OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent

Detalhes bibliográficos
Autor(a) principal: Antunes, Joana
Data de Publicação: 2019
Outros Autores: Barros, Mariana, Ezequiel, Marta, Calado, Rita, Martins, Mafalda
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.25754/pjp.2019.14892
Resumo: OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who
id RCAP_e35c2dc7a7331f4e3e91f1ab64772de8
oai_identifier_str oai:ojs.revistas.rcaap.pt:article/14892
network_acronym_str RCAP
network_name_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository_id_str 7160
spelling OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an AdolescentSíndrome OHVIRACase reportsOHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis whoA Síndrome OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) ou Síndrome de Herlyn-Werner-Wunderlich é uma doença congénita rara, secundária a uma anomalia mulleriana, caracterizada por útero didelfos, obstrução da hemivagina e agenésia renal ipsilateral. Apresenta-se habitualmente após a menarca com dor abdominal progressiva e tumefação pélvica secundárias a hematocolpus. Quando a obstrução da hemivagina não é completa o diagnóstico pode ser atrasado pela diminuição da gravidade dos sintomas e possível regularidade do ciclo menstrual. Raramente, surge na idade adulta como causa de infertilidade primária. É descrito um caso de uma adolescente de 15 anos, com diagnóstico pré-natal de agenésia renal direita com queixas de dor abdominal recorrente associada a tumefação abdomino-pélvica.Sociedade Portuguesa de Pediatria2019-07-15info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25754/pjp.2019.14892eng2184-44532184-3333Antunes, JoanaBarros, MarianaEzequiel, MartaCalado, RitaMartins, Mafaldainfo:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2024-05-06T15:12:14Zoai:ojs.revistas.rcaap.pt:article/14892Portal AgregadorONGhttps://www.rcaap.pt/oai/openairemluisa.alvim@gmail.comopendoar:71602024-05-06T15:12:14Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
Síndrome OHVIRA
title OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
spellingShingle OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
Antunes, Joana
Case reports
title_short OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_full OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_fullStr OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_full_unstemmed OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
title_sort OHVIRA Syndrome: A Müllerian Anomaly as a Cause of Abdominal Pain in an Adolescent
author Antunes, Joana
author_facet Antunes, Joana
Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
author_role author
author2 Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Antunes, Joana
Barros, Mariana
Ezequiel, Marta
Calado, Rita
Martins, Mafalda
dc.subject.por.fl_str_mv Case reports
topic Case reports
description OHVIRA (Obstructed Hemi Vagina with Ipsilateral Renal Agenesis) or Herlyn-Werner-Wunderlich Syndrome is a rare congenital disease, caused by a Mullerian anomaly, characterized by a didelphys uterus, obstruction of the hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive abdominal pain and pelvic mass secondary to hematocolpus. When the hemivagina obstruction is incomplete, the diagnosis may be delayed by the reduction of the severity of symptoms and possible regularity of the menstrual cycle. Rarely, it presents in the adult age as the cause of primary infertility. We describe a case of a 15-year-old girl with prenatal diagnosis of right renal agenesis who
publishDate 2019
dc.date.none.fl_str_mv 2019-07-15
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.25754/pjp.2019.14892
url https://doi.org/10.25754/pjp.2019.14892
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 2184-4453
2184-3333
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
publisher.none.fl_str_mv Sociedade Portuguesa de Pediatria
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
repository.mail.fl_str_mv mluisa.alvim@gmail.com
_version_ 1817544123448557568