Ofuji disease: a rare dermatosis and its challenging therapeutic approach

Detalhes bibliográficos
Autor(a) principal: Brito,Fernanda Freitas de
Data de Publicação: 2016
Outros Autores: Martelli,Antonio Carlos Ceribelli, Cavalcante,Maria Lopes Lamenha Lins, Pinto,Ana Cecília Versiani Duarte, Itimura,Gabriela, Soares,Cleverson Teixeira
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646
Resumo: Abstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.
id SBD-1_2f119d7e2b6f51e7a21443b5504cd6e7
oai_identifier_str oai:scielo:S0365-05962016000500646
network_acronym_str SBD-1
network_name_str Anais brasileiros de dermatologia (Online)
repository_id_str
spelling Ofuji disease: a rare dermatosis and its challenging therapeutic approachSkin DiseasesPregnancyHIVNeutrophil infiltrationAbstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.Sociedade Brasileira de Dermatologia2016-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646Anais Brasileiros de Dermatologia v.91 n.5 2016reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20164778info:eu-repo/semantics/openAccessBrito,Fernanda Freitas deMartelli,Antonio Carlos CeribelliCavalcante,Maria Lopes Lamenha LinsPinto,Ana Cecília Versiani DuarteItimura,GabrielaSoares,Cleverson Teixeiraeng2016-11-04T00:00:00Zoai:scielo:S0365-05962016000500646Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2016-11-04T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Ofuji disease: a rare dermatosis and its challenging therapeutic approach
title Ofuji disease: a rare dermatosis and its challenging therapeutic approach
spellingShingle Ofuji disease: a rare dermatosis and its challenging therapeutic approach
Brito,Fernanda Freitas de
Skin Diseases
Pregnancy
HIV
Neutrophil infiltration
title_short Ofuji disease: a rare dermatosis and its challenging therapeutic approach
title_full Ofuji disease: a rare dermatosis and its challenging therapeutic approach
title_fullStr Ofuji disease: a rare dermatosis and its challenging therapeutic approach
title_full_unstemmed Ofuji disease: a rare dermatosis and its challenging therapeutic approach
title_sort Ofuji disease: a rare dermatosis and its challenging therapeutic approach
author Brito,Fernanda Freitas de
author_facet Brito,Fernanda Freitas de
Martelli,Antonio Carlos Ceribelli
Cavalcante,Maria Lopes Lamenha Lins
Pinto,Ana Cecília Versiani Duarte
Itimura,Gabriela
Soares,Cleverson Teixeira
author_role author
author2 Martelli,Antonio Carlos Ceribelli
Cavalcante,Maria Lopes Lamenha Lins
Pinto,Ana Cecília Versiani Duarte
Itimura,Gabriela
Soares,Cleverson Teixeira
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Brito,Fernanda Freitas de
Martelli,Antonio Carlos Ceribelli
Cavalcante,Maria Lopes Lamenha Lins
Pinto,Ana Cecília Versiani Duarte
Itimura,Gabriela
Soares,Cleverson Teixeira
dc.subject.por.fl_str_mv Skin Diseases
Pregnancy
HIV
Neutrophil infiltration
topic Skin Diseases
Pregnancy
HIV
Neutrophil infiltration
description Abstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.
publishDate 2016
dc.date.none.fl_str_mv 2016-10-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000500646
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20164778
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.91 n.5 2016
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
_version_ 1752126421383249920