Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome

Detalhes bibliográficos
Autor(a) principal: Favorito,Luciano A.
Data de Publicação: 2003
Tipo de documento: Relatório
Idioma: eng
Título da fonte: International Braz J Urol (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-55382003000200010
Resumo: Klippel-Trenaunay-Weber syndrome is characterized by cutaneous hemangiomas, varicosity and bony hypertrophy of extremities. Urinary tract hemangiomas may occur in 3 to 6% of these patients. This work intends to report a case of a patient with a huge vesical hemangioma, who presented this syndrome. A 5 year-old boy with Klippel syndrome sought our services due to 3 episodes of gross hematuria in the past 30 days. Excretory urography and computerized tomography were performed, indicating the presence of a swelling in vesical dome. An exploratory cystotomy was conducted and the dark colored mass in vesical dome was excised by partial cystectomy. The histopathologic finding confirmed that it was a vesical hemangioma. Though rare, urinary tract hemangiomas must always be considered in patients with Klippel-Trenaunay syndrome.
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spelling Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndromebladderhemangiomaKlippel-Trenaunay-Weber syndrometherapeuticsKlippel-Trenaunay-Weber syndrome is characterized by cutaneous hemangiomas, varicosity and bony hypertrophy of extremities. Urinary tract hemangiomas may occur in 3 to 6% of these patients. This work intends to report a case of a patient with a huge vesical hemangioma, who presented this syndrome. A 5 year-old boy with Klippel syndrome sought our services due to 3 episodes of gross hematuria in the past 30 days. Excretory urography and computerized tomography were performed, indicating the presence of a swelling in vesical dome. An exploratory cystotomy was conducted and the dark colored mass in vesical dome was excised by partial cystectomy. The histopathologic finding confirmed that it was a vesical hemangioma. Though rare, urinary tract hemangiomas must always be considered in patients with Klippel-Trenaunay syndrome.Sociedade Brasileira de Urologia2003-04-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-55382003000200010International braz j urol v.29 n.2 2003reponame:International Braz J Urol (Online)instname:Sociedade Brasileira de Urologia (SBU)instacron:SBU10.1590/S1677-55382003000200010info:eu-repo/semantics/openAccessFavorito,Luciano A.eng2003-09-19T00:00:00Zoai:scielo:S1677-55382003000200010Revistahttp://www.brazjurol.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.php||brazjurol@brazjurol.com.br1677-61191677-5538opendoar:2003-09-19T00:00International Braz J Urol (Online) - Sociedade Brasileira de Urologia (SBU)false
dc.title.none.fl_str_mv Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
title Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
spellingShingle Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
Favorito,Luciano A.
bladder
hemangioma
Klippel-Trenaunay-Weber syndrome
therapeutics
title_short Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
title_full Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
title_fullStr Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
title_full_unstemmed Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
title_sort Vesical hemangioma in patient with Klippel-Trenaunay-Weber syndrome
author Favorito,Luciano A.
author_facet Favorito,Luciano A.
author_role author
dc.contributor.author.fl_str_mv Favorito,Luciano A.
dc.subject.por.fl_str_mv bladder
hemangioma
Klippel-Trenaunay-Weber syndrome
therapeutics
topic bladder
hemangioma
Klippel-Trenaunay-Weber syndrome
therapeutics
description Klippel-Trenaunay-Weber syndrome is characterized by cutaneous hemangiomas, varicosity and bony hypertrophy of extremities. Urinary tract hemangiomas may occur in 3 to 6% of these patients. This work intends to report a case of a patient with a huge vesical hemangioma, who presented this syndrome. A 5 year-old boy with Klippel syndrome sought our services due to 3 episodes of gross hematuria in the past 30 days. Excretory urography and computerized tomography were performed, indicating the presence of a swelling in vesical dome. An exploratory cystotomy was conducted and the dark colored mass in vesical dome was excised by partial cystectomy. The histopathologic finding confirmed that it was a vesical hemangioma. Though rare, urinary tract hemangiomas must always be considered in patients with Klippel-Trenaunay syndrome.
publishDate 2003
dc.date.none.fl_str_mv 2003-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-55382003000200010
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-55382003000200010
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/S1677-55382003000200010
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Urologia
publisher.none.fl_str_mv Sociedade Brasileira de Urologia
dc.source.none.fl_str_mv International braz j urol v.29 n.2 2003
reponame:International Braz J Urol (Online)
instname:Sociedade Brasileira de Urologia (SBU)
instacron:SBU
instname_str Sociedade Brasileira de Urologia (SBU)
instacron_str SBU
institution SBU
reponame_str International Braz J Urol (Online)
collection International Braz J Urol (Online)
repository.name.fl_str_mv International Braz J Urol (Online) - Sociedade Brasileira de Urologia (SBU)
repository.mail.fl_str_mv ||brazjurol@brazjurol.com.br
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