Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life

Detalhes bibliográficos
Autor(a) principal: Bellettini,Camila Vieira
Data de Publicação: 2016
Outros Autores: Wagner,Rafaela, Balzanelo,Aleocídio Sette, Andretta,André Luis de Souza, Moura,Arthur Nascimento de, Fabris,Catia Carolina, Gubert,Eduardo Maranhão
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Revista Paulista de Pediatria (Ed. Português. Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384
Resumo: Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.
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spelling Congenital intrahepatic portosystemic shunt diagnosed during intrauterine lifePrenatal diagnosisCongenital abnormalitiesCT scanDoppler ultrasoundAbstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.Sociedade de Pediatria de São Paulo2016-09-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384Revista Paulista de Pediatria v.34 n.3 2016reponame:Revista Paulista de Pediatria (Ed. Português. Online)instname:Sociedade de Pediatria de São Paulo (SPSP)instacron:SPSP10.1016/j.rppede.2016.03.016info:eu-repo/semantics/openAccessBellettini,Camila VieiraWagner,RafaelaBalzanelo,Aleocídio SetteAndretta,André Luis de SouzaMoura,Arthur Nascimento deFabris,Catia CarolinaGubert,Eduardo Maranhãoeng2016-09-08T00:00:00Zoai:scielo:S0103-05822016000300384Revistahttps://www.rpped.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.phppediatria@spsp.org.br||rpp@spsp.org.br1984-04620103-0582opendoar:2016-09-08T00:00Revista Paulista de Pediatria (Ed. Português. Online) - Sociedade de Pediatria de São Paulo (SPSP)false
dc.title.none.fl_str_mv Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
title Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
spellingShingle Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
Bellettini,Camila Vieira
Prenatal diagnosis
Congenital abnormalities
CT scan
Doppler ultrasound
title_short Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
title_full Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
title_fullStr Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
title_full_unstemmed Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
title_sort Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
author Bellettini,Camila Vieira
author_facet Bellettini,Camila Vieira
Wagner,Rafaela
Balzanelo,Aleocídio Sette
Andretta,André Luis de Souza
Moura,Arthur Nascimento de
Fabris,Catia Carolina
Gubert,Eduardo Maranhão
author_role author
author2 Wagner,Rafaela
Balzanelo,Aleocídio Sette
Andretta,André Luis de Souza
Moura,Arthur Nascimento de
Fabris,Catia Carolina
Gubert,Eduardo Maranhão
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv Bellettini,Camila Vieira
Wagner,Rafaela
Balzanelo,Aleocídio Sette
Andretta,André Luis de Souza
Moura,Arthur Nascimento de
Fabris,Catia Carolina
Gubert,Eduardo Maranhão
dc.subject.por.fl_str_mv Prenatal diagnosis
Congenital abnormalities
CT scan
Doppler ultrasound
topic Prenatal diagnosis
Congenital abnormalities
CT scan
Doppler ultrasound
description Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.
publishDate 2016
dc.date.none.fl_str_mv 2016-09-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
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dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384
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dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1016/j.rppede.2016.03.016
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eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade de Pediatria de São Paulo
publisher.none.fl_str_mv Sociedade de Pediatria de São Paulo
dc.source.none.fl_str_mv Revista Paulista de Pediatria v.34 n.3 2016
reponame:Revista Paulista de Pediatria (Ed. Português. Online)
instname:Sociedade de Pediatria de São Paulo (SPSP)
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instname_str Sociedade de Pediatria de São Paulo (SPSP)
instacron_str SPSP
institution SPSP
reponame_str Revista Paulista de Pediatria (Ed. Português. Online)
collection Revista Paulista de Pediatria (Ed. Português. Online)
repository.name.fl_str_mv Revista Paulista de Pediatria (Ed. Português. Online) - Sociedade de Pediatria de São Paulo (SPSP)
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