Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis

Detalhes bibliográficos
Autor(a) principal: Cachão, Joana
Data de Publicação: 2020
Outros Autores: Raminhos, Isabel, Martins, José D., Bravio, Ivan
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18079
Resumo: Herein is described the case of a two-month-old female infant with recurrent respiratory infections, admitted to the Pediatric Emergency Department with productive cough, respiratory distress, and fever. Chest radiography showed an heterogenous hypotransparent image in the left pulmonary field and contralateral deviation of the mediastinum. Angiotomography revealed bilateral bronchopulmonary sequestration and a systemic vessel contributing to area irrigation. The patient was submitted to vessel occlusion and lacquering, left inferior lobectomy, and resection of a right lower lobe segment. Histological examination confirmed intralobar bronchopulmonary sequestration and type 2 congenital pulmonary airway malformation in the left lung, and extralobar bronchopulmonary sequestration in the right lung. With this report, the authors intend to emphasize the importance of clinical suspicion of congenital anomalies in infants with recurrent respiratory infections.
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spelling Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosisMalformação congénita das vias aéreas pulmonares e sequestro pulmonar no lactente - um diagnóstico raroCase ReportsHerein is described the case of a two-month-old female infant with recurrent respiratory infections, admitted to the Pediatric Emergency Department with productive cough, respiratory distress, and fever. Chest radiography showed an heterogenous hypotransparent image in the left pulmonary field and contralateral deviation of the mediastinum. Angiotomography revealed bilateral bronchopulmonary sequestration and a systemic vessel contributing to area irrigation. The patient was submitted to vessel occlusion and lacquering, left inferior lobectomy, and resection of a right lower lobe segment. Histological examination confirmed intralobar bronchopulmonary sequestration and type 2 congenital pulmonary airway malformation in the left lung, and extralobar bronchopulmonary sequestration in the right lung. With this report, the authors intend to emphasize the importance of clinical suspicion of congenital anomalies in infants with recurrent respiratory infections.A malformação congénita das vias aéreas pulmonares e o sequestro pulmonar são anomalias congénitas raras. É apresentado o caso de uma lactente de dois meses com infeções respiratórias de repetição, que recorreu à Urgência Pediátrica hospitalar por tosse produtiva, dificuldade respiratória e febre. A radiografia torácica evidenciou uma imagem hipotransparente heterogénea no campo pulmonar esquerdo e desvio contralateral do mediastino e a angiotomografia revelou sequestro pulmonar bilateral e presença de vaso sistémico a irrigar a área. A doente foi submetida a oclusão e laqueação do vaso, lobectomia inferior esquerda e resseção de segmento do lobo inferior direito. O exame histológico confirmou sequestro pulmonar intralobar associado a malformação congénita das vias aéreas pulmonares tipo 2 à esquerda e sequestro pulmonar extralobar à direita. Com este caso, os autores pretendem salientar a importância da suspeição clínica de anomalias congénitas perante um lactente com infeções respiratórias de repetição.Centro Hospitalar Universitário do Porto2020-11-26T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25753/BirthGrowthMJ.v29.i4.18079eng2183-9417Cachão, JoanaRaminhos, IsabelMartins, José D.Bravio, Ivaninfo:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2022-09-21T14:55:35Zoai:ojs.revistas.rcaap.pt:article/18079Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T15:56:29.498418Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
Malformação congénita das vias aéreas pulmonares e sequestro pulmonar no lactente - um diagnóstico raro
title Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
spellingShingle Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
Cachão, Joana
Case Reports
title_short Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
title_full Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
title_fullStr Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
title_full_unstemmed Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
title_sort Congenital pulmonary airway malformation and bronchopulmonary sequestration in infants - a rare diagnosis
author Cachão, Joana
author_facet Cachão, Joana
Raminhos, Isabel
Martins, José D.
Bravio, Ivan
author_role author
author2 Raminhos, Isabel
Martins, José D.
Bravio, Ivan
author2_role author
author
author
dc.contributor.author.fl_str_mv Cachão, Joana
Raminhos, Isabel
Martins, José D.
Bravio, Ivan
dc.subject.por.fl_str_mv Case Reports
topic Case Reports
description Herein is described the case of a two-month-old female infant with recurrent respiratory infections, admitted to the Pediatric Emergency Department with productive cough, respiratory distress, and fever. Chest radiography showed an heterogenous hypotransparent image in the left pulmonary field and contralateral deviation of the mediastinum. Angiotomography revealed bilateral bronchopulmonary sequestration and a systemic vessel contributing to area irrigation. The patient was submitted to vessel occlusion and lacquering, left inferior lobectomy, and resection of a right lower lobe segment. Histological examination confirmed intralobar bronchopulmonary sequestration and type 2 congenital pulmonary airway malformation in the left lung, and extralobar bronchopulmonary sequestration in the right lung. With this report, the authors intend to emphasize the importance of clinical suspicion of congenital anomalies in infants with recurrent respiratory infections.
publishDate 2020
dc.date.none.fl_str_mv 2020-11-26T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18079
url https://doi.org/10.25753/BirthGrowthMJ.v29.i4.18079
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2183-9417
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Centro Hospitalar Universitário do Porto
publisher.none.fl_str_mv Centro Hospitalar Universitário do Porto
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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