Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma

Detalhes bibliográficos
Autor(a) principal: Pontes, M.
Data de Publicação: 2014
Outros Autores: Barbosa, C., Coelho, M. L., Carvalho, L.
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10316/102689
https://doi.org/10.1016/j.rppneu.2013.06.007
Resumo: A 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.
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spelling Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyomaMediastinalLinfangioleiomiomaLinfangioleiomiomatoseMediastinalLymphangioleiomyomaLymphangioleiomyoma- tosisAgedFemaleHumansLung NeoplasmsLymphangioleiomyomatosisLymphangiomyomaMediastinal NeoplasmsNeoplasms, Multiple PrimaryA 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.Uma mulher de 68 anos foi submetida a uma ressecc¸ão de um linfoangioendotelioma mediastinal observado na monitorizac¸ão de uma lobectomia inferior esquerda devido a bronquiectasia, complicada por quilotórax. Isto levou a uma reavaliac¸ão do espécime pulmonar que revelou, além da bronquiectasia inflamatória, nódulos de pequenas células fusiformes no parênquima pulmonar, semelhantes a nódulos pulmonares de tipo meningotelial, mas com positividade imunohistoquímica para actina do músculo liso. A hipótese de desenvolvimento inicial de linfangioleiomiomatose pulmonar é discutida.2014info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttp://hdl.handle.net/10316/102689http://hdl.handle.net/10316/102689https://doi.org/10.1016/j.rppneu.2013.06.007por08732159Pontes, M.Barbosa, C.Coelho, M. L.Carvalho, L.info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2022-10-06T20:31:39Zoai:estudogeral.uc.pt:10316/102689Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T21:19:37.688005Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
title Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
spellingShingle Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
Pontes, M.
Mediastinal
Linfangioleiomioma
Linfangioleiomiomatose
Mediastinal
Lymphangioleiomyoma
Lymphangioleiomyoma- tosis
Aged
Female
Humans
Lung Neoplasms
Lymphangioleiomyomatosis
Lymphangiomyoma
Mediastinal Neoplasms
Neoplasms, Multiple Primary
title_short Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
title_full Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
title_fullStr Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
title_full_unstemmed Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
title_sort Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma
author Pontes, M.
author_facet Pontes, M.
Barbosa, C.
Coelho, M. L.
Carvalho, L.
author_role author
author2 Barbosa, C.
Coelho, M. L.
Carvalho, L.
author2_role author
author
author
dc.contributor.author.fl_str_mv Pontes, M.
Barbosa, C.
Coelho, M. L.
Carvalho, L.
dc.subject.por.fl_str_mv Mediastinal
Linfangioleiomioma
Linfangioleiomiomatose
Mediastinal
Lymphangioleiomyoma
Lymphangioleiomyoma- tosis
Aged
Female
Humans
Lung Neoplasms
Lymphangioleiomyomatosis
Lymphangiomyoma
Mediastinal Neoplasms
Neoplasms, Multiple Primary
topic Mediastinal
Linfangioleiomioma
Linfangioleiomiomatose
Mediastinal
Lymphangioleiomyoma
Lymphangioleiomyoma- tosis
Aged
Female
Humans
Lung Neoplasms
Lymphangioleiomyomatosis
Lymphangiomyoma
Mediastinal Neoplasms
Neoplasms, Multiple Primary
description A 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.
publishDate 2014
dc.date.none.fl_str_mv 2014
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10316/102689
http://hdl.handle.net/10316/102689
https://doi.org/10.1016/j.rppneu.2013.06.007
url http://hdl.handle.net/10316/102689
https://doi.org/10.1016/j.rppneu.2013.06.007
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv 08732159
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
repository.mail.fl_str_mv
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