Patient suspected susceptibility to malignant hyperthermia: impact of the disease
Autor(a) principal: | |
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Data de Publicação: | 2023 |
Outros Autores: | , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Institucional da UNIFESP |
Texto Completo: | https://www.sciencedirect.com/science/article/pii/S0104001422000033?via%3Dihub https://repositorio.unifesp.br/11600/67327 |
Resumo: | Introduction Malignant Hyperthermia (MH) is an inherited hypermetabolic syndrome triggered by exposure to halogenated anesthetics/succinylcholine. The lack of knowledge regarding this condition might be associated with the rare occurrence of MH reaction and symptoms. Methods This observational study evaluated 68 patients from 48 families with confirmed or suspected MH susceptibility due to medical history of MH reaction or idiopathic increase of creatine kinase or MH-related myopathies. Participants were assessed by a standardized questionnaire and submitted to physical/neurological examination to assess the characteristics of patients with MH, their knowledge about the disease, and the impact suspected MH had on their daily lives. Results Suspected MH impacted the daily life of 50% of patients, creating difficulties in performing surgical/clinical/dental treatment and problems related to their family life/working/practicing sports. The questionnaire on MH revealed a correct answer score of 62.1 ± 20.8 (mean ± standard deviation) on a scale 0 to 100. Abnormal physical/neurological examination findings were detected in 92.6% of susceptible patients. Conclusions Suspected MH had impacted the daily lives of most patients, with patients reporting problems even before MH investigation with IVCT. Patients showed a moderate level of knowledge about MH, suggesting the need to implement continuing education programs. MH susceptible patients require regular follow-up by a health team to detect abnormalities during physical and neurological examination. |
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Rodrigues, Gislene [UNIFESP]Andrade, Pamela Vieira [UNIFESP]Santos, Joilson Moura dos [UNIFESP]Castro, Isac de [UNIFESP]Amaral, Jose Luiz Gomes do [UNIFESP]Silva, Helga Cristina Almeida da [UNIFESP]http://lattes.cnpq.br/08449188622411022023-04-03T15:21:57Z2023-04-03T15:21:57Z2023-03https://www.sciencedirect.com/science/article/pii/S0104001422000033?via%3Dihubhttps://repositorio.unifesp.br/11600/6732710.1016/j.bjane.2021.10.021Introduction Malignant Hyperthermia (MH) is an inherited hypermetabolic syndrome triggered by exposure to halogenated anesthetics/succinylcholine. The lack of knowledge regarding this condition might be associated with the rare occurrence of MH reaction and symptoms. Methods This observational study evaluated 68 patients from 48 families with confirmed or suspected MH susceptibility due to medical history of MH reaction or idiopathic increase of creatine kinase or MH-related myopathies. Participants were assessed by a standardized questionnaire and submitted to physical/neurological examination to assess the characteristics of patients with MH, their knowledge about the disease, and the impact suspected MH had on their daily lives. Results Suspected MH impacted the daily life of 50% of patients, creating difficulties in performing surgical/clinical/dental treatment and problems related to their family life/working/practicing sports. The questionnaire on MH revealed a correct answer score of 62.1 ± 20.8 (mean ± standard deviation) on a scale 0 to 100. Abnormal physical/neurological examination findings were detected in 92.6% of susceptible patients. Conclusions Suspected MH had impacted the daily lives of most patients, with patients reporting problems even before MH investigation with IVCT. Patients showed a moderate level of knowledge about MH, suggesting the need to implement continuing education programs. MH susceptible patients require regular follow-up by a health team to detect abnormalities during physical and neurological examination.Fundação de Amparo à Pesquisa do Estado de São Paulo (FAPESP)0012021_06180-7engSBABrazilian Journal of AnesthesiologyAnesthesiaHealth educationMalignant hyperthermiaPatient suspected susceptibility to malignant hyperthermia: impact of the diseaseinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article732info:eu-repo/semantics/openAccessreponame:Repositório Institucional da UNIFESPinstname:Universidade Federal de São Paulo (UNIFESP)instacron:UNIFESPEscola Paulista de Medicina (EPM)Neurologia-NeurociênciasNeurologiaCirurgiaMedicinaORIGINALarticle.pdfarticle.pdfapplication/pdf619078${dspace.ui.url}/bitstream/11600/67327/1/article.pdf368281c05c52a3f2f3b78360b38ff7abMD51open accessLICENSElicense.txtlicense.txttext/plain; charset=utf-85824${dspace.ui.url}/bitstream/11600/67327/2/license.txtd39042613db9b8cf4f05a2f9745302d7MD52open 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InstitucionalPUBhttp://www.repositorio.unifesp.br/oai/requestopendoar:34652023-10-21T04:02:07Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)false |
dc.title.pt_BR.fl_str_mv |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
title |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
spellingShingle |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease Rodrigues, Gislene [UNIFESP] Anesthesia Health education Malignant hyperthermia |
title_short |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
title_full |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
title_fullStr |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
title_full_unstemmed |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
title_sort |
Patient suspected susceptibility to malignant hyperthermia: impact of the disease |
author |
Rodrigues, Gislene [UNIFESP] |
author_facet |
Rodrigues, Gislene [UNIFESP] Andrade, Pamela Vieira [UNIFESP] Santos, Joilson Moura dos [UNIFESP] Castro, Isac de [UNIFESP] Amaral, Jose Luiz Gomes do [UNIFESP] Silva, Helga Cristina Almeida da [UNIFESP] |
author_role |
author |
author2 |
Andrade, Pamela Vieira [UNIFESP] Santos, Joilson Moura dos [UNIFESP] Castro, Isac de [UNIFESP] Amaral, Jose Luiz Gomes do [UNIFESP] Silva, Helga Cristina Almeida da [UNIFESP] |
author2_role |
author author author author author |
dc.contributor.authorLattes.pt_BR.fl_str_mv |
http://lattes.cnpq.br/0844918862241102 |
dc.contributor.author.fl_str_mv |
Rodrigues, Gislene [UNIFESP] Andrade, Pamela Vieira [UNIFESP] Santos, Joilson Moura dos [UNIFESP] Castro, Isac de [UNIFESP] Amaral, Jose Luiz Gomes do [UNIFESP] Silva, Helga Cristina Almeida da [UNIFESP] |
dc.subject.eng.fl_str_mv |
Anesthesia Health education Malignant hyperthermia |
topic |
Anesthesia Health education Malignant hyperthermia |
description |
Introduction Malignant Hyperthermia (MH) is an inherited hypermetabolic syndrome triggered by exposure to halogenated anesthetics/succinylcholine. The lack of knowledge regarding this condition might be associated with the rare occurrence of MH reaction and symptoms. Methods This observational study evaluated 68 patients from 48 families with confirmed or suspected MH susceptibility due to medical history of MH reaction or idiopathic increase of creatine kinase or MH-related myopathies. Participants were assessed by a standardized questionnaire and submitted to physical/neurological examination to assess the characteristics of patients with MH, their knowledge about the disease, and the impact suspected MH had on their daily lives. Results Suspected MH impacted the daily life of 50% of patients, creating difficulties in performing surgical/clinical/dental treatment and problems related to their family life/working/practicing sports. The questionnaire on MH revealed a correct answer score of 62.1 ± 20.8 (mean ± standard deviation) on a scale 0 to 100. Abnormal physical/neurological examination findings were detected in 92.6% of susceptible patients. Conclusions Suspected MH had impacted the daily lives of most patients, with patients reporting problems even before MH investigation with IVCT. Patients showed a moderate level of knowledge about MH, suggesting the need to implement continuing education programs. MH susceptible patients require regular follow-up by a health team to detect abnormalities during physical and neurological examination. |
publishDate |
2023 |
dc.date.accessioned.fl_str_mv |
2023-04-03T15:21:57Z |
dc.date.available.fl_str_mv |
2023-04-03T15:21:57Z |
dc.date.issued.fl_str_mv |
2023-03 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.pt_BR.fl_str_mv |
https://www.sciencedirect.com/science/article/pii/S0104001422000033?via%3Dihub |
dc.identifier.uri.fl_str_mv |
https://repositorio.unifesp.br/11600/67327 |
dc.identifier.doi.pt_BR.fl_str_mv |
10.1016/j.bjane.2021.10.021 |
url |
https://www.sciencedirect.com/science/article/pii/S0104001422000033?via%3Dihub https://repositorio.unifesp.br/11600/67327 |
identifier_str_mv |
10.1016/j.bjane.2021.10.021 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.ispartof.en.fl_str_mv |
Brazilian Journal of Anesthesiology |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
SBA |
publisher.none.fl_str_mv |
SBA |
dc.source.none.fl_str_mv |
reponame:Repositório Institucional da UNIFESP instname:Universidade Federal de São Paulo (UNIFESP) instacron:UNIFESP |
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Universidade Federal de São Paulo (UNIFESP) |
instacron_str |
UNIFESP |
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UNIFESP |
reponame_str |
Repositório Institucional da UNIFESP |
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Repositório Institucional da UNIFESP |
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Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP) |
repository.mail.fl_str_mv |
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