Cardiac involvement in Erdheim-Chester disease : a case report

Detalhes bibliográficos
Autor(a) principal: Pivatto Junior, Fernando
Data de Publicação: 2014
Outros Autores: Piardi, Diogo Silva, Torres, Felipe Soares
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UFRGS
Texto Completo: http://hdl.handle.net/10183/158942
Resumo: Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.
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spelling Pivatto Junior, FernandoPiardi, Diogo SilvaTorres, Felipe Soares2017-06-01T02:36:26Z20142357-9730http://hdl.handle.net/10183/158942001013789Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.application/pdfengClinical and biomedical research. Porto Alegre. Vol. 34, n. 4, (2014), p. 406-409Doença de Erdheim-ChesterInsuficiência cardíacaImagem por ressonância magnéticaErdheim-Chester diseaseHeart failureMagnetic resonance imagingCardiac involvement in Erdheim-Chester disease : a case reportinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/otherinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UFRGSinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSORIGINAL001013789.pdf001013789.pdfTexto completo (inglês)application/pdf1503259http://www.lume.ufrgs.br/bitstream/10183/158942/1/001013789.pdf094f765a7b0636a8d6e14d659bc6c833MD51TEXT001013789.pdf.txt001013789.pdf.txtExtracted Texttext/plain12771http://www.lume.ufrgs.br/bitstream/10183/158942/2/001013789.pdf.txtecac6897719d6707cefdfe0a164a5975MD5210183/1589422021-05-07 04:55:19.030822oai:www.lume.ufrgs.br:10183/158942Repositório de PublicaçõesPUBhttps://lume.ufrgs.br/oai/requestopendoar:2021-05-07T07:55:19Repositório Institucional da UFRGS - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.pt_BR.fl_str_mv Cardiac involvement in Erdheim-Chester disease : a case report
title Cardiac involvement in Erdheim-Chester disease : a case report
spellingShingle Cardiac involvement in Erdheim-Chester disease : a case report
Pivatto Junior, Fernando
Doença de Erdheim-Chester
Insuficiência cardíaca
Imagem por ressonância magnética
Erdheim-Chester disease
Heart failure
Magnetic resonance imaging
title_short Cardiac involvement in Erdheim-Chester disease : a case report
title_full Cardiac involvement in Erdheim-Chester disease : a case report
title_fullStr Cardiac involvement in Erdheim-Chester disease : a case report
title_full_unstemmed Cardiac involvement in Erdheim-Chester disease : a case report
title_sort Cardiac involvement in Erdheim-Chester disease : a case report
author Pivatto Junior, Fernando
author_facet Pivatto Junior, Fernando
Piardi, Diogo Silva
Torres, Felipe Soares
author_role author
author2 Piardi, Diogo Silva
Torres, Felipe Soares
author2_role author
author
dc.contributor.author.fl_str_mv Pivatto Junior, Fernando
Piardi, Diogo Silva
Torres, Felipe Soares
dc.subject.por.fl_str_mv Doença de Erdheim-Chester
Insuficiência cardíaca
Imagem por ressonância magnética
topic Doença de Erdheim-Chester
Insuficiência cardíaca
Imagem por ressonância magnética
Erdheim-Chester disease
Heart failure
Magnetic resonance imaging
dc.subject.eng.fl_str_mv Erdheim-Chester disease
Heart failure
Magnetic resonance imaging
description Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.
publishDate 2014
dc.date.issued.fl_str_mv 2014
dc.date.accessioned.fl_str_mv 2017-06-01T02:36:26Z
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dc.language.iso.fl_str_mv eng
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dc.relation.ispartof.pt_BR.fl_str_mv Clinical and biomedical research. Porto Alegre. Vol. 34, n. 4, (2014), p. 406-409
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