Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report

Detalhes bibliográficos
Autor(a) principal: Leal,Paula Azevedo Borges
Data de Publicação: 2013
Outros Autores: Adriano,Adrilena Lopes, Breckenfeld,Marcelle Parente, Costa,Igor Santos, Sousa,Antônio Renê Diógenes de, Gonçalves,Heitor de Sá
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200256
Resumo: Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In this study, we report an atypical case of Rosai-Dorfman disease in a female with massive cutaneous manifestation on the thigh, associated with a minimal lymphadenopathy limited to the regional inguinal lymph nodes.
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spelling Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case reportEmperipolesisHistiocytosisHistiocytosis, non-langerhans-cellHistiocytosis, sinusRosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In this study, we report an atypical case of Rosai-Dorfman disease in a female with massive cutaneous manifestation on the thigh, associated with a minimal lymphadenopathy limited to the regional inguinal lymph nodes.Sociedade Brasileira de Dermatologia2013-04-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200256Anais Brasileiros de Dermatologia v.88 n.2 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/S0365-05962013000200014info:eu-repo/semantics/openAccessLeal,Paula Azevedo BorgesAdriano,Adrilena LopesBreckenfeld,Marcelle ParenteCosta,Igor SantosSousa,Antônio Renê Diógenes deGonçalves,Heitor de Sáeng2013-06-04T00:00:00Zoai:scielo:S0365-05962013000200256Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2013-06-04T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
title Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
spellingShingle Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
Leal,Paula Azevedo Borges
Emperipolesis
Histiocytosis
Histiocytosis, non-langerhans-cell
Histiocytosis, sinus
title_short Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
title_full Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
title_fullStr Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
title_full_unstemmed Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
title_sort Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report
author Leal,Paula Azevedo Borges
author_facet Leal,Paula Azevedo Borges
Adriano,Adrilena Lopes
Breckenfeld,Marcelle Parente
Costa,Igor Santos
Sousa,Antônio Renê Diógenes de
Gonçalves,Heitor de Sá
author_role author
author2 Adriano,Adrilena Lopes
Breckenfeld,Marcelle Parente
Costa,Igor Santos
Sousa,Antônio Renê Diógenes de
Gonçalves,Heitor de Sá
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Leal,Paula Azevedo Borges
Adriano,Adrilena Lopes
Breckenfeld,Marcelle Parente
Costa,Igor Santos
Sousa,Antônio Renê Diógenes de
Gonçalves,Heitor de Sá
dc.subject.por.fl_str_mv Emperipolesis
Histiocytosis
Histiocytosis, non-langerhans-cell
Histiocytosis, sinus
topic Emperipolesis
Histiocytosis
Histiocytosis, non-langerhans-cell
Histiocytosis, sinus
description Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In this study, we report an atypical case of Rosai-Dorfman disease in a female with massive cutaneous manifestation on the thigh, associated with a minimal lymphadenopathy limited to the regional inguinal lymph nodes.
publishDate 2013
dc.date.none.fl_str_mv 2013-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200256
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200256
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/S0365-05962013000200014
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.88 n.2 2013
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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