Inherited epidermolysis bullosa: clinical and therapeutic aspects

Detalhes bibliográficos
Autor(a) principal: Boeira,Vanessa Lys Simas Yamakawa
Data de Publicação: 2013
Outros Autores: Souza,Erica Sales, Rocha,Bruno de Oliveira, Oliveira,Pedro Dantas, Oliveira,Maria de Fátima Santos Paim de, Rêgo,Vitória Regina Pedreira de Almeida, Follador,Ivonise
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200185
Resumo: Inherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.
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spelling Inherited epidermolysis bullosa: clinical and therapeutic aspectsEpidermolysis bullosaEpidermolysis bullosa dystrophicaEpidermolysis bullosa, junctionalEpidermolysis bullosa simplexInherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.Sociedade Brasileira de Dermatologia2013-04-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200185Anais Brasileiros de Dermatologia v.88 n.2 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/S0365-05962013000200001info:eu-repo/semantics/openAccessBoeira,Vanessa Lys Simas YamakawaSouza,Erica SalesRocha,Bruno de OliveiraOliveira,Pedro DantasOliveira,Maria de Fátima Santos Paim deRêgo,Vitória Regina Pedreira de AlmeidaFollador,Ivoniseeng2013-06-04T00:00:00Zoai:scielo:S0365-05962013000200185Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2013-06-04T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Inherited epidermolysis bullosa: clinical and therapeutic aspects
title Inherited epidermolysis bullosa: clinical and therapeutic aspects
spellingShingle Inherited epidermolysis bullosa: clinical and therapeutic aspects
Boeira,Vanessa Lys Simas Yamakawa
Epidermolysis bullosa
Epidermolysis bullosa dystrophica
Epidermolysis bullosa, junctional
Epidermolysis bullosa simplex
title_short Inherited epidermolysis bullosa: clinical and therapeutic aspects
title_full Inherited epidermolysis bullosa: clinical and therapeutic aspects
title_fullStr Inherited epidermolysis bullosa: clinical and therapeutic aspects
title_full_unstemmed Inherited epidermolysis bullosa: clinical and therapeutic aspects
title_sort Inherited epidermolysis bullosa: clinical and therapeutic aspects
author Boeira,Vanessa Lys Simas Yamakawa
author_facet Boeira,Vanessa Lys Simas Yamakawa
Souza,Erica Sales
Rocha,Bruno de Oliveira
Oliveira,Pedro Dantas
Oliveira,Maria de Fátima Santos Paim de
Rêgo,Vitória Regina Pedreira de Almeida
Follador,Ivonise
author_role author
author2 Souza,Erica Sales
Rocha,Bruno de Oliveira
Oliveira,Pedro Dantas
Oliveira,Maria de Fátima Santos Paim de
Rêgo,Vitória Regina Pedreira de Almeida
Follador,Ivonise
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv Boeira,Vanessa Lys Simas Yamakawa
Souza,Erica Sales
Rocha,Bruno de Oliveira
Oliveira,Pedro Dantas
Oliveira,Maria de Fátima Santos Paim de
Rêgo,Vitória Regina Pedreira de Almeida
Follador,Ivonise
dc.subject.por.fl_str_mv Epidermolysis bullosa
Epidermolysis bullosa dystrophica
Epidermolysis bullosa, junctional
Epidermolysis bullosa simplex
topic Epidermolysis bullosa
Epidermolysis bullosa dystrophica
Epidermolysis bullosa, junctional
Epidermolysis bullosa simplex
description Inherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.
publishDate 2013
dc.date.none.fl_str_mv 2013-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200185
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000200185
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/S0365-05962013000200001
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.88 n.2 2013
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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