Porokeratosis of Mibelli - literature review and a case report
Autor(a) principal: | |
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Data de Publicação: | 2013 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179 |
Resumo: | Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report. |
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Porokeratosis of Mibelli - literature review and a case reportChildParakeratosisPorokeratosisPorokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.Sociedade Brasileira de Dermatologia2013-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179Anais Brasileiros de Dermatologia v.88 n.6 suppl.1 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20132721info:eu-repo/semantics/openAccessFerreira,Flávia ReginaSantos,Leopoldo Duailibe NogueiraTagliarini,Fernando Augusto Nogueira MendesLira,Marcia Lanzoni de Alvarengaeng2014-06-16T00:00:00Zoai:scielo:S0365-05962013000800179Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-06-16T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Porokeratosis of Mibelli - literature review and a case report |
title |
Porokeratosis of Mibelli - literature review and a case report |
spellingShingle |
Porokeratosis of Mibelli - literature review and a case report Ferreira,Flávia Regina Child Parakeratosis Porokeratosis |
title_short |
Porokeratosis of Mibelli - literature review and a case report |
title_full |
Porokeratosis of Mibelli - literature review and a case report |
title_fullStr |
Porokeratosis of Mibelli - literature review and a case report |
title_full_unstemmed |
Porokeratosis of Mibelli - literature review and a case report |
title_sort |
Porokeratosis of Mibelli - literature review and a case report |
author |
Ferreira,Flávia Regina |
author_facet |
Ferreira,Flávia Regina Santos,Leopoldo Duailibe Nogueira Tagliarini,Fernando Augusto Nogueira Mendes Lira,Marcia Lanzoni de Alvarenga |
author_role |
author |
author2 |
Santos,Leopoldo Duailibe Nogueira Tagliarini,Fernando Augusto Nogueira Mendes Lira,Marcia Lanzoni de Alvarenga |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Ferreira,Flávia Regina Santos,Leopoldo Duailibe Nogueira Tagliarini,Fernando Augusto Nogueira Mendes Lira,Marcia Lanzoni de Alvarenga |
dc.subject.por.fl_str_mv |
Child Parakeratosis Porokeratosis |
topic |
Child Parakeratosis Porokeratosis |
description |
Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report. |
publishDate |
2013 |
dc.date.none.fl_str_mv |
2013-12-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20132721 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.88 n.6 suppl.1 2013 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126419408781312 |