Generalized pustular psoriasis (von Zumbusch)
Autor(a) principal: | |
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Data de Publicação: | 2022 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063 |
Resumo: | Abstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences. |
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Anais brasileiros de dermatologia (Online) |
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Generalized pustular psoriasis (von Zumbusch)AcrodermatitisPsoriasisPsoriasis/epidemiologyPsoriasis/geneticsPsoriasis/physiopathologyPsoriasis/therapyAbstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences.Sociedade Brasileira de Dermatologia2022-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063Anais Brasileiros de Dermatologia v.97 n.1 2022reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2021.05.011info:eu-repo/semantics/openAccessRomiti,RicardoHirayama,André Luís da SilvaArnone,MarceloMagalhães,Renata Ferreiraeng2022-02-16T00:00:00Zoai:scielo:S0365-05962022000100063Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2022-02-16T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Generalized pustular psoriasis (von Zumbusch) |
title |
Generalized pustular psoriasis (von Zumbusch) |
spellingShingle |
Generalized pustular psoriasis (von Zumbusch) Romiti,Ricardo Acrodermatitis Psoriasis Psoriasis/epidemiology Psoriasis/genetics Psoriasis/physiopathology Psoriasis/therapy |
title_short |
Generalized pustular psoriasis (von Zumbusch) |
title_full |
Generalized pustular psoriasis (von Zumbusch) |
title_fullStr |
Generalized pustular psoriasis (von Zumbusch) |
title_full_unstemmed |
Generalized pustular psoriasis (von Zumbusch) |
title_sort |
Generalized pustular psoriasis (von Zumbusch) |
author |
Romiti,Ricardo |
author_facet |
Romiti,Ricardo Hirayama,André Luís da Silva Arnone,Marcelo Magalhães,Renata Ferreira |
author_role |
author |
author2 |
Hirayama,André Luís da Silva Arnone,Marcelo Magalhães,Renata Ferreira |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Romiti,Ricardo Hirayama,André Luís da Silva Arnone,Marcelo Magalhães,Renata Ferreira |
dc.subject.por.fl_str_mv |
Acrodermatitis Psoriasis Psoriasis/epidemiology Psoriasis/genetics Psoriasis/physiopathology Psoriasis/therapy |
topic |
Acrodermatitis Psoriasis Psoriasis/epidemiology Psoriasis/genetics Psoriasis/physiopathology Psoriasis/therapy |
description |
Abstract Generalized pustular psoriasis (von Zumbusch) is a rare and acute eruption characterized by multiple sterile pustules over an erythematous and edematous background, eventually associated with psoriasis vulgaris. Classically, it manifests as a potentially severe systemic picture and demands prompt diagnosis and intervention. The duration of each flare-up and intervals between the pustular episodes is extremely variable. Recently, genetic abnormalities have been identified mainly in the familial and early variants of this disease. The therapeutic arsenal is limited; however, new drugs being evaluated aim to control both pustular flare-ups and disease recurrences. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-02-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962022000100063 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1016/j.abd.2021.05.011 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.97 n.1 2022 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126424650612736 |