Abdominal wall myxofibrosarcoma

Detalhes bibliográficos
Autor(a) principal: Aleixo, Sara
Data de Publicação: 2011
Outros Autores: Teixeira, Diana, Mesquita, Hugo, Costa, Vítor, Magalhães, Jorge, Alpoim, Carlos
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://revista.spcir.com/index.php/spcir/article/view/92
Resumo: There are few cases described of abdominal wall Myxofibrosarcoma. The authors describe the case of a 71 years old patient, who underwent urgent surgical excision of an 11 cm tumoral mass, of the internal inguinal orifice. Two months later, an excision of an 18 cm long inguinal tumor mass and multiple implants was performed. Because of a new recurrence after 4 months, a segmental bowel resection and end colostomy was performed. Patient died 6 months after first surgery. This case represents a high-grade myxofibrosarcoma, with an increasingly aggressive behavior and very short disease-free intervals, which was quickly fatal. Sarcomas are rare lesions, which initial approach should respect surgical principles and be treated by experienced teams. Keywords: Myxofibrosarcoma, high-grade, recurrence, debulking, abdominal wall. 
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spelling Abdominal wall myxofibrosarcomaMixofibrosarcoma da parede abdominalThere are few cases described of abdominal wall Myxofibrosarcoma. The authors describe the case of a 71 years old patient, who underwent urgent surgical excision of an 11 cm tumoral mass, of the internal inguinal orifice. Two months later, an excision of an 18 cm long inguinal tumor mass and multiple implants was performed. Because of a new recurrence after 4 months, a segmental bowel resection and end colostomy was performed. Patient died 6 months after first surgery. This case represents a high-grade myxofibrosarcoma, with an increasingly aggressive behavior and very short disease-free intervals, which was quickly fatal. Sarcomas are rare lesions, which initial approach should respect surgical principles and be treated by experienced teams. Keywords: Myxofibrosarcoma, high-grade, recurrence, debulking, abdominal wall. Existem poucos casos descritos de Mixofibrosarcoma da parede abdominal. Os autores apresentam o caso de um doente de 71 anos, submetido, de urgência, a exérese de massa tumoral com 11 cm, do orifício inguinal interno. Dois meses depois, realizou exérese de recidiva iliaco-inguinal com 18 cm e de múltiplos implantes sarcomatosos. Por nova recidiva, 4 meses depois, procedeu-se a enterectomia segmentar e colostomia terminal. O doente faleceu 6 meses após a cirurgia inicial. Fica aqui representado um caso de um mixofibrosarcoma de alto grau com um comportamento progressivamente agressivo, com intervalos livres de doença muito curtos, que foi rapidamente fatal. Os sarcomas são tumores raros, cuja abordagem inicial deve respeitar princípios cirúrgicos próprios, e devem ser orientados por equipas experientes. Palavras-chave: Mixofibrosarcoma, alto-grau, recidiva, redução tumoral, parede abdominal. Sociedade Portuguesa de Cirurgia2011-06-29info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://revista.spcir.com/index.php/spcir/article/view/92Revista Portuguesa de Cirurgia; No 17 (2011): Junho 2011 - II Série; 53-57Revista Portuguesa de Cirurgia; No 17 (2011): Junho 2011 - II Série; 53-572183-11651646-6918reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spcir.com/index.php/spcir/article/view/92https://revista.spcir.com/index.php/spcir/article/view/92/89Copyright (c) 2016 Revista Portuguesa de Cirurgiainfo:eu-repo/semantics/openAccessAleixo, SaraTeixeira, DianaMesquita, HugoCosta, VítorMagalhães, JorgeAlpoim, Carlos2024-03-14T22:05:03Zoai:revista.spcir.com:article/92Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T04:00:48.216788Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Abdominal wall myxofibrosarcoma
Mixofibrosarcoma da parede abdominal
title Abdominal wall myxofibrosarcoma
spellingShingle Abdominal wall myxofibrosarcoma
Aleixo, Sara
title_short Abdominal wall myxofibrosarcoma
title_full Abdominal wall myxofibrosarcoma
title_fullStr Abdominal wall myxofibrosarcoma
title_full_unstemmed Abdominal wall myxofibrosarcoma
title_sort Abdominal wall myxofibrosarcoma
author Aleixo, Sara
author_facet Aleixo, Sara
Teixeira, Diana
Mesquita, Hugo
Costa, Vítor
Magalhães, Jorge
Alpoim, Carlos
author_role author
author2 Teixeira, Diana
Mesquita, Hugo
Costa, Vítor
Magalhães, Jorge
Alpoim, Carlos
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Aleixo, Sara
Teixeira, Diana
Mesquita, Hugo
Costa, Vítor
Magalhães, Jorge
Alpoim, Carlos
description There are few cases described of abdominal wall Myxofibrosarcoma. The authors describe the case of a 71 years old patient, who underwent urgent surgical excision of an 11 cm tumoral mass, of the internal inguinal orifice. Two months later, an excision of an 18 cm long inguinal tumor mass and multiple implants was performed. Because of a new recurrence after 4 months, a segmental bowel resection and end colostomy was performed. Patient died 6 months after first surgery. This case represents a high-grade myxofibrosarcoma, with an increasingly aggressive behavior and very short disease-free intervals, which was quickly fatal. Sarcomas are rare lesions, which initial approach should respect surgical principles and be treated by experienced teams. Keywords: Myxofibrosarcoma, high-grade, recurrence, debulking, abdominal wall. 
publishDate 2011
dc.date.none.fl_str_mv 2011-06-29
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dc.identifier.uri.fl_str_mv https://revista.spcir.com/index.php/spcir/article/view/92
url https://revista.spcir.com/index.php/spcir/article/view/92
dc.language.iso.fl_str_mv por
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dc.relation.none.fl_str_mv https://revista.spcir.com/index.php/spcir/article/view/92
https://revista.spcir.com/index.php/spcir/article/view/92/89
dc.rights.driver.fl_str_mv Copyright (c) 2016 Revista Portuguesa de Cirurgia
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2016 Revista Portuguesa de Cirurgia
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
dc.source.none.fl_str_mv Revista Portuguesa de Cirurgia; No 17 (2011): Junho 2011 - II Série; 53-57
Revista Portuguesa de Cirurgia; No 17 (2011): Junho 2011 - II Série; 53-57
2183-1165
1646-6918
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
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