Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides
Autor(a) principal: | |
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Data de Publicação: | 2016 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.29021/spdv.74.3.599 |
Resumo: | Introduction: Pagetoid reticulosis is a rare variant of mycosis fungoides. The typical lesion is a solitary, slow-growing, well circumscribed and hyperkeratotic plaque or patch. A widespread form was also described, but, according to the last classification, the term is reserved for the localized variant (classically, "Woringer-Kolopp").Case report: We observed a 58-year-old patient, with a solitary keratotic plaque, 15mm x 18mm, on the plantar surface of the left halux. The lesion had been present for years, recently with local pain. The biopsy showed an infiltrate of small atypical lymphocytes with pagetoid invasion of the epidermis. On immunohistochemistry, a predominance of CD4+ T cells was observed. The results confirmed the diagnosis of pagetoid reticulosis. Two months after 0.05% clobetasol propionate applied daily, significant improvement was observed.Conclusions: Although pagetoid reticulosis is considered a variant of mycosis fungoides, it shows characteristic clinical and histopathological features, and a heterogenous immunophenotype. Extracutaneous involvement has not been reported. |
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Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis FungoidesReticulose Pagetóide de Woringer-Kolopp, uma Variante Rara de Micose FungóideMycosis FungoidesSkin NeoplasmsPagetoid ReticulosisT-cell Lymphoma cutaneousLinfoma células T cutâneoMicose FungóideNeoplasias da PeleReticulose PagetóideIntroduction: Pagetoid reticulosis is a rare variant of mycosis fungoides. The typical lesion is a solitary, slow-growing, well circumscribed and hyperkeratotic plaque or patch. A widespread form was also described, but, according to the last classification, the term is reserved for the localized variant (classically, "Woringer-Kolopp").Case report: We observed a 58-year-old patient, with a solitary keratotic plaque, 15mm x 18mm, on the plantar surface of the left halux. The lesion had been present for years, recently with local pain. The biopsy showed an infiltrate of small atypical lymphocytes with pagetoid invasion of the epidermis. On immunohistochemistry, a predominance of CD4+ T cells was observed. The results confirmed the diagnosis of pagetoid reticulosis. Two months after 0.05% clobetasol propionate applied daily, significant improvement was observed.Conclusions: Although pagetoid reticulosis is considered a variant of mycosis fungoides, it shows characteristic clinical and histopathological features, and a heterogenous immunophenotype. Extracutaneous involvement has not been reported.Introdução: A reticulose pagetóide é uma variante rara de micose fungóide. Caracteriza-se por uma mancha ou placa, geralmente numa extremidade, assintomática, e hiperqueratósica. Foi descrita uma forma disseminada, mas a classificação recente reserva o termo apenas para a variante localizada (classicamente, “Woringer-Kolopp”).Caso clínico: Observámos uma doente, de 58 anos, por uma placa solitária, queratósica, acastanhada, 15mm x 18mm, na face plantar do hálux esquerdo. Tinha anos de evolução, recentemente com dor local. A histopatologia mostrou um infiltrado de pequenos linfócitos atípicos com extensa invasão pagetóide da epiderme. Na imunohistoquímica observou-se um predomínio de células T CD4+. Os achados confirmaram o diagnóstico de reticulose pagetóide. Aplicou-se, diariamente, propionato de clobetasol 0,05%, em pomada, com melhoria clinicamente significativa após dois meses.Conclusões: Embora seja classificada como uma variante da micose fungóide, a reticulose pagetóide tem características clínicas e histopatológicas próprias, relativamente uniformes, e um perfil imunofenotípico heterogéneo. Contrariamente à micose fungóide, não ocorre envolvimento extracutâneo.Sociedade Portuguesa de Dermatologia e Venereologia2016-10-15T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.74.3.599oai:ojs.revista.spdv.com.pt:article/599Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 3 (2016): Julho / Setembro; 285-288Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 3 (2016): Julho / Setembro; 285-2882182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/599https://doi.org/10.29021/spdv.74.3.599https://revista.spdv.com.pt/index.php/spdv/article/view/599/422Roque Ferreira, BarbaraPinto Gouveia, MiguelCardoso, José CarlosReis, José Pedroinfo:eu-repo/semantics/openAccess2022-10-06T12:34:58Zoai:ojs.revista.spdv.com.pt:article/599Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:10:57.741468Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides Reticulose Pagetóide de Woringer-Kolopp, uma Variante Rara de Micose Fungóide |
title |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
spellingShingle |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides Roque Ferreira, Barbara Mycosis Fungoides Skin Neoplasms Pagetoid Reticulosis T-cell Lymphoma cutaneous Linfoma células T cutâneo Micose Fungóide Neoplasias da Pele Reticulose Pagetóide |
title_short |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
title_full |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
title_fullStr |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
title_full_unstemmed |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
title_sort |
Pagetoid Reticulosis Woringer–Kolopp type, a Rare Variant of Mycosis Fungoides |
author |
Roque Ferreira, Barbara |
author_facet |
Roque Ferreira, Barbara Pinto Gouveia, Miguel Cardoso, José Carlos Reis, José Pedro |
author_role |
author |
author2 |
Pinto Gouveia, Miguel Cardoso, José Carlos Reis, José Pedro |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Roque Ferreira, Barbara Pinto Gouveia, Miguel Cardoso, José Carlos Reis, José Pedro |
dc.subject.por.fl_str_mv |
Mycosis Fungoides Skin Neoplasms Pagetoid Reticulosis T-cell Lymphoma cutaneous Linfoma células T cutâneo Micose Fungóide Neoplasias da Pele Reticulose Pagetóide |
topic |
Mycosis Fungoides Skin Neoplasms Pagetoid Reticulosis T-cell Lymphoma cutaneous Linfoma células T cutâneo Micose Fungóide Neoplasias da Pele Reticulose Pagetóide |
description |
Introduction: Pagetoid reticulosis is a rare variant of mycosis fungoides. The typical lesion is a solitary, slow-growing, well circumscribed and hyperkeratotic plaque or patch. A widespread form was also described, but, according to the last classification, the term is reserved for the localized variant (classically, "Woringer-Kolopp").Case report: We observed a 58-year-old patient, with a solitary keratotic plaque, 15mm x 18mm, on the plantar surface of the left halux. The lesion had been present for years, recently with local pain. The biopsy showed an infiltrate of small atypical lymphocytes with pagetoid invasion of the epidermis. On immunohistochemistry, a predominance of CD4+ T cells was observed. The results confirmed the diagnosis of pagetoid reticulosis. Two months after 0.05% clobetasol propionate applied daily, significant improvement was observed.Conclusions: Although pagetoid reticulosis is considered a variant of mycosis fungoides, it shows characteristic clinical and histopathological features, and a heterogenous immunophenotype. Extracutaneous involvement has not been reported. |
publishDate |
2016 |
dc.date.none.fl_str_mv |
2016-10-15T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.74.3.599 oai:ojs.revista.spdv.com.pt:article/599 |
url |
https://doi.org/10.29021/spdv.74.3.599 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/599 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/599 https://doi.org/10.29021/spdv.74.3.599 https://revista.spdv.com.pt/index.php/spdv/article/view/599/422 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 3 (2016): Julho / Setembro; 285-288 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 3 (2016): Julho / Setembro; 285-288 2182-2409 2182-2395 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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