Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome
Autor(a) principal: | |
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Data de Publicação: | 2022 |
Outros Autores: | , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Research, Society and Development |
Texto Completo: | https://rsdjournal.org/index.php/rsd/article/view/25366 |
Resumo: | Introduction: the Bernard-Soulier Syndrome (BSS) is a rare inherited bleeding disorder witch the prevalence is estimated at 1:1,000,000. Its abnormalities are due to defective expression of the glycoproteic complex GPIb/IX/V – the platelets receptor that is crucial for the establishment of the prime hemostasis. Objective: report a rare case of a ruptured ovarian cyst in a patient with Bernard-Soulier Síndromes. Methodology: it's a descriptive and transversal study that consists of the formulation of a case report, built from the analysis of a patient’s medical record with BSS, who evolved with ruptured ovarian cyst. For theoretical foundation we used articles indexed in PubMed's database written in portuguese and english. The following descriptors were considered: Ovarian Cysts, Bernard-Soulier Syndrome and Abdomen Acute. Conclusion: considering the frequency and severity of the hemorrhagic events as highly variable aspects among patients with BSS it is necessary that the surgeon always keep in mind the underlying hematological disorders when faced with a possible hemorrhagic acute abdomen. |
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Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndromeTratamiento quirúrgico de quiste ovárico roto en paciente con síndrome de Bernard-SoulierTratamento cirúrgico de cisto ovariano roto em paciente com síndrome de Bernard-SoulierQuiestes OváricosSíndrome de Bernard-SoulierAbdomen agudo.Ovarian CystsBernard-Soulier SyndromeAbdomen acute.Cistos OvarianosSíndrome de Bernard-SoulierAbdome agudo.Introduction: the Bernard-Soulier Syndrome (BSS) is a rare inherited bleeding disorder witch the prevalence is estimated at 1:1,000,000. Its abnormalities are due to defective expression of the glycoproteic complex GPIb/IX/V – the platelets receptor that is crucial for the establishment of the prime hemostasis. Objective: report a rare case of a ruptured ovarian cyst in a patient with Bernard-Soulier Síndromes. Methodology: it's a descriptive and transversal study that consists of the formulation of a case report, built from the analysis of a patient’s medical record with BSS, who evolved with ruptured ovarian cyst. For theoretical foundation we used articles indexed in PubMed's database written in portuguese and english. The following descriptors were considered: Ovarian Cysts, Bernard-Soulier Syndrome and Abdomen Acute. Conclusion: considering the frequency and severity of the hemorrhagic events as highly variable aspects among patients with BSS it is necessary that the surgeon always keep in mind the underlying hematological disorders when faced with a possible hemorrhagic acute abdomen.Introducción: el Síndrome de Bernard-Soulier (SBS) es un trastorno hemorrágico hereditario poco frecuente cuya prevalencia se estima en 1:1.000.000. Sus anomalías se deben a la expresión defectuosa del complejo glicoproteico GPIb/IX/V, el receptor de plaquetas que es crucial para el estabelecimiento de la hemostasia principal. Objetivo: reportar un caso raro de ruptura de un quiste ovárico en uma paciente con Síndrome de Bernard-Soulier. Metodología: es un estudio descriptivo y transversal que consiste en la formulación de un reporte de caso, construido a partir del análisis de la historia clínica de una paciente con SBS, que evolucionó con ruptura de quiste de ovario. Para la fundamentación teórica utilizamos artículos indexados en la base de datos de PubMed escritos en português e inglés. Se consideraron los siguientes descriptores: Ovarian Cysts, Bernard-Soulier Syndrome, y Abdomen Acute.. Conclusión: considerando la frecuencia y severidad de los eventos hemorrágicos como aspectos altamente variables entre los pacientes con SBS, es necessario que el cirurjano tenga siempre presentes los trastornos hematológicos subyacentes ante un posible abdomen agudo hemorrágico.Introdução: A síndrome de Bernard-Soulier (SBS) é uma doença hematológica e hereditária rara que possui uma prevalência estimada em 1:1.000.000. Suas anormalidades são decorrentes da expressão defeituosa do complexo glicoproteico GPIb/IX/V- receptor plaquetário que é crucial para o estabelecimento da hemostasia primária. Objetivo: Relatar um caso raro de cisto ovariano roto em portador da Síndrome de Bernard-Soulier. Metodologia: estudo descritivo, transversal, que consiste na elaboração de um relato de caso, elaborado a partir de uma análise do prontuário de um paciente portador da Síndrome de Bernard-Soulier que evoluiu com cisto ovariano roto. Para embasamento teórico foram utilizados artigos indexados em português e inglês na base de dados PubMed. Foram considerados os seguintes descritores: Ovarian Cysts, Bernard-Soulier Syndrome, e Abdomen Acute. Conclusão: Considerando a frequência e a gravidade dos eventos hemorrágicos como aspectos muito variáveis entre os pacientes portadores de SBS é necessário que o cirurgião sempre tenha em mente distúrbios hematológicos subjacentes ao se deparar com um possível abdome agudo hemorrágico.Research, Society and Development2022-02-03info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/2536610.33448/rsd-v11i2.25366Research, Society and Development; Vol. 11 No. 2; e47911225366Research, Society and Development; Vol. 11 Núm. 2; e47911225366Research, Society and Development; v. 11 n. 2; e479112253662525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/25366/22786Copyright (c) 2022 João Victor Alcântara Pires; Julliana Ferrari Campêlo Libório de Santana; Etienny de Brito Dias Fernandes; Nadia Cristina Berton; Isabela Furlan Franchello; Rubia Martinez Santos; Camila Paixão Marques; Letícia Cristino Francisco; Renata Fornaciari Larahttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessPires, João Victor AlcântaraSantana, Julliana Ferrari Campêlo Libório de Fernandes, Etienny de Brito DiasBerton, Nadia CristinaFranchello, Isabela FurlanSantos, Rubia MartinezMarques, Camila Paixão Francisco, Letícia Cristino Lara, Renata Fornaciari 2022-02-07T01:42:50Zoai:ojs.pkp.sfu.ca:article/25366Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:43:40.118328Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false |
dc.title.none.fl_str_mv |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome Tratamiento quirúrgico de quiste ovárico roto en paciente con síndrome de Bernard-Soulier Tratamento cirúrgico de cisto ovariano roto em paciente com síndrome de Bernard-Soulier |
title |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
spellingShingle |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome Pires, João Victor Alcântara Quiestes Ováricos Síndrome de Bernard-Soulier Abdomen agudo. Ovarian Cysts Bernard-Soulier Syndrome Abdomen acute. Cistos Ovarianos Síndrome de Bernard-Soulier Abdome agudo. |
title_short |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
title_full |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
title_fullStr |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
title_full_unstemmed |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
title_sort |
Surgical treatment of ruptured ovarian cyst in a patient with Bernard-Soulier syndrome |
author |
Pires, João Victor Alcântara |
author_facet |
Pires, João Victor Alcântara Santana, Julliana Ferrari Campêlo Libório de Fernandes, Etienny de Brito Dias Berton, Nadia Cristina Franchello, Isabela Furlan Santos, Rubia Martinez Marques, Camila Paixão Francisco, Letícia Cristino Lara, Renata Fornaciari |
author_role |
author |
author2 |
Santana, Julliana Ferrari Campêlo Libório de Fernandes, Etienny de Brito Dias Berton, Nadia Cristina Franchello, Isabela Furlan Santos, Rubia Martinez Marques, Camila Paixão Francisco, Letícia Cristino Lara, Renata Fornaciari |
author2_role |
author author author author author author author author |
dc.contributor.author.fl_str_mv |
Pires, João Victor Alcântara Santana, Julliana Ferrari Campêlo Libório de Fernandes, Etienny de Brito Dias Berton, Nadia Cristina Franchello, Isabela Furlan Santos, Rubia Martinez Marques, Camila Paixão Francisco, Letícia Cristino Lara, Renata Fornaciari |
dc.subject.por.fl_str_mv |
Quiestes Ováricos Síndrome de Bernard-Soulier Abdomen agudo. Ovarian Cysts Bernard-Soulier Syndrome Abdomen acute. Cistos Ovarianos Síndrome de Bernard-Soulier Abdome agudo. |
topic |
Quiestes Ováricos Síndrome de Bernard-Soulier Abdomen agudo. Ovarian Cysts Bernard-Soulier Syndrome Abdomen acute. Cistos Ovarianos Síndrome de Bernard-Soulier Abdome agudo. |
description |
Introduction: the Bernard-Soulier Syndrome (BSS) is a rare inherited bleeding disorder witch the prevalence is estimated at 1:1,000,000. Its abnormalities are due to defective expression of the glycoproteic complex GPIb/IX/V – the platelets receptor that is crucial for the establishment of the prime hemostasis. Objective: report a rare case of a ruptured ovarian cyst in a patient with Bernard-Soulier Síndromes. Methodology: it's a descriptive and transversal study that consists of the formulation of a case report, built from the analysis of a patient’s medical record with BSS, who evolved with ruptured ovarian cyst. For theoretical foundation we used articles indexed in PubMed's database written in portuguese and english. The following descriptors were considered: Ovarian Cysts, Bernard-Soulier Syndrome and Abdomen Acute. Conclusion: considering the frequency and severity of the hemorrhagic events as highly variable aspects among patients with BSS it is necessary that the surgeon always keep in mind the underlying hematological disorders when faced with a possible hemorrhagic acute abdomen. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-02-03 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/25366 10.33448/rsd-v11i2.25366 |
url |
https://rsdjournal.org/index.php/rsd/article/view/25366 |
identifier_str_mv |
10.33448/rsd-v11i2.25366 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/25366/22786 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Research, Society and Development |
publisher.none.fl_str_mv |
Research, Society and Development |
dc.source.none.fl_str_mv |
Research, Society and Development; Vol. 11 No. 2; e47911225366 Research, Society and Development; Vol. 11 Núm. 2; e47911225366 Research, Society and Development; v. 11 n. 2; e47911225366 2525-3409 reponame:Research, Society and Development instname:Universidade Federal de Itajubá (UNIFEI) instacron:UNIFEI |
instname_str |
Universidade Federal de Itajubá (UNIFEI) |
instacron_str |
UNIFEI |
institution |
UNIFEI |
reponame_str |
Research, Society and Development |
collection |
Research, Society and Development |
repository.name.fl_str_mv |
Research, Society and Development - Universidade Federal de Itajubá (UNIFEI) |
repository.mail.fl_str_mv |
rsd.articles@gmail.com |
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1797052761517326336 |