Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports
Autor(a) principal: | |
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Data de Publicação: | 2019 |
Outros Autores: | , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Brazilian Dental Science |
Texto Completo: | https://ojs.ict.unesp.br/index.php/cob/article/view/1704 |
Resumo: | Objective: The objective of this paper was to describe the oral conditions of two children accompanied by their mothers who reported to the Department of Pediatric Dentistry of Fluminense Federal University with Williams-Beuren syndrome (WBS). Case report: The 9-year-old female patient had a family and medical history significant for placental abruption, caesarean section, delayed psychomotor development, learning disabilities, tendency to selfdistract and congenital heart disease. In contrast, the 7-year-old male patient had a normal birth and no gestational intercurrences. Discussion: Clinically, the female presented with mixed dentition, crowding in the maxillary and mandibular arches, prolonged retention of deciduous teeth, anterior and posterior cross-bite and Angle Class I malocclusion, while the male had mixed dentition and retarded psychomotor development. Due to the patients having congenital heart disease, a prophylactic antibiotic regimen was prescribed prior to the dental procedures in both of them. Conclusion: These patients had been followed up for 2 years and this case report underscores the importance of early dental evaluation and counselling for parents of WBS patients.KeywordsWilliams Beuren syndrome; Oral manifestations; Child. |
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Brazilian Dental Science |
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Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reportsObjective: The objective of this paper was to describe the oral conditions of two children accompanied by their mothers who reported to the Department of Pediatric Dentistry of Fluminense Federal University with Williams-Beuren syndrome (WBS). Case report: The 9-year-old female patient had a family and medical history significant for placental abruption, caesarean section, delayed psychomotor development, learning disabilities, tendency to selfdistract and congenital heart disease. In contrast, the 7-year-old male patient had a normal birth and no gestational intercurrences. Discussion: Clinically, the female presented with mixed dentition, crowding in the maxillary and mandibular arches, prolonged retention of deciduous teeth, anterior and posterior cross-bite and Angle Class I malocclusion, while the male had mixed dentition and retarded psychomotor development. Due to the patients having congenital heart disease, a prophylactic antibiotic regimen was prescribed prior to the dental procedures in both of them. Conclusion: These patients had been followed up for 2 years and this case report underscores the importance of early dental evaluation and counselling for parents of WBS patients.KeywordsWilliams Beuren syndrome; Oral manifestations; Child.Institute of Science and Technology of São José dos Campos2019-04-30info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfapplication/vnd.openxmlformats-officedocument.wordprocessingml.documenthttps://ojs.ict.unesp.br/index.php/cob/article/view/170410.14295/bds.2019.v22i2.1704Brazilian Dental Science; Vol. 22 No. 2 (2019): Apr. - Jun. / 2019 - Published April 2019; 281-288Brazilian Dental Science; v. 22 n. 2 (2019): Apr. - Jun. / 2019 - Published April 2019; 281-2882178-6011reponame:Brazilian Dental Scienceinstname:Universidade Estadual Paulista Júlio de Mesquita Filho (UNESP)instacron:UNESPenghttps://ojs.ict.unesp.br/index.php/cob/article/view/1704/1334https://ojs.ict.unesp.br/index.php/cob/article/view/1704/3596Copyright (c) 2019 Brazilian Dental Scienceinfo:eu-repo/semantics/openAccessPires, Flávia SilvaPaula, Viviane Andrade CancioFaker, KhawanaDi Lanaro, NataliaCarvalho, Raissa Christiane O deTostes, Mônica Almeida2020-01-28T11:57:54Zoai:ojs.pkp.sfu.ca:article/1704Revistahttp://bds.ict.unesp.br/PUBhttp://ojs.fosjc.unesp.br/index.php/index/oaisergio@fosjc.unesp.br||sergio@fosjc.unesp.br2178-60112178-6011opendoar:2022-11-08T16:30:20.971863Brazilian Dental Science - Universidade Estadual Paulista Júlio de Mesquita Filho (UNESP)true |
dc.title.none.fl_str_mv |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
title |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
spellingShingle |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports Pires, Flávia Silva |
title_short |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
title_full |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
title_fullStr |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
title_full_unstemmed |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
title_sort |
Oral conditions of pediatric patients with Williams-Beuren syndrome: two case reports |
author |
Pires, Flávia Silva |
author_facet |
Pires, Flávia Silva Paula, Viviane Andrade Cancio Faker, Khawana Di Lanaro, Natalia Carvalho, Raissa Christiane O de Tostes, Mônica Almeida |
author_role |
author |
author2 |
Paula, Viviane Andrade Cancio Faker, Khawana Di Lanaro, Natalia Carvalho, Raissa Christiane O de Tostes, Mônica Almeida |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Pires, Flávia Silva Paula, Viviane Andrade Cancio Faker, Khawana Di Lanaro, Natalia Carvalho, Raissa Christiane O de Tostes, Mônica Almeida |
description |
Objective: The objective of this paper was to describe the oral conditions of two children accompanied by their mothers who reported to the Department of Pediatric Dentistry of Fluminense Federal University with Williams-Beuren syndrome (WBS). Case report: The 9-year-old female patient had a family and medical history significant for placental abruption, caesarean section, delayed psychomotor development, learning disabilities, tendency to selfdistract and congenital heart disease. In contrast, the 7-year-old male patient had a normal birth and no gestational intercurrences. Discussion: Clinically, the female presented with mixed dentition, crowding in the maxillary and mandibular arches, prolonged retention of deciduous teeth, anterior and posterior cross-bite and Angle Class I malocclusion, while the male had mixed dentition and retarded psychomotor development. Due to the patients having congenital heart disease, a prophylactic antibiotic regimen was prescribed prior to the dental procedures in both of them. Conclusion: These patients had been followed up for 2 years and this case report underscores the importance of early dental evaluation and counselling for parents of WBS patients.KeywordsWilliams Beuren syndrome; Oral manifestations; Child. |
publishDate |
2019 |
dc.date.none.fl_str_mv |
2019-04-30 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://ojs.ict.unesp.br/index.php/cob/article/view/1704 10.14295/bds.2019.v22i2.1704 |
url |
https://ojs.ict.unesp.br/index.php/cob/article/view/1704 |
identifier_str_mv |
10.14295/bds.2019.v22i2.1704 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://ojs.ict.unesp.br/index.php/cob/article/view/1704/1334 https://ojs.ict.unesp.br/index.php/cob/article/view/1704/3596 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2019 Brazilian Dental Science info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2019 Brazilian Dental Science |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf application/vnd.openxmlformats-officedocument.wordprocessingml.document |
dc.publisher.none.fl_str_mv |
Institute of Science and Technology of São José dos Campos |
publisher.none.fl_str_mv |
Institute of Science and Technology of São José dos Campos |
dc.source.none.fl_str_mv |
Brazilian Dental Science; Vol. 22 No. 2 (2019): Apr. - Jun. / 2019 - Published April 2019; 281-288 Brazilian Dental Science; v. 22 n. 2 (2019): Apr. - Jun. / 2019 - Published April 2019; 281-288 2178-6011 reponame:Brazilian Dental Science instname:Universidade Estadual Paulista Júlio de Mesquita Filho (UNESP) instacron:UNESP |
instname_str |
Universidade Estadual Paulista Júlio de Mesquita Filho (UNESP) |
instacron_str |
UNESP |
institution |
UNESP |
reponame_str |
Brazilian Dental Science |
collection |
Brazilian Dental Science |
repository.name.fl_str_mv |
Brazilian Dental Science - Universidade Estadual Paulista Júlio de Mesquita Filho (UNESP) |
repository.mail.fl_str_mv |
sergio@fosjc.unesp.br||sergio@fosjc.unesp.br |
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1788346900784611328 |