Epidermolysis Bullosa: oral manifestations and dental management

Detalhes bibliográficos
Autor(a) principal: Santos, Marcela Nogueira dos
Data de Publicação: 2022
Outros Autores: Franco, Amanda Gonçalves, Santos, Daniele Saara dos, Silva, Wenys Cláudio Gomes da, Gomes, Lecy Anne Braga, Miranda, Alexandre de Souza, Rodrigues , Marcelo Costa, Carneiro , Grace Kelly Martins, Lima, Thallita Monalisa Sizenando Souza, Fernandes, Nívia Delamoniky Lima, Fernandes, Jefferson Douglas Lima, Ramalho , Matheus Almeida, Reis, Jaqueline Lopes, Menezes , Vitória Ribeiro Barbosa de, Castro , Jamille de Souza, Afonso , Áquila de Oliveira
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/25188
Resumo: Epidermolysis Bullosa (EB), a group of rare hereditary diseases, characterized by the development of blisters in the cutaneous-mucosal region of the entire body, in response to minimal trauma, heat, or no apparent cause. birth or during the first years of life. The present study aims to review the literature on the oral manifestations found in patients with Epidermolysis Bullosa, as well as to define the dental clinical management to be followed in cases of EB. SciVerse Scopus, Scientific Electronic Library Online (Scielo), US National Library of Medicine (PUBMED) and ScienceDirect, using the Mendeley Reference Manager. In the oral cavity, an EB can manifest itself in several ways, with changes that vary in severity and quantity, depending on the type of EB, such as the formation of blisters and ulcerations (in the mucosa, palate and tongue), anodontia, junction of the vestibular sulcus (union of the attached gingiva with the oral mucosa), presence of caries and severe periodontal diseases, alveolar bone resorption and hypoplastic dental anomalies, in addition to maxillary atrophy, mandibular prognathism and mandibular course. Malocclusion is even more severe due to atresia of the alveolar arches and delay in tooth eruption. Due to the great difficulty and risk of offering dental treatment to patients with EB, the prevention of disease, biofilm and periodontal disease must be emphasized from childhood. Professionals in treatment should carry out oral hygiene and adequate prophylaxis, a diet program to prevent caries, use of gels, mouthwashes, adjuvant therapies with chlorhexidine D, cotton swabs, sprays and topical varnish applications, fluorides, biofilm scraping and leisure.
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spelling Epidermolysis Bullosa: oral manifestations and dental managementEpidermólisis ampollosa: manifestaciones bucales y tratamiento dentalEpidermólise Bolhosa: manifestações orais e manejo odontológico Manejo DentalManifestaciones oralesEpidermólisis ampollosa.Dental ManagementOral ManifestationsBullous epidermolysis.Manifestações OraisEpidermólise BolhosaEpidermólise bolhosa. Epidermolysis Bullosa (EB), a group of rare hereditary diseases, characterized by the development of blisters in the cutaneous-mucosal region of the entire body, in response to minimal trauma, heat, or no apparent cause. birth or during the first years of life. The present study aims to review the literature on the oral manifestations found in patients with Epidermolysis Bullosa, as well as to define the dental clinical management to be followed in cases of EB. SciVerse Scopus, Scientific Electronic Library Online (Scielo), US National Library of Medicine (PUBMED) and ScienceDirect, using the Mendeley Reference Manager. In the oral cavity, an EB can manifest itself in several ways, with changes that vary in severity and quantity, depending on the type of EB, such as the formation of blisters and ulcerations (in the mucosa, palate and tongue), anodontia, junction of the vestibular sulcus (union of the attached gingiva with the oral mucosa), presence of caries and severe periodontal diseases, alveolar bone resorption and hypoplastic dental anomalies, in addition to maxillary atrophy, mandibular prognathism and mandibular course. Malocclusion is even more severe due to atresia of the alveolar arches and delay in tooth eruption. Due to the great difficulty and risk of offering dental treatment to patients with EB, the prevention of disease, biofilm and periodontal disease must be emphasized from childhood. Professionals in treatment should carry out oral hygiene and adequate prophylaxis, a diet program to prevent caries, use of gels, mouthwashes, adjuvant therapies with chlorhexidine D, cotton swabs, sprays and topical varnish applications, fluorides, biofilm scraping and leisure.Epidermólisis ampollosa (EB), grupo de enfermedades hereditarias raras, caracterizadas por el desarrollo de ampollas en la región cutáneo-mucosa de todo el cuerpo, en respuesta a traumatismos mínimos, calor o sin causa aparente. Nacimiento o durante los primeros años de vida. vida. El presente estudio tiene como objetivo revisar la literatura sobre las manifestaciones bucales encontradas en pacientes con Epidermólisis Bullosa, así como definir el manejo clínico dental a seguir en los casos de EB. SciVerse Scopus, Scientific Electronic Library Online (Scielo), Biblioteca Nacional de Medicina de EE. UU. (PUBMED) y ScienceDirect, utilizando el Administrador de referencias de Mendeley. En la cavidad oral, una EB puede manifestarse de varias formas, con cambios que varían en gravedad y cantidad, según el tipo de EB, como la formación de ampollas y ulceraciones (en la mucosa, paladar y lengua), anodoncia, unión del surco vestibular (unión de la encía adherida con la mucosa oral), presencia de caries y enfermedades periodontales graves, reabsorción ósea alveolar y anomalías dentales hipoplásicas, además de atrofia maxilar, prognatismo mandibular y curso mandibular. La maloclusión es aún más grave debido a la atresia de los arcos alveolares y al retraso de la erupción dentaria. Debido a la gran dificultad y riesgo de ofrecer tratamiento odontológico a pacientes con EB, se debe enfatizar la prevención de enfermedades, biofilm y enfermedad periodontal desde la niñez. Los profesionales en tratamiento deben realizar higiene bucal y profilaxis adecuada, un programa de dieta para prevenir caries, uso de geles, enjuagues bucales, terapias adyuvantes con clorhexidina D, hisopos de algodón, aerosoles y aplicaciones de barnices tópicos, fluoruros, raspado de biofilm y ocio.A Epidermólise Bolhosa (EB) descreve um grupo de doenças rara, de caráter hereditário, caracterizada pelo desenvolvimento de bolhas na região cutaneomucosa de todo o corpo, em resposta ao trauma mínimo, ao calor, ou a nenhuma causa aparente, podendo manifestar-se ao nascimento ou durante os primeiros anos de vida. o presente estudo possui como objetivo revisar a literatura acerca das manifestações orais encontradas em pacientes portadores da Epidermólise Bolhosa, bem como descrever o manejo clínico odontológico a ser seguido em casos de EB. Para a construção deste trabalho foi feito um levantamento bibliográfico nas bases de dados SciVerse Scopus, Scientific Eletronic Library Online (Scielo), U.S. National Library of Medicine (PUBMED) e ScienceDirect, utilizando o gerenciador de referências Mendeley. Na cavidade oral, a EB pode manifestar-se de diversas formas, com inúmeras alterações, que variam em severidade e quantidade, dependendo do tipo de EB, como a formação de bolhas e ulcerações (na mucosa, palato e língua), anodontia, junção do sulco vestibular (união da gengiva inserida com a mucosa bucal), presença das doenças cárie e periodontal severas, reabsorção óssea alveolar e anomalias dentárias hipoplásicas, além de atrofia da maxila, prognatismo mandibular e ângulo da mandíbula aumentado. A maloclusão torna-se ainda mais severa pela atresia dos arcos alveolares e pelo atraso na erupção dentária. Devido à grande dificuldade e risco de se oferecer tratamento odontológico aos pacientes com EB, a prevenção da cárie, biofilme e da doença periodontal deve ser enfatizada desde a infância. Devendo o profissional no tratamento realizar higiene oral e profilaxia adequada, um programa dietético de prevenção de cárie, uso de géis, enxaguantes bucais, terapias adjuvantes com clorexidina D, cotonetes, sprays e aplicações de verniz tópico, fluoretos, raspagem de biofilme e lazer.Research, Society and Development2022-01-10info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/2518810.33448/rsd-v11i1.25188Research, Society and Development; Vol. 11 No. 1; e40411125188Research, Society and Development; Vol. 11 Núm. 1; e40411125188Research, Society and Development; v. 11 n. 1; e404111251882525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/25188/22011Copyright (c) 2022 Marcela Nogueira dos Santos; Amanda Gonçalves Franco; Daniele Saara dos Santos; Wenys Cláudio Gomes da Silva; Lecy Anne Braga Gomes; Alexandre de Souza Miranda; Marcelo Costa Rodrigues ; Grace Kelly Martins Carneiro ; Thallita Monalisa Sizenando Souza Lima; Nívia Delamoniky Lima Fernandes; Jefferson Douglas Lima Fernandes; Matheus Almeida Ramalho ; Jaqueline Lopes Reis; Vitória Ribeiro Barbosa de Menezes ; Jamille de Souza Castro ; Áquila de Oliveira Afonso https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessSantos, Marcela Nogueira dosFranco, Amanda Gonçalves Santos, Daniele Saara dos Silva, Wenys Cláudio Gomes da Gomes, Lecy Anne BragaMiranda, Alexandre de Souza Rodrigues , Marcelo Costa Carneiro , Grace Kelly Martins Lima, Thallita Monalisa Sizenando Souza Fernandes, Nívia Delamoniky Lima Fernandes, Jefferson Douglas Lima Ramalho , Matheus Almeida Reis, Jaqueline Lopes Menezes , Vitória Ribeiro Barbosa de Castro , Jamille de Souza Afonso , Áquila de Oliveira2022-01-16T18:08:18Zoai:ojs.pkp.sfu.ca:article/25188Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:43:31.862003Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Epidermolysis Bullosa: oral manifestations and dental management
Epidermólisis ampollosa: manifestaciones bucales y tratamiento dental
Epidermólise Bolhosa: manifestações orais e manejo odontológico
title Epidermolysis Bullosa: oral manifestations and dental management
spellingShingle Epidermolysis Bullosa: oral manifestations and dental management
Santos, Marcela Nogueira dos
Manejo Dental
Manifestaciones orales
Epidermólisis ampollosa.
Dental Management
Oral Manifestations
Bullous epidermolysis.
Manifestações Orais
Epidermólise Bolhosa
Epidermólise bolhosa.
title_short Epidermolysis Bullosa: oral manifestations and dental management
title_full Epidermolysis Bullosa: oral manifestations and dental management
title_fullStr Epidermolysis Bullosa: oral manifestations and dental management
title_full_unstemmed Epidermolysis Bullosa: oral manifestations and dental management
title_sort Epidermolysis Bullosa: oral manifestations and dental management
author Santos, Marcela Nogueira dos
author_facet Santos, Marcela Nogueira dos
Franco, Amanda Gonçalves
Santos, Daniele Saara dos
Silva, Wenys Cláudio Gomes da
Gomes, Lecy Anne Braga
Miranda, Alexandre de Souza
Rodrigues , Marcelo Costa
Carneiro , Grace Kelly Martins
Lima, Thallita Monalisa Sizenando Souza
Fernandes, Nívia Delamoniky Lima
Fernandes, Jefferson Douglas Lima
Ramalho , Matheus Almeida
Reis, Jaqueline Lopes
Menezes , Vitória Ribeiro Barbosa de
Castro , Jamille de Souza
Afonso , Áquila de Oliveira
author_role author
author2 Franco, Amanda Gonçalves
Santos, Daniele Saara dos
Silva, Wenys Cláudio Gomes da
Gomes, Lecy Anne Braga
Miranda, Alexandre de Souza
Rodrigues , Marcelo Costa
Carneiro , Grace Kelly Martins
Lima, Thallita Monalisa Sizenando Souza
Fernandes, Nívia Delamoniky Lima
Fernandes, Jefferson Douglas Lima
Ramalho , Matheus Almeida
Reis, Jaqueline Lopes
Menezes , Vitória Ribeiro Barbosa de
Castro , Jamille de Souza
Afonso , Áquila de Oliveira
author2_role author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Santos, Marcela Nogueira dos
Franco, Amanda Gonçalves
Santos, Daniele Saara dos
Silva, Wenys Cláudio Gomes da
Gomes, Lecy Anne Braga
Miranda, Alexandre de Souza
Rodrigues , Marcelo Costa
Carneiro , Grace Kelly Martins
Lima, Thallita Monalisa Sizenando Souza
Fernandes, Nívia Delamoniky Lima
Fernandes, Jefferson Douglas Lima
Ramalho , Matheus Almeida
Reis, Jaqueline Lopes
Menezes , Vitória Ribeiro Barbosa de
Castro , Jamille de Souza
Afonso , Áquila de Oliveira
dc.subject.por.fl_str_mv Manejo Dental
Manifestaciones orales
Epidermólisis ampollosa.
Dental Management
Oral Manifestations
Bullous epidermolysis.
Manifestações Orais
Epidermólise Bolhosa
Epidermólise bolhosa.
topic Manejo Dental
Manifestaciones orales
Epidermólisis ampollosa.
Dental Management
Oral Manifestations
Bullous epidermolysis.
Manifestações Orais
Epidermólise Bolhosa
Epidermólise bolhosa.
description Epidermolysis Bullosa (EB), a group of rare hereditary diseases, characterized by the development of blisters in the cutaneous-mucosal region of the entire body, in response to minimal trauma, heat, or no apparent cause. birth or during the first years of life. The present study aims to review the literature on the oral manifestations found in patients with Epidermolysis Bullosa, as well as to define the dental clinical management to be followed in cases of EB. SciVerse Scopus, Scientific Electronic Library Online (Scielo), US National Library of Medicine (PUBMED) and ScienceDirect, using the Mendeley Reference Manager. In the oral cavity, an EB can manifest itself in several ways, with changes that vary in severity and quantity, depending on the type of EB, such as the formation of blisters and ulcerations (in the mucosa, palate and tongue), anodontia, junction of the vestibular sulcus (union of the attached gingiva with the oral mucosa), presence of caries and severe periodontal diseases, alveolar bone resorption and hypoplastic dental anomalies, in addition to maxillary atrophy, mandibular prognathism and mandibular course. Malocclusion is even more severe due to atresia of the alveolar arches and delay in tooth eruption. Due to the great difficulty and risk of offering dental treatment to patients with EB, the prevention of disease, biofilm and periodontal disease must be emphasized from childhood. Professionals in treatment should carry out oral hygiene and adequate prophylaxis, a diet program to prevent caries, use of gels, mouthwashes, adjuvant therapies with chlorhexidine D, cotton swabs, sprays and topical varnish applications, fluorides, biofilm scraping and leisure.
publishDate 2022
dc.date.none.fl_str_mv 2022-01-10
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/25188
10.33448/rsd-v11i1.25188
url https://rsdjournal.org/index.php/rsd/article/view/25188
identifier_str_mv 10.33448/rsd-v11i1.25188
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/25188/22011
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 11 No. 1; e40411125188
Research, Society and Development; Vol. 11 Núm. 1; e40411125188
Research, Society and Development; v. 11 n. 1; e40411125188
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
instacron:UNIFEI
instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
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