Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case
Autor(a) principal: | |
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Data de Publicação: | 2022 |
Outros Autores: | , , , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.24915/aup.37.1-2.162 |
Resumo: | Pheochromocytomas with vena cava thrombus are extremely rare, with only a few cases reported in the literature. Radical nephrectomy with adrenalectomy and inferior vena cava (IVC) thrombectomy is the treatment of choice. However, it is a challenging procedure and its surgical approach is yet to be standardized. We present a case of a 49-year-old male incidentally diagnosed with a pheochromocytoma with aggressive local invasion and a level 1 vena cava thrombus. A laparoscopic right radical nephrectomy with right adrenalectomy, IVC thrombectomy and cavorraphy. A detailed revision of the technique is performed and compared with current strategies for pheochromocytoma optimal treatment. Renal and adrenal masses with vena cava thrombus are associated with high morbidity and mortality, particularly in the case of pheochromocytoma. The management is complex but minimally invasive surgery can be performed safely in the context of an experienced multidisciplinary team. |
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Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma CaseNefrectomia Radical com Trombectomia da Veia Cava Laparoscópica num Caso de Feocromocitoma MalignoPheochromocytomaLaparoscopyNephrectomyRobotic Surgical ProceduresThrombectomyVena Cava, InferiorFeocromocitomaLaparoscopiaNefrectomiaProcedimentos Cirúrgicos RobóticosTrombectomiaVeia Cava InferiorPheochromocytomas with vena cava thrombus are extremely rare, with only a few cases reported in the literature. Radical nephrectomy with adrenalectomy and inferior vena cava (IVC) thrombectomy is the treatment of choice. However, it is a challenging procedure and its surgical approach is yet to be standardized. We present a case of a 49-year-old male incidentally diagnosed with a pheochromocytoma with aggressive local invasion and a level 1 vena cava thrombus. A laparoscopic right radical nephrectomy with right adrenalectomy, IVC thrombectomy and cavorraphy. A detailed revision of the technique is performed and compared with current strategies for pheochromocytoma optimal treatment. Renal and adrenal masses with vena cava thrombus are associated with high morbidity and mortality, particularly in the case of pheochromocytoma. The management is complex but minimally invasive surgery can be performed safely in the context of an experienced multidisciplinary team.Os feocromocitomas com trombo na veia cava são entidades extremamente raras, estando poucos casos descritos na literatura. Apesar da nefrectomia radical com adrenalectomia/suprarrenalectomia e trombectomia da veia cava inferior (VCI) corresponder ao tratamento de escolha, esta é uma técnica cirúrgica desafiante com uma abordagem ainda não padronizada. Apresenta-se um caso de um homem de 49 anos com diagnóstico incidental de um feocromocitoma localmente invasivo, com trombo na VCI nível 1. Foi proposta uma nefrectomia radical direita laparoscópica com adrenalectomia/suprarrenalectomia, trombectomia da VCI e cavorrafia. Neste artigo faz-se uma descrição detalhada da técnica cirúrgica e uma comparação com as estratégias atualmente utilizadas no tratamento do feocromocitoma. Tumores renais e suprarrenais/adrenais com trombo na veia cava estão associados a maior morbilidade e mortalidade, sobretudo no caso do feocromocitoma. Apesar de complexa, a cirurgia minimamente invasiva é uma opção segura no contexto de uma equipa experiente e multidisciplinar.Associação Portuguesa de Urologia2022-01-26info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://doi.org/10.24915/aup.37.1-2.162https://doi.org/10.24915/aup.37.1-2.162Acta Urológica Portuguesa; Vol. 37 No. 1-2 (2020): January - June; 27-31Acta Urológica Portuguesa; v. 37 n. 1-2 (2020): Janeiro - Junho; 27-312387-04192341-4022reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://www.actaurologicaportuguesa.com/index.php/aup/article/view/162http://www.actaurologicaportuguesa.com/index.php/aup/article/view/162/65Copyright (c) 2022 Portuguese Association of Urologyhttp://creativecommons.org/licenses/by-nc-nd/4.0info:eu-repo/semantics/openAccessPalmela Leitão, TitoMiranda, MiguelOliveira, TiagoOliveira, PedroPereira Pereira, InêsPalma dos Reis, JoséFernandes, IsabelOrmonde, LucindoCosta, LuisMendes Pedro, LuisLopes, Tomé2023-04-09T06:45:08Zoai:oai.actaurologicaportuguesa.com:article/162Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T15:55:55.287388Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case Nefrectomia Radical com Trombectomia da Veia Cava Laparoscópica num Caso de Feocromocitoma Maligno |
title |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
spellingShingle |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case Palmela Leitão, Tito Pheochromocytoma Laparoscopy Nephrectomy Robotic Surgical Procedures Thrombectomy Vena Cava, Inferior Feocromocitoma Laparoscopia Nefrectomia Procedimentos Cirúrgicos Robóticos Trombectomia Veia Cava Inferior |
title_short |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
title_full |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
title_fullStr |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
title_full_unstemmed |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
title_sort |
Laparoscopic Vena Cava Thrombectomy and Radical Nephrectomy in a Malignant Pheochromocytoma Case |
author |
Palmela Leitão, Tito |
author_facet |
Palmela Leitão, Tito Miranda, Miguel Oliveira, Tiago Oliveira, Pedro Pereira Pereira, Inês Palma dos Reis, José Fernandes, Isabel Ormonde, Lucindo Costa, Luis Mendes Pedro, Luis Lopes, Tomé |
author_role |
author |
author2 |
Miranda, Miguel Oliveira, Tiago Oliveira, Pedro Pereira Pereira, Inês Palma dos Reis, José Fernandes, Isabel Ormonde, Lucindo Costa, Luis Mendes Pedro, Luis Lopes, Tomé |
author2_role |
author author author author author author author author author author |
dc.contributor.author.fl_str_mv |
Palmela Leitão, Tito Miranda, Miguel Oliveira, Tiago Oliveira, Pedro Pereira Pereira, Inês Palma dos Reis, José Fernandes, Isabel Ormonde, Lucindo Costa, Luis Mendes Pedro, Luis Lopes, Tomé |
dc.subject.por.fl_str_mv |
Pheochromocytoma Laparoscopy Nephrectomy Robotic Surgical Procedures Thrombectomy Vena Cava, Inferior Feocromocitoma Laparoscopia Nefrectomia Procedimentos Cirúrgicos Robóticos Trombectomia Veia Cava Inferior |
topic |
Pheochromocytoma Laparoscopy Nephrectomy Robotic Surgical Procedures Thrombectomy Vena Cava, Inferior Feocromocitoma Laparoscopia Nefrectomia Procedimentos Cirúrgicos Robóticos Trombectomia Veia Cava Inferior |
description |
Pheochromocytomas with vena cava thrombus are extremely rare, with only a few cases reported in the literature. Radical nephrectomy with adrenalectomy and inferior vena cava (IVC) thrombectomy is the treatment of choice. However, it is a challenging procedure and its surgical approach is yet to be standardized. We present a case of a 49-year-old male incidentally diagnosed with a pheochromocytoma with aggressive local invasion and a level 1 vena cava thrombus. A laparoscopic right radical nephrectomy with right adrenalectomy, IVC thrombectomy and cavorraphy. A detailed revision of the technique is performed and compared with current strategies for pheochromocytoma optimal treatment. Renal and adrenal masses with vena cava thrombus are associated with high morbidity and mortality, particularly in the case of pheochromocytoma. The management is complex but minimally invasive surgery can be performed safely in the context of an experienced multidisciplinary team. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-01-26 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.24915/aup.37.1-2.162 https://doi.org/10.24915/aup.37.1-2.162 |
url |
https://doi.org/10.24915/aup.37.1-2.162 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
http://www.actaurologicaportuguesa.com/index.php/aup/article/view/162 http://www.actaurologicaportuguesa.com/index.php/aup/article/view/162/65 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2022 Portuguese Association of Urology http://creativecommons.org/licenses/by-nc-nd/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2022 Portuguese Association of Urology http://creativecommons.org/licenses/by-nc-nd/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Associação Portuguesa de Urologia |
publisher.none.fl_str_mv |
Associação Portuguesa de Urologia |
dc.source.none.fl_str_mv |
Acta Urológica Portuguesa; Vol. 37 No. 1-2 (2020): January - June; 27-31 Acta Urológica Portuguesa; v. 37 n. 1-2 (2020): Janeiro - Junho; 27-31 2387-0419 2341-4022 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
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1799130427761360896 |