Case for Diagnosis

Detalhes bibliográficos
Autor(a) principal: Maio, P
Data de Publicação: 2013
Outros Autores: Afonso, A, Cabeçadas, J, Fernandes, C, Sachse, F, Cardoso, J
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10400.17/1252
Resumo: Blastic plasmacytoid dendritic cell tumor is a rare, highly aggressive systemic neoplasm for which effective therapies have not yet been established. We describe a 73-year-old man with multiple nodules and patches emerging on the trunk and limbs. Lesional skin biopsy revealed a plasmacytoid dendritic cell tumor with dense dermal infiltrate of tumor cells with blastoid features. No apparent systemic involvement was identified in the initial stage. The patient was treated with prednisone daily, with notorious improvement of the skin lesions, although no complete remission was obtained. During the six-month follow-up period, no disease progression was documented, but fatal systemic progression occurred after that period of time.
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spelling Case for DiagnosisCaso para DiagnósticoAntigénio CDHCC DERHCC ANPATCélulas DendríticasResultado FatalNeoplasias da PeleBlastic plasmacytoid dendritic cell tumor is a rare, highly aggressive systemic neoplasm for which effective therapies have not yet been established. We describe a 73-year-old man with multiple nodules and patches emerging on the trunk and limbs. Lesional skin biopsy revealed a plasmacytoid dendritic cell tumor with dense dermal infiltrate of tumor cells with blastoid features. No apparent systemic involvement was identified in the initial stage. The patient was treated with prednisone daily, with notorious improvement of the skin lesions, although no complete remission was obtained. During the six-month follow-up period, no disease progression was documented, but fatal systemic progression occurred after that period of time.Sociedade Brasileira de DermatologiaRepositório do Centro Hospitalar Universitário de Lisboa Central, EPEMaio, PAfonso, ACabeçadas, JFernandes, CSachse, FCardoso, J2013-05-14T16:45:58Z20132013-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/1252engAn Bras Dermatol. 2013 Jan-Feb;88(1):131-3info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-10T09:30:36Zoai:repositorio.chlc.min-saude.pt:10400.17/1252Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:18:47.996717Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Case for Diagnosis
Caso para Diagnóstico
title Case for Diagnosis
spellingShingle Case for Diagnosis
Maio, P
Antigénio CD
HCC DER
HCC ANPAT
Células Dendríticas
Resultado Fatal
Neoplasias da Pele
title_short Case for Diagnosis
title_full Case for Diagnosis
title_fullStr Case for Diagnosis
title_full_unstemmed Case for Diagnosis
title_sort Case for Diagnosis
author Maio, P
author_facet Maio, P
Afonso, A
Cabeçadas, J
Fernandes, C
Sachse, F
Cardoso, J
author_role author
author2 Afonso, A
Cabeçadas, J
Fernandes, C
Sachse, F
Cardoso, J
author2_role author
author
author
author
author
dc.contributor.none.fl_str_mv Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE
dc.contributor.author.fl_str_mv Maio, P
Afonso, A
Cabeçadas, J
Fernandes, C
Sachse, F
Cardoso, J
dc.subject.por.fl_str_mv Antigénio CD
HCC DER
HCC ANPAT
Células Dendríticas
Resultado Fatal
Neoplasias da Pele
topic Antigénio CD
HCC DER
HCC ANPAT
Células Dendríticas
Resultado Fatal
Neoplasias da Pele
description Blastic plasmacytoid dendritic cell tumor is a rare, highly aggressive systemic neoplasm for which effective therapies have not yet been established. We describe a 73-year-old man with multiple nodules and patches emerging on the trunk and limbs. Lesional skin biopsy revealed a plasmacytoid dendritic cell tumor with dense dermal infiltrate of tumor cells with blastoid features. No apparent systemic involvement was identified in the initial stage. The patient was treated with prednisone daily, with notorious improvement of the skin lesions, although no complete remission was obtained. During the six-month follow-up period, no disease progression was documented, but fatal systemic progression occurred after that period of time.
publishDate 2013
dc.date.none.fl_str_mv 2013-05-14T16:45:58Z
2013
2013-01-01T00:00:00Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/1252
url http://hdl.handle.net/10400.17/1252
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv An Bras Dermatol. 2013 Jan-Feb;88(1):131-3
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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