Porokeratosis of Mibelli - literature review and a case report

Detalhes bibliográficos
Autor(a) principal: Ferreira,Flávia Regina
Data de Publicação: 2013
Outros Autores: Santos,Leopoldo Duailibe Nogueira, Tagliarini,Fernando Augusto Nogueira Mendes, Lira,Marcia Lanzoni de Alvarenga
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179
Resumo: Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.
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spelling Porokeratosis of Mibelli - literature review and a case reportChildParakeratosisPorokeratosisPorokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.Sociedade Brasileira de Dermatologia2013-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179Anais Brasileiros de Dermatologia v.88 n.6 suppl.1 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20132721info:eu-repo/semantics/openAccessFerreira,Flávia ReginaSantos,Leopoldo Duailibe NogueiraTagliarini,Fernando Augusto Nogueira MendesLira,Marcia Lanzoni de Alvarengaeng2014-06-16T00:00:00Zoai:scielo:S0365-05962013000800179Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-06-16T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Porokeratosis of Mibelli - literature review and a case report
title Porokeratosis of Mibelli - literature review and a case report
spellingShingle Porokeratosis of Mibelli - literature review and a case report
Ferreira,Flávia Regina
Child
Parakeratosis
Porokeratosis
title_short Porokeratosis of Mibelli - literature review and a case report
title_full Porokeratosis of Mibelli - literature review and a case report
title_fullStr Porokeratosis of Mibelli - literature review and a case report
title_full_unstemmed Porokeratosis of Mibelli - literature review and a case report
title_sort Porokeratosis of Mibelli - literature review and a case report
author Ferreira,Flávia Regina
author_facet Ferreira,Flávia Regina
Santos,Leopoldo Duailibe Nogueira
Tagliarini,Fernando Augusto Nogueira Mendes
Lira,Marcia Lanzoni de Alvarenga
author_role author
author2 Santos,Leopoldo Duailibe Nogueira
Tagliarini,Fernando Augusto Nogueira Mendes
Lira,Marcia Lanzoni de Alvarenga
author2_role author
author
author
dc.contributor.author.fl_str_mv Ferreira,Flávia Regina
Santos,Leopoldo Duailibe Nogueira
Tagliarini,Fernando Augusto Nogueira Mendes
Lira,Marcia Lanzoni de Alvarenga
dc.subject.por.fl_str_mv Child
Parakeratosis
Porokeratosis
topic Child
Parakeratosis
Porokeratosis
description Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.
publishDate 2013
dc.date.none.fl_str_mv 2013-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800179
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20132721
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.88 n.6 suppl.1 2013
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
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institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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