Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report

Detalhes bibliográficos
Autor(a) principal: Andrade, Guilherme Cabral de [UNIFESP]
Data de Publicação: 2003
Outros Autores: Braga, Otávio Piccirillo [UNIFESP], Hisatugo, Marcelo Ken-Iti [UNIFESP], Paiva Neto, Manoel Antonio de [UNIFESP], Succi, Ernesto [UNIFESP], Braga, Fernando Menezes [UNIFESP]
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UNIFESP
Texto Completo: http://repositorio.unifesp.br/handle/11600/1825
http://dx.doi.org/10.1590/S0004-282X2003000400029
Resumo: Meningocele intratorácica é patologia rara e, quando presente, está quase sempre associada a neurofibromatose tipo I. Há poucos casos descritos na literatura e em sua maioria destes são de cistos pequenos ou assintomáticos, sendo a cirurgia indicada quando são grandes ou sintomáticos. Relatamos o caso de um homem de 59 anos com a doença de Von Recklinghausen familiar, com cistos gigantes extirpados cirurgicamente através de toracotomia.
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spelling Andrade, Guilherme Cabral de [UNIFESP]Braga, Otávio Piccirillo [UNIFESP]Hisatugo, Marcelo Ken-Iti [UNIFESP]Paiva Neto, Manoel Antonio de [UNIFESP]Succi, Ernesto [UNIFESP]Braga, Fernando Menezes [UNIFESP]Universidade Federal de São Paulo (UNIFESP)2015-06-14T13:30:06Z2015-06-14T13:30:06Z2003-09-01Arquivos de Neuro-Psiquiatria. Academia Brasileira de Neurologia - ABNEURO, v. 61, n. 3A, p. 677-681, 2003.0004-282Xhttp://repositorio.unifesp.br/handle/11600/1825http://dx.doi.org/10.1590/S0004-282X2003000400029S0004-282X2003000400029.pdfS0004-282X200300040002910.1590/S0004-282X2003000400029WOS:000186186300029Meningocele intratorácica é patologia rara e, quando presente, está quase sempre associada a neurofibromatose tipo I. Há poucos casos descritos na literatura e em sua maioria destes são de cistos pequenos ou assintomáticos, sendo a cirurgia indicada quando são grandes ou sintomáticos. Relatamos o caso de um homem de 59 anos com a doença de Von Recklinghausen familiar, com cistos gigantes extirpados cirurgicamente através de toracotomia.BACKGROUND: Intrathoracic meningocele is a rare pathology, almost always associated with neurofibromatosis type I and with a few cases related in the literature. In the majority of cases cysts are small or asymptomatic, and the surgery is indicated when big or symptomatic cysts are present. We report a case of giant intrathoracic cysts surgically extirpated through out thoracotomy. CASE: A 59-year-old male with familiar Von Recklinghausen's disease which developed thoracic radicular pain after a fall. On examination he presented some difficulty in walking fast and dyspneia on small efforts. The chest plain x-ray showed the presence of 3 huge left side intrathoracic cysts (10 to 15cm). The patient was submitted to a surgical treatment and complete extirpation of the cysts was performed through a left side thoracotomy. During the surgery a fourth smaller cyst was detected and also extirpated. Evolution was uneventful and the patient remains well in these last 12 years. This finding of intrathoracic cysts related to neurofibromatosis type I is rare and is probably unique in the literature the presence of 4 huge cysts in one side of the thorax.Federal University of São Paulo EPMUNIFESP, EPMSciELO677-681engAcademia Brasileira de Neurologia - ABNEUROArquivos de Neuro-Psiquiatriameningocele intratorácicaneurofibromatose tipo Iintrathoracic meningoceleneurofibromatosis type IGiant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case reportMeningoceles intratorácicas gigantes associadas a neurofibromatose tipo I: relato de casoinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleinfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UNIFESPinstname:Universidade Federal de São Paulo (UNIFESP)instacron:UNIFESPORIGINALS0004-282X2003000400029.pdfapplication/pdf208401${dspace.ui.url}/bitstream/11600/1825/1/S0004-282X2003000400029.pdf8ce4294bfafbaffbab666be7cf40a556MD51open accessTEXTS0004-282X2003000400029.pdf.txtS0004-282X2003000400029.pdf.txtExtracted texttext/plain19131${dspace.ui.url}/bitstream/11600/1825/2/S0004-282X2003000400029.pdf.txte7945921449a95e2a1db22ea908c1909MD52open access11600/18252022-09-27 09:48:34.624open accessoai:repositorio.unifesp.br:11600/1825Repositório InstitucionalPUBhttp://www.repositorio.unifesp.br/oai/requestopendoar:34652023-05-25T12:23:33.645221Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)false
dc.title.en.fl_str_mv Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
dc.title.alternative.pt.fl_str_mv Meningoceles intratorácicas gigantes associadas a neurofibromatose tipo I: relato de caso
title Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
spellingShingle Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
Andrade, Guilherme Cabral de [UNIFESP]
meningocele intratorácica
neurofibromatose tipo I
intrathoracic meningocele
neurofibromatosis type I
title_short Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
title_full Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
title_fullStr Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
title_full_unstemmed Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
title_sort Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report
author Andrade, Guilherme Cabral de [UNIFESP]
author_facet Andrade, Guilherme Cabral de [UNIFESP]
Braga, Otávio Piccirillo [UNIFESP]
Hisatugo, Marcelo Ken-Iti [UNIFESP]
Paiva Neto, Manoel Antonio de [UNIFESP]
Succi, Ernesto [UNIFESP]
Braga, Fernando Menezes [UNIFESP]
author_role author
author2 Braga, Otávio Piccirillo [UNIFESP]
Hisatugo, Marcelo Ken-Iti [UNIFESP]
Paiva Neto, Manoel Antonio de [UNIFESP]
Succi, Ernesto [UNIFESP]
Braga, Fernando Menezes [UNIFESP]
author2_role author
author
author
author
author
dc.contributor.institution.none.fl_str_mv Universidade Federal de São Paulo (UNIFESP)
dc.contributor.author.fl_str_mv Andrade, Guilherme Cabral de [UNIFESP]
Braga, Otávio Piccirillo [UNIFESP]
Hisatugo, Marcelo Ken-Iti [UNIFESP]
Paiva Neto, Manoel Antonio de [UNIFESP]
Succi, Ernesto [UNIFESP]
Braga, Fernando Menezes [UNIFESP]
dc.subject.por.fl_str_mv meningocele intratorácica
neurofibromatose tipo I
topic meningocele intratorácica
neurofibromatose tipo I
intrathoracic meningocele
neurofibromatosis type I
dc.subject.eng.fl_str_mv intrathoracic meningocele
neurofibromatosis type I
description Meningocele intratorácica é patologia rara e, quando presente, está quase sempre associada a neurofibromatose tipo I. Há poucos casos descritos na literatura e em sua maioria destes são de cistos pequenos ou assintomáticos, sendo a cirurgia indicada quando são grandes ou sintomáticos. Relatamos o caso de um homem de 59 anos com a doença de Von Recklinghausen familiar, com cistos gigantes extirpados cirurgicamente através de toracotomia.
publishDate 2003
dc.date.issued.fl_str_mv 2003-09-01
dc.date.accessioned.fl_str_mv 2015-06-14T13:30:06Z
dc.date.available.fl_str_mv 2015-06-14T13:30:06Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.citation.fl_str_mv Arquivos de Neuro-Psiquiatria. Academia Brasileira de Neurologia - ABNEURO, v. 61, n. 3A, p. 677-681, 2003.
dc.identifier.uri.fl_str_mv http://repositorio.unifesp.br/handle/11600/1825
http://dx.doi.org/10.1590/S0004-282X2003000400029
dc.identifier.issn.none.fl_str_mv 0004-282X
dc.identifier.file.none.fl_str_mv S0004-282X2003000400029.pdf
dc.identifier.scielo.none.fl_str_mv S0004-282X2003000400029
dc.identifier.doi.none.fl_str_mv 10.1590/S0004-282X2003000400029
dc.identifier.wos.none.fl_str_mv WOS:000186186300029
identifier_str_mv Arquivos de Neuro-Psiquiatria. Academia Brasileira de Neurologia - ABNEURO, v. 61, n. 3A, p. 677-681, 2003.
0004-282X
S0004-282X2003000400029.pdf
S0004-282X2003000400029
10.1590/S0004-282X2003000400029
WOS:000186186300029
url http://repositorio.unifesp.br/handle/11600/1825
http://dx.doi.org/10.1590/S0004-282X2003000400029
dc.language.iso.fl_str_mv eng
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dc.relation.ispartof.none.fl_str_mv Arquivos de Neuro-Psiquiatria
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv 677-681
dc.publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
dc.source.none.fl_str_mv reponame:Repositório Institucional da UNIFESP
instname:Universidade Federal de São Paulo (UNIFESP)
instacron:UNIFESP
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instacron_str UNIFESP
institution UNIFESP
reponame_str Repositório Institucional da UNIFESP
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