Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Autor(a) principal: | |
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Data de Publicação: | 2012 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Institucional da UNIFESP |
dARK ID: | ark:/48912/001300000vpvg |
DOI: | 10.1590/S0004-27492012000200015 |
Texto Completo: | http://dx.doi.org/10.1590/S0004-27492012000200015 http://repositorio.unifesp.br/handle/11600/7072 |
Resumo: | A case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization. |
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Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de casoIdiopathic retinal, vasculitis, aneurysms and neuroretinitis (IRVAN): case reportUveitisRetinitisAneurysmRetinal vasculitisFluorescein angiographyGlucocorticoidsSyndromeHumansMaleAdolescentCase reportsUveíteRetiniteAneurismaVasculite retinianaAngiofluoresceinografiaGlucocorticoidesSíndromeHumanosMasculinoAdolescenteRelato de casosA case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization.Relatamos caso de um paciente de 14 anos, sexo masculino, que foi admitido com queixa de embaçamento visual bilateral há dois anos. Ao exame oftalmológico observou-se leve hiperemia e edema de disco óptico bilateral, exsudação retiniana, poucas hemorragias retinianas, múltiplos aneurismas, assim como sinais de vasculite. A angiofluoresceinografia demonstrou isquemia periférica extensa, dilatações e hiperfluorescência das paredes dos vasos, e vazamento tardio do disco óptico nas fases finais do exame em ambos os olhos. Este caso representa uma rara entidade caracterizada por oclusão retiniana vascular periférica, vasculite retiniana, múltiplos aneurismas retinianos e neurorretinite (IRVAN). Avaliação sistêmica e laboratorial não revelaram nenhuma anormalidade. O paciente foi submetido à panfotocoagulação de retina com laser de argônio em ambos os olhos, e iniciado tratamento com prednisona via oral, com manutenção da acuidade visual de 20/25 depois de um ano de acompanhamento. O tratamento com laser deve ser considerado quando houver qualquer evidência angiográfica de má perfusão retiniana, e antes do desenvolvimento de qualquer sinal de neovascularização de retina.Universidade Federal de São Paulo (UNIFESP)UNIFESPSciELOConselho Brasileiro de OftalmologiaUniversidade Federal de São Paulo (UNIFESP)Rodrigues, Kelly Fernandes de Paula [UNIFESP]Lima, Verônica Castro [UNIFESP]Arantes, Tiago Eugênio Faria e [UNIFESP]Matos, Kimble Teixeira Fonseca [UNIFESP]Muccioli, Cristina [UNIFESP]2015-06-14T13:43:43Z2015-06-14T13:43:43Z2012-04-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersion140-142application/pdfhttp://dx.doi.org/10.1590/S0004-27492012000200015Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012.10.1590/S0004-27492012000200015S0004-27492012000200015.pdf0004-2749S0004-27492012000200015http://repositorio.unifesp.br/handle/11600/7072WOS:000310841600015ark:/48912/001300000vpvgporArquivos Brasileiros de Oftalmologiainfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UNIFESPinstname:Universidade Federal de São Paulo (UNIFESP)instacron:UNIFESP2024-08-05T04:56:54Zoai:repositorio.unifesp.br/:11600/7072Repositório InstitucionalPUBhttp://www.repositorio.unifesp.br/oai/requestbiblioteca.csp@unifesp.bropendoar:34652024-12-11T20:39:48.856874Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)false |
dc.title.none.fl_str_mv |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso Idiopathic retinal, vasculitis, aneurysms and neuroretinitis (IRVAN): case report |
title |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
spellingShingle |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso Rodrigues, Kelly Fernandes de Paula [UNIFESP] Uveitis Retinitis Aneurysm Retinal vasculitis Fluorescein angiography Glucocorticoids Syndrome Humans Male Adolescent Case reports Uveíte Retinite Aneurisma Vasculite retiniana Angiofluoresceinografia Glucocorticoides Síndrome Humanos Masculino Adolescente Relato de casos Rodrigues, Kelly Fernandes de Paula [UNIFESP] Uveitis Retinitis Aneurysm Retinal vasculitis Fluorescein angiography Glucocorticoids Syndrome Humans Male Adolescent Case reports Uveíte Retinite Aneurisma Vasculite retiniana Angiofluoresceinografia Glucocorticoides Síndrome Humanos Masculino Adolescente Relato de casos |
title_short |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
title_full |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
title_fullStr |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
title_full_unstemmed |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
title_sort |
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso |
author |
Rodrigues, Kelly Fernandes de Paula [UNIFESP] |
author_facet |
Rodrigues, Kelly Fernandes de Paula [UNIFESP] Rodrigues, Kelly Fernandes de Paula [UNIFESP] Lima, Verônica Castro [UNIFESP] Arantes, Tiago Eugênio Faria e [UNIFESP] Matos, Kimble Teixeira Fonseca [UNIFESP] Muccioli, Cristina [UNIFESP] Lima, Verônica Castro [UNIFESP] Arantes, Tiago Eugênio Faria e [UNIFESP] Matos, Kimble Teixeira Fonseca [UNIFESP] Muccioli, Cristina [UNIFESP] |
author_role |
author |
author2 |
Lima, Verônica Castro [UNIFESP] Arantes, Tiago Eugênio Faria e [UNIFESP] Matos, Kimble Teixeira Fonseca [UNIFESP] Muccioli, Cristina [UNIFESP] |
author2_role |
author author author author |
dc.contributor.none.fl_str_mv |
Universidade Federal de São Paulo (UNIFESP) |
dc.contributor.author.fl_str_mv |
Rodrigues, Kelly Fernandes de Paula [UNIFESP] Lima, Verônica Castro [UNIFESP] Arantes, Tiago Eugênio Faria e [UNIFESP] Matos, Kimble Teixeira Fonseca [UNIFESP] Muccioli, Cristina [UNIFESP] |
dc.subject.por.fl_str_mv |
Uveitis Retinitis Aneurysm Retinal vasculitis Fluorescein angiography Glucocorticoids Syndrome Humans Male Adolescent Case reports Uveíte Retinite Aneurisma Vasculite retiniana Angiofluoresceinografia Glucocorticoides Síndrome Humanos Masculino Adolescente Relato de casos |
topic |
Uveitis Retinitis Aneurysm Retinal vasculitis Fluorescein angiography Glucocorticoids Syndrome Humans Male Adolescent Case reports Uveíte Retinite Aneurisma Vasculite retiniana Angiofluoresceinografia Glucocorticoides Síndrome Humanos Masculino Adolescente Relato de casos |
description |
A case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization. |
publishDate |
2012 |
dc.date.none.fl_str_mv |
2012-04-01 2015-06-14T13:43:43Z 2015-06-14T13:43:43Z |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://dx.doi.org/10.1590/S0004-27492012000200015 Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012. 10.1590/S0004-27492012000200015 S0004-27492012000200015.pdf 0004-2749 S0004-27492012000200015 http://repositorio.unifesp.br/handle/11600/7072 WOS:000310841600015 |
dc.identifier.dark.fl_str_mv |
ark:/48912/001300000vpvg |
url |
http://dx.doi.org/10.1590/S0004-27492012000200015 http://repositorio.unifesp.br/handle/11600/7072 |
identifier_str_mv |
Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012. 10.1590/S0004-27492012000200015 S0004-27492012000200015.pdf 0004-2749 S0004-27492012000200015 WOS:000310841600015 ark:/48912/001300000vpvg |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
Arquivos Brasileiros de Oftalmologia |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
140-142 application/pdf |
dc.publisher.none.fl_str_mv |
Conselho Brasileiro de Oftalmologia |
publisher.none.fl_str_mv |
Conselho Brasileiro de Oftalmologia |
dc.source.none.fl_str_mv |
reponame:Repositório Institucional da UNIFESP instname:Universidade Federal de São Paulo (UNIFESP) instacron:UNIFESP |
instname_str |
Universidade Federal de São Paulo (UNIFESP) |
instacron_str |
UNIFESP |
institution |
UNIFESP |
reponame_str |
Repositório Institucional da UNIFESP |
collection |
Repositório Institucional da UNIFESP |
repository.name.fl_str_mv |
Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP) |
repository.mail.fl_str_mv |
biblioteca.csp@unifesp.br |
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1822251075022880768 |
dc.identifier.doi.none.fl_str_mv |
10.1590/S0004-27492012000200015 |