Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)

Detalhes bibliográficos
Autor(a) principal: Esposito,Ana Cláudia Cavalcante
Data de Publicação: 2016
Outros Autores: Munhoz,Tania, Abbade,Luciana Patrícia Fernandes, Miot,Hélio Amante
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000600840
Resumo: Abstract A 57-year-old female showed bulky, loose tumors, which progressively spread to her arms, anterior chest, and back. She reported dysphagia and dyspnea after mild exertion. She denied alcohol consumption. CT scan of her chest showed no internal lesions. Benign symmetric lipomatosis is a rare syndrome, clinically described as multiple nonencapsulated lipomas of various sizes and symmetrical distribution. This syndrome has three known phenotypes; in type 2 (Launois-Bensaude syndrome), lesions occur primarily on the shoulders, upper arms, and chest, and is unrelated to alcoholism. It causes aesthetic deformities and might block the upper airways. Mediastinal invasion might occur as well.
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spelling Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)lipomalipomatosismultiple symmetric lipomatosisAbstract A 57-year-old female showed bulky, loose tumors, which progressively spread to her arms, anterior chest, and back. She reported dysphagia and dyspnea after mild exertion. She denied alcohol consumption. CT scan of her chest showed no internal lesions. Benign symmetric lipomatosis is a rare syndrome, clinically described as multiple nonencapsulated lipomas of various sizes and symmetrical distribution. This syndrome has three known phenotypes; in type 2 (Launois-Bensaude syndrome), lesions occur primarily on the shoulders, upper arms, and chest, and is unrelated to alcoholism. It causes aesthetic deformities and might block the upper airways. Mediastinal invasion might occur as well.Sociedade Brasileira de Dermatologia2016-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000600840Anais Brasileiros de Dermatologia v.91 n.6 2016reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20164744info:eu-repo/semantics/openAccessEsposito,Ana Cláudia CavalcanteMunhoz,TaniaAbbade,Luciana Patrícia FernandesMiot,Hélio Amanteeng2017-01-06T00:00:00Zoai:scielo:S0365-05962016000600840Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2017-01-06T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
title Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
spellingShingle Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
Esposito,Ana Cláudia Cavalcante
lipoma
lipomatosis
multiple symmetric lipomatosis
title_short Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
title_full Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
title_fullStr Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
title_full_unstemmed Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
title_sort Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
author Esposito,Ana Cláudia Cavalcante
author_facet Esposito,Ana Cláudia Cavalcante
Munhoz,Tania
Abbade,Luciana Patrícia Fernandes
Miot,Hélio Amante
author_role author
author2 Munhoz,Tania
Abbade,Luciana Patrícia Fernandes
Miot,Hélio Amante
author2_role author
author
author
dc.contributor.author.fl_str_mv Esposito,Ana Cláudia Cavalcante
Munhoz,Tania
Abbade,Luciana Patrícia Fernandes
Miot,Hélio Amante
dc.subject.por.fl_str_mv lipoma
lipomatosis
multiple symmetric lipomatosis
topic lipoma
lipomatosis
multiple symmetric lipomatosis
description Abstract A 57-year-old female showed bulky, loose tumors, which progressively spread to her arms, anterior chest, and back. She reported dysphagia and dyspnea after mild exertion. She denied alcohol consumption. CT scan of her chest showed no internal lesions. Benign symmetric lipomatosis is a rare syndrome, clinically described as multiple nonencapsulated lipomas of various sizes and symmetrical distribution. This syndrome has three known phenotypes; in type 2 (Launois-Bensaude syndrome), lesions occur primarily on the shoulders, upper arms, and chest, and is unrelated to alcoholism. It causes aesthetic deformities and might block the upper airways. Mediastinal invasion might occur as well.
publishDate 2016
dc.date.none.fl_str_mv 2016-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000600840
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000600840
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20164744
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.91 n.6 2016
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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