Sturge-Weber Syndrome: report of a clinical case

Detalhes bibliográficos
Autor(a) principal: Martorelli, Sérgio Bartolomeu de Farias
Data de Publicação: 2021
Outros Autores: Barbosa, Marina Rosa, Gheno, Caciana Farias da Silva, Silva, Hadassa Fonsêca da, Andrade, Beatriz Barbosa de, Alves, Maria Clara da Mota, Rocha, Rafaela Véras de Morais, Cavalcanti, Kemilly Raissa Pereira
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/23327
Resumo: Sturge-Weber syndrome is a rare congenital developmental pathology that is not hereditary. It is characterized by cerebral cortex angiomatosis, with the presence of cerebral calcifications, epilepsy, facial nevus, and ocular alterations. The present study aimed to perform a case report of Sturge-Weber Syndrome, in a patient seen at the clinic school of the Recife School of Dentistry, presenting intraoral port wine staining, face region, pinna, and cervical region, unilateral location, right side. Because it is a rare syndrome, the present case report incorporated the other cases reported in the literature, providing more knowledge of the dental class about the disease, from the aid to diagnosis to the necessary care in the dental treatment of patients with this syndrome.
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spelling Sturge-Weber Syndrome: report of a clinical caseSíndrome Sturge-Weber: reporte de un caso clínicoSíndrome de Sturge-Weber: relato de caso clínicoSíndrome de Sturge-WeberSíndromes neurocutâneasAngiomatose.Síndrome de Sturge-WeberSíndromes neurocutáneosAngiomatosis.Sturge-Weber syndromeNeurocutaneous syndromesAngiomatosis.Sturge-Weber syndrome is a rare congenital developmental pathology that is not hereditary. It is characterized by cerebral cortex angiomatosis, with the presence of cerebral calcifications, epilepsy, facial nevus, and ocular alterations. The present study aimed to perform a case report of Sturge-Weber Syndrome, in a patient seen at the clinic school of the Recife School of Dentistry, presenting intraoral port wine staining, face region, pinna, and cervical region, unilateral location, right side. Because it is a rare syndrome, the present case report incorporated the other cases reported in the literature, providing more knowledge of the dental class about the disease, from the aid to diagnosis to the necessary care in the dental treatment of patients with this syndrome.El síndrome de Sturge-Weber es una rara patología congénita del desarrollo que no es hereditaria. Se caracteriza por angiomatosis de la corteza cerebral, con presencia de calcificaciones cerebrales, epilepsia, nevus facial y alteraciones oculares. El presente estudio tuvo como objetivo realizar el reporte de un caso de Síndrome de Sturge-Weber, en un paciente atendido en la clínica escuela de la Facultad de Odontología de Recife, presentando manchas intraorales de vino de Oporto, región de la cara, pabellón auricular y en la región de la cara, el pabellón auricular y la región cervical, de localización unilateral, en el lado derecho. Por tratarse de un síndrome raro, el presente informe de caso incorporó los otros casos reportados en la literatura, proporcionando mayor conocimiento de la clase odontológica sobre la enfermedad, desde la ayuda al diagnóstico hasta los cuidados necesarios en el tratamiento odontológico de pacientes con este síndrome.A síndrome de Sturge-Weber é uma patologia congênita rara de desenvolvimento, não hereditária. É caracterizada por uma angiomatose cortical cerebral, com presença de calcificações cerebrais, epilepsia, nevus faciais e alterações oculares. O presente estudo teve como objetivo realizar um relato de caso de Síndrome de Sturge-Weber, em paciente atendido na clínica escola da Faculdade de Odontologia do Recife, apresentando manchas vinho do porto intrabucais, região da face, pavilhão auricular e região cervical, de localização unilateral, lado direito. Por ser síndrome rara, o presente relato de caso incorporado aos demais casos relatados na literatura, proporcionando maior conhecimento da classe odontológica sobre a doença, desde o auxílio ao diagnóstico aos cuidados necessários no tratamento odontológico dos pacientes portadores dessa síndrome.Research, Society and Development2021-12-08info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/2332710.33448/rsd-v10i16.23327Research, Society and Development; Vol. 10 No. 16; e120101623327Research, Society and Development; Vol. 10 Núm. 16; e120101623327Research, Society and Development; v. 10 n. 16; e1201016233272525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/23327/20785Copyright (c) 2021 Sérgio Bartolomeu de Farias Martorelli; Marina Rosa Barbosa; Caciana Farias da Silva Gheno; Hadassa Fonsêca da Silva; Beatriz Barbosa de Andrade; Maria Clara da Mota Alves; Rafaela Véras de Morais Rocha; Kemilly Raissa Pereira Cavalcantihttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessMartorelli, Sérgio Bartolomeu de FariasBarbosa, Marina RosaGheno, Caciana Farias da Silva Silva, Hadassa Fonsêca da Andrade, Beatriz Barbosa deAlves, Maria Clara da MotaRocha, Rafaela Véras de Morais Cavalcanti, Kemilly Raissa Pereira 2021-12-20T11:03:07Zoai:ojs.pkp.sfu.ca:article/23327Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:42:14.388580Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Sturge-Weber Syndrome: report of a clinical case
Síndrome Sturge-Weber: reporte de un caso clínico
Síndrome de Sturge-Weber: relato de caso clínico
title Sturge-Weber Syndrome: report of a clinical case
spellingShingle Sturge-Weber Syndrome: report of a clinical case
Martorelli, Sérgio Bartolomeu de Farias
Síndrome de Sturge-Weber
Síndromes neurocutâneas
Angiomatose.
Síndrome de Sturge-Weber
Síndromes neurocutáneos
Angiomatosis.
Sturge-Weber syndrome
Neurocutaneous syndromes
Angiomatosis.
title_short Sturge-Weber Syndrome: report of a clinical case
title_full Sturge-Weber Syndrome: report of a clinical case
title_fullStr Sturge-Weber Syndrome: report of a clinical case
title_full_unstemmed Sturge-Weber Syndrome: report of a clinical case
title_sort Sturge-Weber Syndrome: report of a clinical case
author Martorelli, Sérgio Bartolomeu de Farias
author_facet Martorelli, Sérgio Bartolomeu de Farias
Barbosa, Marina Rosa
Gheno, Caciana Farias da Silva
Silva, Hadassa Fonsêca da
Andrade, Beatriz Barbosa de
Alves, Maria Clara da Mota
Rocha, Rafaela Véras de Morais
Cavalcanti, Kemilly Raissa Pereira
author_role author
author2 Barbosa, Marina Rosa
Gheno, Caciana Farias da Silva
Silva, Hadassa Fonsêca da
Andrade, Beatriz Barbosa de
Alves, Maria Clara da Mota
Rocha, Rafaela Véras de Morais
Cavalcanti, Kemilly Raissa Pereira
author2_role author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Martorelli, Sérgio Bartolomeu de Farias
Barbosa, Marina Rosa
Gheno, Caciana Farias da Silva
Silva, Hadassa Fonsêca da
Andrade, Beatriz Barbosa de
Alves, Maria Clara da Mota
Rocha, Rafaela Véras de Morais
Cavalcanti, Kemilly Raissa Pereira
dc.subject.por.fl_str_mv Síndrome de Sturge-Weber
Síndromes neurocutâneas
Angiomatose.
Síndrome de Sturge-Weber
Síndromes neurocutáneos
Angiomatosis.
Sturge-Weber syndrome
Neurocutaneous syndromes
Angiomatosis.
topic Síndrome de Sturge-Weber
Síndromes neurocutâneas
Angiomatose.
Síndrome de Sturge-Weber
Síndromes neurocutáneos
Angiomatosis.
Sturge-Weber syndrome
Neurocutaneous syndromes
Angiomatosis.
description Sturge-Weber syndrome is a rare congenital developmental pathology that is not hereditary. It is characterized by cerebral cortex angiomatosis, with the presence of cerebral calcifications, epilepsy, facial nevus, and ocular alterations. The present study aimed to perform a case report of Sturge-Weber Syndrome, in a patient seen at the clinic school of the Recife School of Dentistry, presenting intraoral port wine staining, face region, pinna, and cervical region, unilateral location, right side. Because it is a rare syndrome, the present case report incorporated the other cases reported in the literature, providing more knowledge of the dental class about the disease, from the aid to diagnosis to the necessary care in the dental treatment of patients with this syndrome.
publishDate 2021
dc.date.none.fl_str_mv 2021-12-08
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/23327
10.33448/rsd-v10i16.23327
url https://rsdjournal.org/index.php/rsd/article/view/23327
identifier_str_mv 10.33448/rsd-v10i16.23327
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/23327/20785
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 10 No. 16; e120101623327
Research, Society and Development; Vol. 10 Núm. 16; e120101623327
Research, Society and Development; v. 10 n. 16; e120101623327
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
instacron:UNIFEI
instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
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