Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
Autor(a) principal: | |
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Data de Publicação: | 2016 |
Outros Autores: | , , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Revista Paulista de Pediatria (Ed. Português. Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384 |
Resumo: | Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed. |
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Congenital intrahepatic portosystemic shunt diagnosed during intrauterine lifePrenatal diagnosisCongenital abnormalitiesCT scanDoppler ultrasoundAbstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.Sociedade de Pediatria de São Paulo2016-09-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384Revista Paulista de Pediatria v.34 n.3 2016reponame:Revista Paulista de Pediatria (Ed. Português. Online)instname:Sociedade de Pediatria de São Paulo (SPSP)instacron:SPSP10.1016/j.rppede.2016.03.016info:eu-repo/semantics/openAccessBellettini,Camila VieiraWagner,RafaelaBalzanelo,Aleocídio SetteAndretta,André Luis de SouzaMoura,Arthur Nascimento deFabris,Catia CarolinaGubert,Eduardo Maranhãoeng2016-09-08T00:00:00Zoai:scielo:S0103-05822016000300384Revistahttps://www.rpped.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.phppediatria@spsp.org.br||rpp@spsp.org.br1984-04620103-0582opendoar:2016-09-08T00:00Revista Paulista de Pediatria (Ed. Português. Online) - Sociedade de Pediatria de São Paulo (SPSP)false |
dc.title.none.fl_str_mv |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
spellingShingle |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life Bellettini,Camila Vieira Prenatal diagnosis Congenital abnormalities CT scan Doppler ultrasound |
title_short |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_full |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_fullStr |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_full_unstemmed |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_sort |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
author |
Bellettini,Camila Vieira |
author_facet |
Bellettini,Camila Vieira Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão |
author_role |
author |
author2 |
Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão |
author2_role |
author author author author author author |
dc.contributor.author.fl_str_mv |
Bellettini,Camila Vieira Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão |
dc.subject.por.fl_str_mv |
Prenatal diagnosis Congenital abnormalities CT scan Doppler ultrasound |
topic |
Prenatal diagnosis Congenital abnormalities CT scan Doppler ultrasound |
description |
Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed. |
publishDate |
2016 |
dc.date.none.fl_str_mv |
2016-09-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1016/j.rppede.2016.03.016 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade de Pediatria de São Paulo |
publisher.none.fl_str_mv |
Sociedade de Pediatria de São Paulo |
dc.source.none.fl_str_mv |
Revista Paulista de Pediatria v.34 n.3 2016 reponame:Revista Paulista de Pediatria (Ed. Português. Online) instname:Sociedade de Pediatria de São Paulo (SPSP) instacron:SPSP |
instname_str |
Sociedade de Pediatria de São Paulo (SPSP) |
instacron_str |
SPSP |
institution |
SPSP |
reponame_str |
Revista Paulista de Pediatria (Ed. Português. Online) |
collection |
Revista Paulista de Pediatria (Ed. Português. Online) |
repository.name.fl_str_mv |
Revista Paulista de Pediatria (Ed. Português. Online) - Sociedade de Pediatria de São Paulo (SPSP) |
repository.mail.fl_str_mv |
pediatria@spsp.org.br||rpp@spsp.org.br |
_version_ |
1750318249696821248 |