The Hybrid Approach for Palliation of Hypoplastic Left Heart Syndrome: Intermediate Results of a Single-Center Experience

• Autor(a) principal: Laranjo, S
• Data de Publicação: 2015
• Outros Autores: Costa, G, Freitas, I, Martins, JD, Bakero, L, Trigo, C, Fragata, I, Fragata, J, Pinto, MF
• Tipo de documento: Artigo
• Idioma: eng
• Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
• Texto Completo: http://hdl.handle.net/10400.17/2175
• topic: HSM CAR PED; HSM CCT; HSM ANS; Cardiac Surgical Procedures/adverse effects; Cardiac Surgical Procedures/methods; Hypoplastic Left Heart Syndrome/mortality; Hypoplastic Left Heart Syndrome/surgery; Palliative Care; Prospective Studies; Survival Rate; Time Factors; Treatment Outcome

INTRODUCTION: Hypoplastic left heart syndrome (HLHS) is a major cause of cardiac death during the first week of life. The hybrid approach is a reliable, reproducible treatment option for patients with HLHS. Herein we report our results using this approach, focusing on its efficacy, safety and late outcome. METHODS: We reviewed prospectively collected data on patients treated for HLHS using a hybrid approach between July 2007 and September 2014. RESULTS: Nine patients had a stage 1 hybrid procedure, with seven undergoing a comprehensive stage 2 procedure. One patient completed the Fontan procedure. Five patients underwent balloon atrial septostomy after the hybrid procedure; in three patients, a stent was placed across the atrial septum. There were three deaths: two early after the hybrid procedure and one early after stage two palliation. Overall survival was 66%. CONCLUSIONS: In our single-center series, the hybrid approach for HLHS yields intermediate results comparable to those of the Norwood strategy. The existence of dedicated teams for the diagnosis and management of these patients, preferably in high-volume centers, is of major importance in this condition.