Ofuji disease: a rare dermatosis and its challenging therapeutic approach
Autor(a) principal: | |
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Data de Publicação: | 2016 |
Outros Autores: | , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646 |
Resumo: | Abstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario. |
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Ofuji disease: a rare dermatosis and its challenging therapeutic approachSkin DiseasesPregnancyHIVNeutrophil infiltrationAbstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.Sociedade Brasileira de Dermatologia2016-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646Anais Brasileiros de Dermatologia v.91 n.5 2016reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20164778info:eu-repo/semantics/openAccessBrito,Fernanda Freitas deMartelli,Antonio Carlos CeribelliCavalcante,Maria Lopes Lamenha LinsPinto,Ana Cecília Versiani DuarteItimura,GabrielaSoares,Cleverson Teixeiraeng2016-11-04T00:00:00Zoai:scielo:S0365-05962016000500646Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2016-11-04T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
title |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
spellingShingle |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach Brito,Fernanda Freitas de Skin Diseases Pregnancy HIV Neutrophil infiltration |
title_short |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
title_full |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
title_fullStr |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
title_full_unstemmed |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
title_sort |
Ofuji disease: a rare dermatosis and its challenging therapeutic approach |
author |
Brito,Fernanda Freitas de |
author_facet |
Brito,Fernanda Freitas de Martelli,Antonio Carlos Ceribelli Cavalcante,Maria Lopes Lamenha Lins Pinto,Ana Cecília Versiani Duarte Itimura,Gabriela Soares,Cleverson Teixeira |
author_role |
author |
author2 |
Martelli,Antonio Carlos Ceribelli Cavalcante,Maria Lopes Lamenha Lins Pinto,Ana Cecília Versiani Duarte Itimura,Gabriela Soares,Cleverson Teixeira |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Brito,Fernanda Freitas de Martelli,Antonio Carlos Ceribelli Cavalcante,Maria Lopes Lamenha Lins Pinto,Ana Cecília Versiani Duarte Itimura,Gabriela Soares,Cleverson Teixeira |
dc.subject.por.fl_str_mv |
Skin Diseases Pregnancy HIV Neutrophil infiltration |
topic |
Skin Diseases Pregnancy HIV Neutrophil infiltration |
description |
Abstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario. |
publishDate |
2016 |
dc.date.none.fl_str_mv |
2016-10-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20164778 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.91 n.5 2016 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126421383249920 |