Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Colloquium Vitae |
Texto Completo: | http://revistas.unoeste.br/index.php/cv/article/view/3603 |
Resumo: | Agenesis of IVC is a rare cardiovascular malformation that occurs between the sixth and tenth week of embryogenesis. It may be associated with cardiac and abdominal malformations, in addition to complications such as DVT. The present work reports the case of a patient randomly diagnosed with total IVC agenesis associated with malformation of the portohepatic system and polysplenia. Female patient, 9 years old, being monitored for hemorrhagic dengue, with CT and abdominal US revealing anomaly of the development of the hepatic portal system associated with the absence of inferior vena cava with continuation of the retrocrural azygos vein, in addition to multiple accessory spleens. When the anastomoses of the VCI primitive veins are not formed properly, partial or total agenesis of this vessel may occur. Consequently, the blood is diverted to the retrocrural azygos. Identification of these malformations is important for the patients receive proper guidance about DVT prevention, in addition to monitoring them for diagnosis of other possible malformations. Keywords: inferior vena cava, cardiovascular abnormalities, vascular malformations, deep vein thrombosis, polysplenia. |
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Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case reportPOLIESPLENIA E ANOMALIA DO SISTEMA PORTAL HEPÁTICO ASSOCIADAS À AUSÊNCIA DE VEIA CAVA INFERIOR EM CRIANÇA: RELATO DE CASOAgenesis of IVC is a rare cardiovascular malformation that occurs between the sixth and tenth week of embryogenesis. It may be associated with cardiac and abdominal malformations, in addition to complications such as DVT. The present work reports the case of a patient randomly diagnosed with total IVC agenesis associated with malformation of the portohepatic system and polysplenia. Female patient, 9 years old, being monitored for hemorrhagic dengue, with CT and abdominal US revealing anomaly of the development of the hepatic portal system associated with the absence of inferior vena cava with continuation of the retrocrural azygos vein, in addition to multiple accessory spleens. When the anastomoses of the VCI primitive veins are not formed properly, partial or total agenesis of this vessel may occur. Consequently, the blood is diverted to the retrocrural azygos. Identification of these malformations is important for the patients receive proper guidance about DVT prevention, in addition to monitoring them for diagnosis of other possible malformations. Keywords: inferior vena cava, cardiovascular abnormalities, vascular malformations, deep vein thrombosis, polysplenia.A agenesia da VCI é uma malformação cardiovascular rara que ocorre entre a sexta e décima semana da embriogênese. Pode estar associada a malformações cardíacas e abdominais, além de complicações como a TVP. O presente trabalho relata o caso de uma paciente diagnosticada ao acaso com agenesia total de VCI associada à malformação do sistema porto-hepático e poliesplenia. Paciente do sexo feminino, 9 anos, em monitorização por dengue hemorrágica, com TC e US de abdome revelando anomalia do desenvolvimento do sistema portal hepático associado à ausência de veia cava inferior com continuação da veia ázigos retrocrural, além de múltiplos baços acessórios. Quando as anastomoses das veias primitivas da VCI não se formam adequadamente, pode ocorrer agenesia parcial ou total desse vaso. Consequentemente, o sangue é desviado para a ázigos retrocrural. A identificação dessas malformações é importante para que sejam dadas as devidas orientações aos portadores sobre prevenção de TVP, além do acompanhamento desses para monitorização e diagnóstico de outras possíveis malformações. Palavras-chave: veia cava inferior, anormalidades cardiovasculares, malformações vasculares, trombose venosa profunda, poliesplenia.Universidade do Oeste Paulista - UNOESTE2021-01-26info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttp://revistas.unoeste.br/index.php/cv/article/view/3603Colloquium Vitae. ISSN: 1984-6436; v. 12 n. 3 (2020): Colloquium Vitae, Vol. 12, n. 3; 102-1051984-6436reponame:Colloquium Vitaeinstname:Universidade do Oeste Paulista (UNOESTE)instacron:UNIOESTEporhttp://revistas.unoeste.br/index.php/cv/article/view/3603/3174Copyright (c) 2021 Colloquium Vitae. ISSN: 1984-6436info:eu-repo/semantics/openAccessCavalcanti dos Santos, LucasNascimento Jorge, Eloisa Alvares Calvo, Luciana de Souza Cavalcante, Janilson2021-01-26T18:54:23Zoai:ojs.pkp.sfu.ca:article/3603Revistahttps://revistas.unoeste.br/index.php/cv/indexONGhttp://revistas.unoeste.br/revistas/ojs/index.php/cv/oaijgjunior@unoeste.br||jgjunior@unoeste.br1984-64361984-6436opendoar:2021-01-26T18:54:23Colloquium Vitae - Universidade do Oeste Paulista (UNOESTE)false |
dc.title.none.fl_str_mv |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report POLIESPLENIA E ANOMALIA DO SISTEMA PORTAL HEPÁTICO ASSOCIADAS À AUSÊNCIA DE VEIA CAVA INFERIOR EM CRIANÇA: RELATO DE CASO |
title |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
spellingShingle |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report Cavalcanti dos Santos, Lucas |
title_short |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
title_full |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
title_fullStr |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
title_full_unstemmed |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
title_sort |
Polysplenia and anomaly of the hepatic portal system associated with the absence of inferior vena cava in a child: a case report |
author |
Cavalcanti dos Santos, Lucas |
author_facet |
Cavalcanti dos Santos, Lucas Nascimento Jorge, Eloisa Alvares Calvo, Luciana de Souza Cavalcante, Janilson |
author_role |
author |
author2 |
Nascimento Jorge, Eloisa Alvares Calvo, Luciana de Souza Cavalcante, Janilson |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Cavalcanti dos Santos, Lucas Nascimento Jorge, Eloisa Alvares Calvo, Luciana de Souza Cavalcante, Janilson |
description |
Agenesis of IVC is a rare cardiovascular malformation that occurs between the sixth and tenth week of embryogenesis. It may be associated with cardiac and abdominal malformations, in addition to complications such as DVT. The present work reports the case of a patient randomly diagnosed with total IVC agenesis associated with malformation of the portohepatic system and polysplenia. Female patient, 9 years old, being monitored for hemorrhagic dengue, with CT and abdominal US revealing anomaly of the development of the hepatic portal system associated with the absence of inferior vena cava with continuation of the retrocrural azygos vein, in addition to multiple accessory spleens. When the anastomoses of the VCI primitive veins are not formed properly, partial or total agenesis of this vessel may occur. Consequently, the blood is diverted to the retrocrural azygos. Identification of these malformations is important for the patients receive proper guidance about DVT prevention, in addition to monitoring them for diagnosis of other possible malformations. Keywords: inferior vena cava, cardiovascular abnormalities, vascular malformations, deep vein thrombosis, polysplenia. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-01-26 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://revistas.unoeste.br/index.php/cv/article/view/3603 |
url |
http://revistas.unoeste.br/index.php/cv/article/view/3603 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
http://revistas.unoeste.br/index.php/cv/article/view/3603/3174 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2021 Colloquium Vitae. ISSN: 1984-6436 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2021 Colloquium Vitae. ISSN: 1984-6436 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Universidade do Oeste Paulista - UNOESTE |
publisher.none.fl_str_mv |
Universidade do Oeste Paulista - UNOESTE |
dc.source.none.fl_str_mv |
Colloquium Vitae. ISSN: 1984-6436; v. 12 n. 3 (2020): Colloquium Vitae, Vol. 12, n. 3; 102-105 1984-6436 reponame:Colloquium Vitae instname:Universidade do Oeste Paulista (UNOESTE) instacron:UNIOESTE |
instname_str |
Universidade do Oeste Paulista (UNOESTE) |
instacron_str |
UNIOESTE |
institution |
UNIOESTE |
reponame_str |
Colloquium Vitae |
collection |
Colloquium Vitae |
repository.name.fl_str_mv |
Colloquium Vitae - Universidade do Oeste Paulista (UNOESTE) |
repository.mail.fl_str_mv |
jgjunior@unoeste.br||jgjunior@unoeste.br |
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1800218925805338624 |