Pseudopapillary Tumor of Pancreas: a case report

Detalhes bibliográficos
Autor(a) principal: da Silva, Diana Teixeira Ferreira
Data de Publicação: 2012
Outros Autores: Moreira, Ricardo Manuel Lopes, Magalhães, Jorge Manuel, Ferreira, Manuel Teixeira, Alpoim e Meneses, José Carlos Machado
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://revista.spcir.com/index.php/spcir/article/view/38
Resumo: Introduction: Solid pseudopapillary tumors of the pancreas (SPT) is a rare entity, representing about 1-2% of all primary tumors of the pancreas. It affects women in their second or third decade. These tumors have a low malignant potential and prognosis is very good. Methods: Female, 47 years, referred to the emergency department for epigastric pain constant, with 15 days of evolution, associated with anorexia and nausea. Analytical study without changes and abdominal CT revealed “in the body of the pancreas, massive forma- tion of cystic appearance with 9.5 X 4 X 5 cm(...) lobulated, heterogeneous areas with fluid. Cystic mass in appearance but complex”, as confirmed by NMR. Submitted to laparotomic distal pancreactectomy with total splenectomy. Discharged on the 5rd day, with a good postoperative evolution. Histopathology revealed “neoformation 10cm centrally cavitated, with solid areas in the periphery and hemorrhagic, accounting for pseudopapillary solid tumor of the pancreas, immunohistochemistry positive: cytokeratin AE1/AE3, 8 / 18, vimentin, NSE and progesterone receptors.Discussion: The SPT of the pancreas is a rare tumor. The most common clinical picture is characterized by mass / swelling palpable abdominal and abdominal pain. The diagnosis of PTSD based on factors, clinical and imaging studies. Surgical treatment consists of distal pancreatectomy or pancrea- ticoduodenectomy, laparoscopy or laparotomy. Although surgical resection can be curative, the failure to timely diagnose these tumors may delay proper treatment, thereby increasing mortality. Keywords: solid pseudopapillary pancreatic tumor, diagnosis, surgical treatment, prognosis. 
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spelling Pseudopapillary Tumor of Pancreas: a case reportTumor Pseudopapilar do Pâncreas: relato de um casoIntroduction: Solid pseudopapillary tumors of the pancreas (SPT) is a rare entity, representing about 1-2% of all primary tumors of the pancreas. It affects women in their second or third decade. These tumors have a low malignant potential and prognosis is very good. Methods: Female, 47 years, referred to the emergency department for epigastric pain constant, with 15 days of evolution, associated with anorexia and nausea. Analytical study without changes and abdominal CT revealed “in the body of the pancreas, massive forma- tion of cystic appearance with 9.5 X 4 X 5 cm(...) lobulated, heterogeneous areas with fluid. Cystic mass in appearance but complex”, as confirmed by NMR. Submitted to laparotomic distal pancreactectomy with total splenectomy. Discharged on the 5rd day, with a good postoperative evolution. Histopathology revealed “neoformation 10cm centrally cavitated, with solid areas in the periphery and hemorrhagic, accounting for pseudopapillary solid tumor of the pancreas, immunohistochemistry positive: cytokeratin AE1/AE3, 8 / 18, vimentin, NSE and progesterone receptors.Discussion: The SPT of the pancreas is a rare tumor. The most common clinical picture is characterized by mass / swelling palpable abdominal and abdominal pain. The diagnosis of PTSD based on factors, clinical and imaging studies. Surgical treatment consists of distal pancreatectomy or pancrea- ticoduodenectomy, laparoscopy or laparotomy. Although surgical resection can be curative, the failure to timely diagnose these tumors may delay proper treatment, thereby increasing mortality. Keywords: solid pseudopapillary pancreatic tumor, diagnosis, surgical treatment, prognosis. Introdução: Os tumores sólidos pseudopapilares do pâncreas (SPT) são uma entidade rara, representando cerca 1-2% de todos os tumores primários de pâncreas. Afecta mulheres, na 2a ou 3a década. Esses tumores apresentam baixo potencial maligno e seu prog- nóstico é muito bom. Caso clínico: Mulher, 47 anos, referenciada ao serviço de urgência por dor abdominal epigástrica constante, com 15 dias de evolução, associada a anorexia e naúseas. Estudo analítico sem alterações e TC abdominal revelando: “no corpo do pâncreas, volumosa formação de aspecto cístico, com 9,5 X 4 X 5 cm(...) lobulada, heterogénea, com áreas fluídas. Massa cística de aspecto complexo”, confirmada por RMN. Submetida a pancreactectomia corpo-caudal com esplenectomia total em bloco laparotómica. Alta ao 5o dia pós-operatório sem registo de intercorrências. O exame histopatológico revelou – neoformação com 10cm, centralmente cavitada, com áreas sólidas na periferia e hemorrágicas, correspondendo a tumor sólido pseudopapilar do pâncreas, imunohistoquímica positiva: citoqueratinas AE1/AE3 e 8/18, vimentina, NSE e receptores de progesterona. Discussão: O SPT do pâncreas é um tumor raro. O quadro clínico mais comum é caracterizado por massa/tumefação abdominal palpável e dor abdominal inespecífica. O diagnóstico do SPT assenta em elementos de ordem clínica e nos exames de imagem. O tratamento cirúrgico consiste na pancreatectomia distal ou duodenopancreatectomia, laparoscópica ou laparotómica. Muito embora a ressecção cirúrgica possa ser curativa, a incapacidade de diagnosticar atempadamente estes tumores pode atrasar o tratamento ade- quado, aumentando assim a morbimortalidade. Palavras-chave: tumor sólido pseudopapilar pâncreas, diagnóstico, abordagem cirúrgica, prognóstico. Sociedade Portuguesa de Cirurgia2012-09-14info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://revista.spcir.com/index.php/spcir/article/view/38Revista Portuguesa de Cirurgia; No 22 (2012): Setembro 2012 - II Série; 55-60Revista Portuguesa de Cirurgia; No 22 (2012): Setembro 2012 - II Série; 55-602183-11651646-6918reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spcir.com/index.php/spcir/article/view/38https://revista.spcir.com/index.php/spcir/article/view/38/35Copyright (c) 2016 Revista Portuguesa de Cirurgiainfo:eu-repo/semantics/openAccessda Silva, Diana Teixeira FerreiraMoreira, Ricardo Manuel LopesMagalhães, Jorge ManuelFerreira, Manuel TeixeiraAlpoim e Meneses, José Carlos Machado2024-03-14T22:04:37Zoai:revista.spcir.com:article/38Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T04:00:40.300596Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Pseudopapillary Tumor of Pancreas: a case report
Tumor Pseudopapilar do Pâncreas: relato de um caso
title Pseudopapillary Tumor of Pancreas: a case report
spellingShingle Pseudopapillary Tumor of Pancreas: a case report
da Silva, Diana Teixeira Ferreira
title_short Pseudopapillary Tumor of Pancreas: a case report
title_full Pseudopapillary Tumor of Pancreas: a case report
title_fullStr Pseudopapillary Tumor of Pancreas: a case report
title_full_unstemmed Pseudopapillary Tumor of Pancreas: a case report
title_sort Pseudopapillary Tumor of Pancreas: a case report
author da Silva, Diana Teixeira Ferreira
author_facet da Silva, Diana Teixeira Ferreira
Moreira, Ricardo Manuel Lopes
Magalhães, Jorge Manuel
Ferreira, Manuel Teixeira
Alpoim e Meneses, José Carlos Machado
author_role author
author2 Moreira, Ricardo Manuel Lopes
Magalhães, Jorge Manuel
Ferreira, Manuel Teixeira
Alpoim e Meneses, José Carlos Machado
author2_role author
author
author
author
dc.contributor.author.fl_str_mv da Silva, Diana Teixeira Ferreira
Moreira, Ricardo Manuel Lopes
Magalhães, Jorge Manuel
Ferreira, Manuel Teixeira
Alpoim e Meneses, José Carlos Machado
description Introduction: Solid pseudopapillary tumors of the pancreas (SPT) is a rare entity, representing about 1-2% of all primary tumors of the pancreas. It affects women in their second or third decade. These tumors have a low malignant potential and prognosis is very good. Methods: Female, 47 years, referred to the emergency department for epigastric pain constant, with 15 days of evolution, associated with anorexia and nausea. Analytical study without changes and abdominal CT revealed “in the body of the pancreas, massive forma- tion of cystic appearance with 9.5 X 4 X 5 cm(...) lobulated, heterogeneous areas with fluid. Cystic mass in appearance but complex”, as confirmed by NMR. Submitted to laparotomic distal pancreactectomy with total splenectomy. Discharged on the 5rd day, with a good postoperative evolution. Histopathology revealed “neoformation 10cm centrally cavitated, with solid areas in the periphery and hemorrhagic, accounting for pseudopapillary solid tumor of the pancreas, immunohistochemistry positive: cytokeratin AE1/AE3, 8 / 18, vimentin, NSE and progesterone receptors.Discussion: The SPT of the pancreas is a rare tumor. The most common clinical picture is characterized by mass / swelling palpable abdominal and abdominal pain. The diagnosis of PTSD based on factors, clinical and imaging studies. Surgical treatment consists of distal pancreatectomy or pancrea- ticoduodenectomy, laparoscopy or laparotomy. Although surgical resection can be curative, the failure to timely diagnose these tumors may delay proper treatment, thereby increasing mortality. Keywords: solid pseudopapillary pancreatic tumor, diagnosis, surgical treatment, prognosis. 
publishDate 2012
dc.date.none.fl_str_mv 2012-09-14
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dc.relation.none.fl_str_mv https://revista.spcir.com/index.php/spcir/article/view/38
https://revista.spcir.com/index.php/spcir/article/view/38/35
dc.rights.driver.fl_str_mv Copyright (c) 2016 Revista Portuguesa de Cirurgia
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rights_invalid_str_mv Copyright (c) 2016 Revista Portuguesa de Cirurgia
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dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
publisher.none.fl_str_mv Sociedade Portuguesa de Cirurgia
dc.source.none.fl_str_mv Revista Portuguesa de Cirurgia; No 22 (2012): Setembro 2012 - II Série; 55-60
Revista Portuguesa de Cirurgia; No 22 (2012): Setembro 2012 - II Série; 55-60
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