Generalized pustular psoriasis (von Zumbusch)

Detalhes bibliográficos
Autor(a) principal: Romiti,Ricardo
Data de Publicação: 2022
Outros Autores: Hirayama,André Luís da Silva, Arnone,Marcelo, Magalhães,Renata Ferreira
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063
Resumo: Abstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences.
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spelling Generalized pustular psoriasis (von Zumbusch)AcrodermatitisPsoriasisPsoriasis/epidemiologyPsoriasis/geneticsPsoriasis/physiopathologyPsoriasis/therapyAbstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences.Sociedade Brasileira de Dermatologia2022-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063Anais Brasileiros de Dermatologia v.97 n.1 2022reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2021.05.011info:eu-repo/semantics/openAccessRomiti,RicardoHirayama,André Luís da SilvaArnone,MarceloMagalhães,Renata Ferreiraeng2022-02-16T00:00:00Zoai:scielo:S0365-05962022000100063Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2022-02-16T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Generalized pustular psoriasis (von Zumbusch)
title Generalized pustular psoriasis (von Zumbusch)
spellingShingle Generalized pustular psoriasis (von Zumbusch)
Romiti,Ricardo
Acrodermatitis
Psoriasis
Psoriasis/epidemiology
Psoriasis/genetics
Psoriasis/physiopathology
Psoriasis/therapy
title_short Generalized pustular psoriasis (von Zumbusch)
title_full Generalized pustular psoriasis (von Zumbusch)
title_fullStr Generalized pustular psoriasis (von Zumbusch)
title_full_unstemmed Generalized pustular psoriasis (von Zumbusch)
title_sort Generalized pustular psoriasis (von Zumbusch)
author Romiti,Ricardo
author_facet Romiti,Ricardo
Hirayama,André Luís da Silva
Arnone,Marcelo
Magalhães,Renata Ferreira
author_role author
author2 Hirayama,André Luís da Silva
Arnone,Marcelo
Magalhães,Renata Ferreira
author2_role author
author
author
dc.contributor.author.fl_str_mv Romiti,Ricardo
Hirayama,André Luís da Silva
Arnone,Marcelo
Magalhães,Renata Ferreira
dc.subject.por.fl_str_mv Acrodermatitis
Psoriasis
Psoriasis/epidemiology
Psoriasis/genetics
Psoriasis/physiopathology
Psoriasis/therapy
topic Acrodermatitis
Psoriasis
Psoriasis/epidemiology
Psoriasis/genetics
Psoriasis/physiopathology
Psoriasis/therapy
description Abstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences.
publishDate 2022
dc.date.none.fl_str_mv 2022-02-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1016/j.abd.2021.05.011
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.97 n.1 2022
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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