Gastaut type idiopathic childhood occipital epilepsy

• Autor(a) principal: Ferrari-Marinho, Taissa [UNIFESP]
• Data de Publicação: 2013
• Outros Autores: Macedo, Eugenia Fialho [UNIFESP], Neves, Rafael Scarpa da Costa [UNIFESP], Costa, Livia Vianez [UNIFESP], Tudesco, Ivanda de Souza Silva [UNIFESP], Carvalho, Kelly C. [UNIFESP], Carrete, Henrique [UNIFESP], Caboclo, Luis Otávio [UNIFESP], Yacubian, Elza Márcia Targas [UNIFESP], Hamad, Ana Paula [UNIFESP]
• Tipo de documento: Artigo
• Idioma: eng
• Título da fonte: Repositório Institucional da UNIFESP
• Texto Completo: http://dx.doi.org/10.1684/epd.2013.0551; http://repositorio.unifesp.br/handle/11600/36010
• topic: idiopathic childhood epilepsy; Gastaut type epilepsy; video-EEG

Gastaut type idiopathic childhood occipital epilepsy is an uncommon epileptic syndrome characterised by frequent seizures, most commonly presenting as elementary visual hallucinations or blindness. Other occipital (non-visual) symptoms may also occur. Interictal EEG typically shows occipital paroxysms, often with fixation-off sensitivity. Ictal EEG is usually characterised by interruption by paroxysms and sudden appearance of low-voltage, occipital, fast rhythm and/or spikes. Despite well described clinical and EEG patterns, to our knowledge, there are very few reports in the literature with video-EEG recording of either seizure semiology or fixation-off phenomena. We present a video-EEG recording of a 12-year-old girl with Gastaut type epilepsy, illustrating the interictal and ictal aspects of this syndrome. Our aim was to demonstrate the clinical and neurophysiological pattern of a typical seizure of Gastaut type epilepsy, as well as the fixation-off phenomena, in order to further clarify the typical presentation of this syndrome. [Published with video sequences]