Granulomatous slack skin: a rare subtype of mycosis fungoides

Detalhes bibliográficos
Autor(a) principal: Motta,Letícia Marra da
Data de Publicação: 2017
Outros Autores: Soares,Cleverson Teixeira, Nakandakari,Sadamitsu, Silva,Gardênia Viana da, Nigro,Maria Helena Mazzi Freire, Brandão,Leticia Stella Gardini
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000500694
Resumo: Abstract: We report a case of granulomatous slack skin, a rare and indolent subtype of mycosis fungoides. It affects mainly men between the third and fourth decades. It is characterized by hardened and erithematous plaques that mainly affect flexural areas and become pedunculated after some years. Histological examination shows a dense infiltrate of small atypical lymphocytes involving the dermis (and sometimes the subcutaneous tissue) associated with histiocytic and multinucleated giant cells containing lymphocytes and elastic fibers (lymphophagocytosis and elastophagocytosis, respectively). Patients affected by this entity can develop secondary lymphomas. There are several but little effective therapeutic modalities described. Despite the indolent behavior of granulomatous slack skin, its early recognition and continuous monitoring by a dermatologist becomes essential for its management and prevention of an unfavorable outcome.
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spelling Granulomatous slack skin: a rare subtype of mycosis fungoidescutaneous T-cell lymphomaLymphoproliferative disordersMycosis fungoidesAbstract: We report a case of granulomatous slack skin, a rare and indolent subtype of mycosis fungoides. It affects mainly men between the third and fourth decades. It is characterized by hardened and erithematous plaques that mainly affect flexural areas and become pedunculated after some years. Histological examination shows a dense infiltrate of small atypical lymphocytes involving the dermis (and sometimes the subcutaneous tissue) associated with histiocytic and multinucleated giant cells containing lymphocytes and elastic fibers (lymphophagocytosis and elastophagocytosis, respectively). Patients affected by this entity can develop secondary lymphomas. There are several but little effective therapeutic modalities described. Despite the indolent behavior of granulomatous slack skin, its early recognition and continuous monitoring by a dermatologist becomes essential for its management and prevention of an unfavorable outcome.Sociedade Brasileira de Dermatologia2017-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000500694Anais Brasileiros de Dermatologia v.92 n.5 2017reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20175099info:eu-repo/semantics/openAccessMotta,Letícia Marra daSoares,Cleverson TeixeiraNakandakari,SadamitsuSilva,Gardênia Viana daNigro,Maria Helena Mazzi FreireBrandão,Leticia Stella Gardinieng2017-11-14T00:00:00Zoai:scielo:S0365-05962017000500694Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2017-11-14T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Granulomatous slack skin: a rare subtype of mycosis fungoides
title Granulomatous slack skin: a rare subtype of mycosis fungoides
spellingShingle Granulomatous slack skin: a rare subtype of mycosis fungoides
Motta,Letícia Marra da
cutaneous T-cell lymphoma
Lymphoproliferative disorders
Mycosis fungoides
title_short Granulomatous slack skin: a rare subtype of mycosis fungoides
title_full Granulomatous slack skin: a rare subtype of mycosis fungoides
title_fullStr Granulomatous slack skin: a rare subtype of mycosis fungoides
title_full_unstemmed Granulomatous slack skin: a rare subtype of mycosis fungoides
title_sort Granulomatous slack skin: a rare subtype of mycosis fungoides
author Motta,Letícia Marra da
author_facet Motta,Letícia Marra da
Soares,Cleverson Teixeira
Nakandakari,Sadamitsu
Silva,Gardênia Viana da
Nigro,Maria Helena Mazzi Freire
Brandão,Leticia Stella Gardini
author_role author
author2 Soares,Cleverson Teixeira
Nakandakari,Sadamitsu
Silva,Gardênia Viana da
Nigro,Maria Helena Mazzi Freire
Brandão,Leticia Stella Gardini
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Motta,Letícia Marra da
Soares,Cleverson Teixeira
Nakandakari,Sadamitsu
Silva,Gardênia Viana da
Nigro,Maria Helena Mazzi Freire
Brandão,Leticia Stella Gardini
dc.subject.por.fl_str_mv cutaneous T-cell lymphoma
Lymphoproliferative disorders
Mycosis fungoides
topic cutaneous T-cell lymphoma
Lymphoproliferative disorders
Mycosis fungoides
description Abstract: We report a case of granulomatous slack skin, a rare and indolent subtype of mycosis fungoides. It affects mainly men between the third and fourth decades. It is characterized by hardened and erithematous plaques that mainly affect flexural areas and become pedunculated after some years. Histological examination shows a dense infiltrate of small atypical lymphocytes involving the dermis (and sometimes the subcutaneous tissue) associated with histiocytic and multinucleated giant cells containing lymphocytes and elastic fibers (lymphophagocytosis and elastophagocytosis, respectively). Patients affected by this entity can develop secondary lymphomas. There are several but little effective therapeutic modalities described. Despite the indolent behavior of granulomatous slack skin, its early recognition and continuous monitoring by a dermatologist becomes essential for its management and prevention of an unfavorable outcome.
publishDate 2017
dc.date.none.fl_str_mv 2017-10-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000500694
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000500694
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20175099
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.92 n.5 2017
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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