Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso

Detalhes bibliográficos
Autor(a) principal: Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Data de Publicação: 2012
Outros Autores: Lima, Verônica Castro [UNIFESP], Arantes, Tiago Eugênio Faria e [UNIFESP], Matos, Kimble Teixeira Fonseca [UNIFESP], Muccioli, Cristina [UNIFESP]
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Institucional da UNIFESP
dARK ID: ark:/48912/001300000vpvg
DOI: 10.1590/S0004-27492012000200015
Texto Completo: http://dx.doi.org/10.1590/S0004-27492012000200015
http://repositorio.unifesp.br/handle/11600/7072
Resumo: A case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization.
id UFSP_b5375c59ad6d60d2f100544b099d2cee
oai_identifier_str oai:repositorio.unifesp.br/:11600/7072
network_acronym_str UFSP
network_name_str Repositório Institucional da UNIFESP
repository_id_str 3465
spelling Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de casoIdiopathic retinal, vasculitis, aneurysms and neuroretinitis (IRVAN): case reportUveitisRetinitisAneurysmRetinal vasculitisFluorescein angiographyGlucocorticoidsSyndromeHumansMaleAdolescentCase reportsUveíteRetiniteAneurismaVasculite retinianaAngiofluoresceinografiaGlucocorticoidesSíndromeHumanosMasculinoAdolescenteRelato de casosA case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization.Relatamos caso de um paciente de 14 anos, sexo masculino, que foi admitido com queixa de embaçamento visual bilateral há dois anos. Ao exame oftalmológico observou-se leve hiperemia e edema de disco óptico bilateral, exsudação retiniana, poucas hemorragias retinianas, múltiplos aneurismas, assim como sinais de vasculite. A angiofluoresceinografia demonstrou isquemia periférica extensa, dilatações e hiperfluorescência das paredes dos vasos, e vazamento tardio do disco óptico nas fases finais do exame em ambos os olhos. Este caso representa uma rara entidade caracterizada por oclusão retiniana vascular periférica, vasculite retiniana, múltiplos aneurismas retinianos e neurorretinite (IRVAN). Avaliação sistêmica e laboratorial não revelaram nenhuma anormalidade. O paciente foi submetido à panfotocoagulação de retina com laser de argônio em ambos os olhos, e iniciado tratamento com prednisona via oral, com manutenção da acuidade visual de 20/25 depois de um ano de acompanhamento. O tratamento com laser deve ser considerado quando houver qualquer evidência angiográfica de má perfusão retiniana, e antes do desenvolvimento de qualquer sinal de neovascularização de retina.Universidade Federal de São Paulo (UNIFESP)UNIFESPSciELOConselho Brasileiro de OftalmologiaUniversidade Federal de São Paulo (UNIFESP)Rodrigues, Kelly Fernandes de Paula [UNIFESP]Lima, Verônica Castro [UNIFESP]Arantes, Tiago Eugênio Faria e [UNIFESP]Matos, Kimble Teixeira Fonseca [UNIFESP]Muccioli, Cristina [UNIFESP]2015-06-14T13:43:43Z2015-06-14T13:43:43Z2012-04-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersion140-142application/pdfhttp://dx.doi.org/10.1590/S0004-27492012000200015Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012.10.1590/S0004-27492012000200015S0004-27492012000200015.pdf0004-2749S0004-27492012000200015http://repositorio.unifesp.br/handle/11600/7072WOS:000310841600015ark:/48912/001300000vpvgporArquivos Brasileiros de Oftalmologiainfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UNIFESPinstname:Universidade Federal de São Paulo (UNIFESP)instacron:UNIFESP2024-08-05T04:56:54Zoai:repositorio.unifesp.br/:11600/7072Repositório InstitucionalPUBhttp://www.repositorio.unifesp.br/oai/requestbiblioteca.csp@unifesp.bropendoar:34652024-12-11T20:39:48.856874Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)false
dc.title.none.fl_str_mv Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Idiopathic retinal, vasculitis, aneurysms and neuroretinitis (IRVAN): case report
title Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
spellingShingle Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Uveitis
Retinitis
Aneurysm
Retinal vasculitis
Fluorescein angiography
Glucocorticoids
Syndrome
Humans
Male
Adolescent
Case reports
Uveíte
Retinite
Aneurisma
Vasculite retiniana
Angiofluoresceinografia
Glucocorticoides
Síndrome
Humanos
Masculino
Adolescente
Relato de casos
Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Uveitis
Retinitis
Aneurysm
Retinal vasculitis
Fluorescein angiography
Glucocorticoids
Syndrome
Humans
Male
Adolescent
Case reports
Uveíte
Retinite
Aneurisma
Vasculite retiniana
Angiofluoresceinografia
Glucocorticoides
Síndrome
Humanos
Masculino
Adolescente
Relato de casos
title_short Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
title_full Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
title_fullStr Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
title_full_unstemmed Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
title_sort Retinite idiopática, vasculite, aneurismas e neurorretinite (IRVAN): relato de caso
author Rodrigues, Kelly Fernandes de Paula [UNIFESP]
author_facet Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Lima, Verônica Castro [UNIFESP]
Arantes, Tiago Eugênio Faria e [UNIFESP]
Matos, Kimble Teixeira Fonseca [UNIFESP]
Muccioli, Cristina [UNIFESP]
Lima, Verônica Castro [UNIFESP]
Arantes, Tiago Eugênio Faria e [UNIFESP]
Matos, Kimble Teixeira Fonseca [UNIFESP]
Muccioli, Cristina [UNIFESP]
author_role author
author2 Lima, Verônica Castro [UNIFESP]
Arantes, Tiago Eugênio Faria e [UNIFESP]
Matos, Kimble Teixeira Fonseca [UNIFESP]
Muccioli, Cristina [UNIFESP]
author2_role author
author
author
author
dc.contributor.none.fl_str_mv Universidade Federal de São Paulo (UNIFESP)
dc.contributor.author.fl_str_mv Rodrigues, Kelly Fernandes de Paula [UNIFESP]
Lima, Verônica Castro [UNIFESP]
Arantes, Tiago Eugênio Faria e [UNIFESP]
Matos, Kimble Teixeira Fonseca [UNIFESP]
Muccioli, Cristina [UNIFESP]
dc.subject.por.fl_str_mv Uveitis
Retinitis
Aneurysm
Retinal vasculitis
Fluorescein angiography
Glucocorticoids
Syndrome
Humans
Male
Adolescent
Case reports
Uveíte
Retinite
Aneurisma
Vasculite retiniana
Angiofluoresceinografia
Glucocorticoides
Síndrome
Humanos
Masculino
Adolescente
Relato de casos
topic Uveitis
Retinitis
Aneurysm
Retinal vasculitis
Fluorescein angiography
Glucocorticoids
Syndrome
Humans
Male
Adolescent
Case reports
Uveíte
Retinite
Aneurisma
Vasculite retiniana
Angiofluoresceinografia
Glucocorticoides
Síndrome
Humanos
Masculino
Adolescente
Relato de casos
description A case of a 14 year-old boy that was admitted complaining of bilateral ocular visual blurring for 2 years is reported. The ophthalmological examination disclosed bilateral mild optic disc hyperemia and swelling, retinal exudation, few retinal hemorrhages, multiple aneurysms, as well as vasculitis. Fluorescein angiography showed extensive peripheral retinal ischemia, dilatations and hyperfluorescence of the vessels walls, and leakage of the optic disc in the late phases in both eyes. This rare case represents an entity characterized by peripheral retinal vascular occlusion, retinal vasculitis, multiple posterior retinal aneurysms, and neuroretinitis (IRVAN). Systemic evaluation and laboratory work-up did not suggest any systemic abnormality. Panretinal laser photocoagulation was performed in both eyes, and the patient was treated with oral prednisone with maintenance of the visual acuity after 1 year of follow-up. Laser treatment should be considered when angiographic evidence of widespread retinal no perfusion is present, and before the development of signs of retinal neovascularization.
publishDate 2012
dc.date.none.fl_str_mv 2012-04-01
2015-06-14T13:43:43Z
2015-06-14T13:43:43Z
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://dx.doi.org/10.1590/S0004-27492012000200015
Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012.
10.1590/S0004-27492012000200015
S0004-27492012000200015.pdf
0004-2749
S0004-27492012000200015
http://repositorio.unifesp.br/handle/11600/7072
WOS:000310841600015
dc.identifier.dark.fl_str_mv ark:/48912/001300000vpvg
url http://dx.doi.org/10.1590/S0004-27492012000200015
http://repositorio.unifesp.br/handle/11600/7072
identifier_str_mv Arquivos Brasileiros de Oftalmologia. Conselho Brasileiro de Oftalmologia, v. 75, n. 2, p. 140-142, 2012.
10.1590/S0004-27492012000200015
S0004-27492012000200015.pdf
0004-2749
S0004-27492012000200015
WOS:000310841600015
ark:/48912/001300000vpvg
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv Arquivos Brasileiros de Oftalmologia
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv 140-142
application/pdf
dc.publisher.none.fl_str_mv Conselho Brasileiro de Oftalmologia
publisher.none.fl_str_mv Conselho Brasileiro de Oftalmologia
dc.source.none.fl_str_mv reponame:Repositório Institucional da UNIFESP
instname:Universidade Federal de São Paulo (UNIFESP)
instacron:UNIFESP
instname_str Universidade Federal de São Paulo (UNIFESP)
instacron_str UNIFESP
institution UNIFESP
reponame_str Repositório Institucional da UNIFESP
collection Repositório Institucional da UNIFESP
repository.name.fl_str_mv Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)
repository.mail.fl_str_mv biblioteca.csp@unifesp.br
_version_ 1822251075022880768
dc.identifier.doi.none.fl_str_mv 10.1590/S0004-27492012000200015