Chiari malformation and central sleep apnea syndrome: efficacy of treatment with adaptive servo-ventilation

• Autor(a) principal: Vale,Jorge Marques do
• Data de Publicação: 2014
• Outros Autores: Silva,Eloísa, Pereira,Isabel Gil, Marques,Catarina, Sanchez-Serrano,Amparo, Torres,António Simões
• Tipo de documento: Relatório
• Idioma: eng
• Título da fonte: Jornal Brasileiro de Pneumologia (Online)
• Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132014000500574
• topic: Sleep apnea, central; Arnold-Chiari malformation; Noninvasive ventilation

The Chiari malformation type I (CM-I) has been associated with sleep-disordered breathing, especially central sleep apnea syndrome. We report the case of a 44-year-old female with CM-I who was referred to our sleep laboratory for suspected sleep apnea. The patient had undergone decompressive surgery 3 years prior. An arterial blood gas analysis showed hypercapnia. Polysomnography showed a respiratory disturbance index of 108 events/h, and all were central apnea events. Treatment with adaptive servo-ventilation was initiated, and central apnea was resolved. This report demonstrates the efficacy of servo-ventilation in the treatment of central sleep apnea syndrome associated with alveolar hypoventilation in a CM-I patient with a history of decompressive surgery.