Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart

• Autor(a) principal: Leite,Luiz Roberto
• Data de Publicação: 2001
• Outros Autores: Pereira,Kleber R. Ponzi, Alessi,Sílvio R. B., Paola,Angelo A. V. de
• Tipo de documento: Relatório
• Idioma: eng
• Título da fonte: Arquivos Brasileiros de Cardiologia (Online)
• Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2001000100007

Syncope in children is primarily related to vagal hyperreactivity, but ventricular tachycardia (VT) way rarely be seen. Catecholaminergic polymorphic VT is a rare entity that can occur in children without heart disease and with a normal QT interval, which may cause syncope and sudden cardiac death. In this report, we describe the clinical features, treatment, and clinical follow-up of three children with syncope associated with physical effort or emotion and cathecolaminergic polymorphic VT. Symptoms were controlled with beta-blockers, but one patient died suddenly in the fourth year of follow-up. Despite the rare occurrence, catecholaminergic polymorphic VT is an important cause of syncope and sudden death in children with no identified heart disease and normal QT interval.