OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
Autor(a) principal: | |
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Data de Publicação: | 2019 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.25754/pjp.2019.14892 |
Resumo: | OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an AdolescentSíndrome OHVIRACase reportsOHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis whoA Síndrome OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) ou Síndrome de Herlyn-Werner-Wunderlich é uma doença congénita rara, secundária a uma anomalia mulleriana, caracterizada por útero didelfos, obstrução da hemivagina e agenésia renal ipsilateral. Apresenta-se habitualmente após a menarca com dor abdominal progressiva e tumefação pélvica secundárias a hematocolpus. Quando a obstrução da hemivagina não é completa o diagnóstico pode ser atrasado pela diminuição da gravidade dos sintomas e possível regularidade do ciclo menstrual. Raramente, surge na idade adulta como causa de infertilidade primária. É descrito um caso de uma adolescente de 15 anos, com diagnóstico pré-natal de agenésia renal direita com queixas de dor abdominal recorrente associada a tumefação abdomino-pélvica.Sociedade Portuguesa de Pediatria2019-07-15info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25754/pjp.2019.14892eng2184-44532184-3333Antunes, JoanaBarros, MarianaEzequiel, MartaCalado, RitaMartins, Mafaldainfo:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2024-05-06T15:12:14Zoai:ojs.revistas.rcaap.pt:article/14892Portal AgregadorONGhttps://www.rcaap.pt/oai/openairemluisa.alvim@gmail.comopendoar:71602024-05-06T15:12:14Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent Síndrome OHVIRA |
title |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
spellingShingle |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent Antunes, Joana Case reports |
title_short |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
title_full |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
title_fullStr |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
title_full_unstemmed |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
title_sort |
OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent |
author |
Antunes, Joana |
author_facet |
Antunes, Joana Barros, Mariana Ezequiel, Marta Calado, Rita Martins, Mafalda |
author_role |
author |
author2 |
Barros, Mariana Ezequiel, Marta Calado, Rita Martins, Mafalda |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Antunes, Joana Barros, Mariana Ezequiel, Marta Calado, Rita Martins, Mafalda |
dc.subject.por.fl_str_mv |
Case reports |
topic |
Case reports |
description |
OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who |
publishDate |
2019 |
dc.date.none.fl_str_mv |
2019-07-15 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.25754/pjp.2019.14892 |
url |
https://doi.org/10.25754/pjp.2019.14892 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
2184-4453 2184-3333 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Pediatria |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Pediatria |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
mluisa.alvim@gmail.com |
_version_ |
1817544123448557568 |