association centers between January 1992 and January 2005 were reviewed retrospectively. Patients with congenitally corrected transposition were excluded. RESULTS: Most patients (81%) had Ebstein disease type B or C and significant functional impairment (61% in New York Heart Association class III or IV) and 16% had prior operations. Surgical procedures (n = 179) included valve replacement (n = 60, 33.5%), valve repair (n = 49, 27.3%), 1(1/2) ventricle repair (n = 46, 25.6%), palliative shunt (n = 13, 7.26%), and other complex procedures (n = 11, 6.14%). There were 20 hospital deaths (operative mortality 13.3%) after valve replacement in 5 patients, valve repair in 3, 1(1/2) ventricle repair in 7, palliative procedures in 3, and miscellaneous procedures in 2. Younger age and palliative procedures were univariate risk factors for operative death, but only age was an independent predictor on multivariable analysis. CONCLUSIONS: Most patients coming to surgery presented in childhood and were significantly symptomatic. More than half underwent valve replacement or repair, but a considerable proportion had severe disease necessitating 1(1/2) ventricle repair or palliative procedures. Operative mortality did not differ significantly among repair, replacement, and 1(1/2) ventricle repair but was associated with palliative procedures for severe disease early in life, young age being the only independent predictor of operative death.ElsevierRepositório do Centro Hospitalar Universitário de Lisboa Central, EPESarris, GGiannopoulos, NTsoutsinos, AChatzis, AKirvassilis, GBrawn, WComas, JCorno, ACarlo, DFragata, JHraska, VJacobs, JKrupianko, SSairanen, HStellin, GUrban, AZiemer, G2011-10-19T15:51:12Z20062006-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/419engJ Thorac Cardiovasc Surg. 2006 Jul;132(1):50-7. Epub 2006 Jun 2info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-10T09:26:43Zoai:repositorio.chlc.min-saude.pt:10400.17/419Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:18:13.931285Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
title |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
spellingShingle |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association Sarris, G Distribuição por Idade Anomalia de Ebstein Europa Válvulas Cardíacas Ventrículos Cardíacos Mortalidade Hospitalar Modelos Logísticos Análise Multivariada Cuidados Paliativos Estudos Retrospectivos Resultado de Tratamento |
title_short |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
title_full |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
title_fullStr |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
title_full_unstemmed |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
title_sort |
Results of Surgery for Ebstein Anomaly: a Multicenter Study from the European Congenital Heart Surgeons Association |
author |
Sarris, G |
author_facet |
Sarris, G Giannopoulos, N Tsoutsinos, A Chatzis, A Kirvassilis, G Brawn, W Comas, J Corno, A Carlo, D Fragata, J Hraska, V Jacobs, J Krupianko, S Sairanen, H Stellin, G Urban, A Ziemer, G |
author_role |
author |
author2 |
Giannopoulos, N Tsoutsinos, A Chatzis, A Kirvassilis, G Brawn, W Comas, J Corno, A Carlo, D Fragata, J Hraska, V Jacobs, J Krupianko, S Sairanen, H Stellin, G Urban, A Ziemer, G |
author2_role |
author author author author author author author author author author author author author author author author |
dc.contributor.none.fl_str_mv |
Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE |
dc.contributor.author.fl_str_mv |
Sarris, G Giannopoulos, N Tsoutsinos, A Chatzis, A Kirvassilis, G Brawn, W Comas, J Corno, A Carlo, D Fragata, J Hraska, V Jacobs, J Krupianko, S Sairanen, H Stellin, G Urban, A Ziemer, G |
dc.subject.por.fl_str_mv |
Distribuição por Idade Anomalia de Ebstein Europa Válvulas Cardíacas Ventrículos Cardíacos Mortalidade Hospitalar Modelos Logísticos Análise Multivariada Cuidados Paliativos Estudos Retrospectivos Resultado de Tratamento |
topic |
Distribuição por Idade Anomalia de Ebstein Europa Válvulas Cardíacas Ventrículos Cardíacos Mortalidade Hospitalar Modelos Logísticos Análise Multivariada Cuidados Paliativos Estudos Retrospectivos Resultado de Tratamento |
description |
OBJECTIVE: Since most centers' experience with Ebstein anomaly is limited, we sought to analyze the collective experience of participating institutions of the European Congenital Heart Surgeons Association with surgery for this rare malformation. METHODS: The records of all 150 patients (median age 6.4 years) who underwent surgery for Ebstein anomaly in the 13 participating Association centers between January 1992 and January 2005 were reviewed retrospectively. Patients with congenitally corrected transposition were excluded. RESULTS: Most patients (81%) had Ebstein disease type B or C and significant functional impairment (61% in New York Heart Association class III or IV) and 16% had prior operations. Surgical procedures (n = 179) included valve replacement (n = 60, 33.5%), valve repair (n = 49, 27.3%), 1(1/2) ventricle repair (n = 46, 25.6%), palliative shunt (n = 13, 7.26%), and other complex procedures (n = 11, 6.14%). There were 20 hospital deaths (operative mortality 13.3%) after valve replacement in 5 patients, valve repair in 3, 1(1/2) ventricle repair in 7, palliative procedures in 3, and miscellaneous procedures in 2. Younger age and palliative procedures were univariate risk factors for operative death, but only age was an independent predictor on multivariable analysis. CONCLUSIONS: Most patients coming to surgery presented in childhood and were significantly symptomatic. More than half underwent valve replacement or repair, but a considerable proportion had severe disease necessitating 1(1/2) ventricle repair or palliative procedures. Operative mortality did not differ significantly among repair, replacement, and 1(1/2) ventricle repair but was associated with palliative procedures for severe disease early in life, young age being the only independent predictor of operative death. |
publishDate |
2006 |
dc.date.none.fl_str_mv |
2006 2006-01-01T00:00:00Z 2011-10-19T15:51:12Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.17/419 |
url |
http://hdl.handle.net/10400.17/419 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
J Thorac Cardiovasc Surg. 2006 Jul;132(1):50-7. Epub 2006 Jun 2 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Elsevier |
publisher.none.fl_str_mv |
Elsevier |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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