Castleman`s Disease and POEMS Syndrome: case reporte and review of literature

Detalhes bibliográficos
Autor(a) principal: Fontana, Bianca
Data de Publicação: 2008
Outros Autores: Zanella, André, Prezzi, Sérgio
Tipo de documento: Artigo
Idioma: por
Título da fonte: Clinical and Biomedical Research
Texto Completo: https://seer.ufrgs.br/index.php/hcpa/article/view/3976
Resumo: Castleman’s disease is a lymphoproliferative disorder related with human herpesvirus 8 and HIV, presenting in two different ways. The unicentric form is benign, doesn’t have systemic symptoms and is usually cured with surgery. The multicentric form usually presents with generalized lymphadenopathy, fever, weight loss, and other systemic manifestations and it can be associated with malignancy, especially POEMS syndrome. We report a case of a 50 year old man presenting with weight loss, fever and lymphadenopathy, associated with monoclonal gammopathy, organomegaly, endocrinopathy and neuropathy, which diagnosis was Castleman’s disease with POEMS syndrome
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spelling Castleman`s Disease and POEMS Syndrome: case reporte and review of literatureDoença de Castleman e Síndrome de POEMS: relato de caso e revisão da literaturaDoença de CastlemanSíndrome de POEMSE01.370.374.050Castleman’s disease is a lymphoproliferative disorder related with human herpesvirus 8 and HIV, presenting in two different ways. The unicentric form is benign, doesn’t have systemic symptoms and is usually cured with surgery. The multicentric form usually presents with generalized lymphadenopathy, fever, weight loss, and other systemic manifestations and it can be associated with malignancy, especially POEMS syndrome. We report a case of a 50 year old man presenting with weight loss, fever and lymphadenopathy, associated with monoclonal gammopathy, organomegaly, endocrinopathy and neuropathy, which diagnosis was Castleman’s disease with POEMS syndromeA Doença de Castleman é uma desordem linfoproliferativa que apresenta relação etiológica com o herpes vírus tipo 8 e o HIV, manifestando-se de duas formas distintas. A forma unicêntrica é benigna, não cursa com sintomas sistêmicos e geralmente é curada com a ressecção cirúrgica. A forma multicêntrica geralmente apresenta-se com linfadenopatia generalizada, febre, emagrecimento, entre outras manifestações sistêmicas e pode estar associada a malignidades, entre as quais a síndrome de POEMS (polineuropatia, organomegalia, endocrinopatia, gamopatia monoclonal e alterações de pele). Relatamos o caso de um homem de 50 anos que se apresentava com emagrecimento, febre e linfadenopatia, associado a gamopatia monoclonal, organomegalia, endocrinopatia e neuropatia, cujo diagnóstico foi de Doença de Castleman cursando com síndrome de POEMS.HCPA/FAMED/UFRGS2008-08-27info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed ArticleAvaliado por paresapplication/pdfhttps://seer.ufrgs.br/index.php/hcpa/article/view/3976Clinical & Biomedical Research; Vol. 28 No. 2 (2008): Revista HCPAClinical and Biomedical Research; v. 28 n. 2 (2008): Revista HCPA2357-9730reponame:Clinical and Biomedical Researchinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSporhttps://seer.ufrgs.br/index.php/hcpa/article/view/3976/3405Fontana, BiancaZanella, AndréPrezzi, Sérgioinfo:eu-repo/semantics/openAccess2020-01-16T16:16:53Zoai:seer.ufrgs.br:article/3976Revistahttps://www.seer.ufrgs.br/index.php/hcpaPUBhttps://seer.ufrgs.br/index.php/hcpa/oai||cbr@hcpa.edu.br2357-97302357-9730opendoar:2020-01-16T16:16:53Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.none.fl_str_mv Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
Doença de Castleman e Síndrome de POEMS: relato de caso e revisão da literatura
title Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
spellingShingle Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
Fontana, Bianca
Doença de Castleman
Síndrome de POEMS
E01.370.374.050
title_short Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
title_full Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
title_fullStr Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
title_full_unstemmed Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
title_sort Castleman`s Disease and POEMS Syndrome: case reporte and review of literature
author Fontana, Bianca
author_facet Fontana, Bianca
Zanella, André
Prezzi, Sérgio
author_role author
author2 Zanella, André
Prezzi, Sérgio
author2_role author
author
dc.contributor.author.fl_str_mv Fontana, Bianca
Zanella, André
Prezzi, Sérgio
dc.subject.por.fl_str_mv Doença de Castleman
Síndrome de POEMS
E01.370.374.050
topic Doença de Castleman
Síndrome de POEMS
E01.370.374.050
description Castleman’s disease is a lymphoproliferative disorder related with human herpesvirus 8 and HIV, presenting in two different ways. The unicentric form is benign, doesn’t have systemic symptoms and is usually cured with surgery. The multicentric form usually presents with generalized lymphadenopathy, fever, weight loss, and other systemic manifestations and it can be associated with malignancy, especially POEMS syndrome. We report a case of a 50 year old man presenting with weight loss, fever and lymphadenopathy, associated with monoclonal gammopathy, organomegaly, endocrinopathy and neuropathy, which diagnosis was Castleman’s disease with POEMS syndrome
publishDate 2008
dc.date.none.fl_str_mv 2008-08-27
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed Article
Avaliado por pares
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/3976
url https://seer.ufrgs.br/index.php/hcpa/article/view/3976
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/3976/3405
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv HCPA/FAMED/UFRGS
publisher.none.fl_str_mv HCPA/FAMED/UFRGS
dc.source.none.fl_str_mv Clinical & Biomedical Research; Vol. 28 No. 2 (2008): Revista HCPA
Clinical and Biomedical Research; v. 28 n. 2 (2008): Revista HCPA
2357-9730
reponame:Clinical and Biomedical Research
instname:Universidade Federal do Rio Grande do Sul (UFRGS)
instacron:UFRGS
instname_str Universidade Federal do Rio Grande do Sul (UFRGS)
instacron_str UFRGS
institution UFRGS
reponame_str Clinical and Biomedical Research
collection Clinical and Biomedical Research
repository.name.fl_str_mv Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)
repository.mail.fl_str_mv ||cbr@hcpa.edu.br
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