Hyaline fibromatosis syndrome: Cutaneous manifestations

Detalhes bibliográficos
Autor(a) principal: Marques, Silvio Alencar [UNESP]
Data de Publicação: 2016
Outros Autores: Stolf, Hamilton Ometto [UNESP], Polizel, Juliana Ocanha [UNESP], Munhoz, Tânia [UNESP], Brandão, Marcela Calixto [UNESP], Marques, Mariangela Esther Alencar [UNESP]
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UNESP
Texto Completo: http://dx.doi.org/10.1590/abd1806-4841.20163799
http://hdl.handle.net/11449/178021
Resumo: Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.
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spelling Hyaline fibromatosis syndrome: Cutaneous manifestationsFibromaGingival hypertrophyMutationSkin: Skin manifestationsHyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.Universidade Estadual Paulista “Júlio de Mesquita Filho” (Unesp)Universidade Estadual Paulista “Júlio de Mesquita Filho” (Unesp)Universidade Estadual Paulista (Unesp)Marques, Silvio Alencar [UNESP]Stolf, Hamilton Ometto [UNESP]Polizel, Juliana Ocanha [UNESP]Munhoz, Tânia [UNESP]Brandão, Marcela Calixto [UNESP]Marques, Mariangela Esther Alencar [UNESP]2018-12-11T17:28:16Z2018-12-11T17:28:16Z2016-03-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article226-229application/pdfhttp://dx.doi.org/10.1590/abd1806-4841.20163799Anais Brasileiros de Dermatologia, v. 91, n. 2, p. 226-229, 2016.1806-48410365-0596http://hdl.handle.net/11449/17802110.1590/abd1806-4841.20163799S0365-059620160002002262-s2.0-84967262072S0365-05962016000200226.pdf7528116925519142Scopusreponame:Repositório Institucional da UNESPinstname:Universidade Estadual Paulista (UNESP)instacron:UNESPengAnais Brasileiros de Dermatologia0,520info:eu-repo/semantics/openAccess2023-11-14T06:13:41Zoai:repositorio.unesp.br:11449/178021Repositório InstitucionalPUBhttp://repositorio.unesp.br/oai/requestopendoar:29462023-11-14T06:13:41Repositório Institucional da UNESP - Universidade Estadual Paulista (UNESP)false
dc.title.none.fl_str_mv Hyaline fibromatosis syndrome: Cutaneous manifestations
title Hyaline fibromatosis syndrome: Cutaneous manifestations
spellingShingle Hyaline fibromatosis syndrome: Cutaneous manifestations
Marques, Silvio Alencar [UNESP]
Fibroma
Gingival hypertrophy
Mutation
Skin: Skin manifestations
title_short Hyaline fibromatosis syndrome: Cutaneous manifestations
title_full Hyaline fibromatosis syndrome: Cutaneous manifestations
title_fullStr Hyaline fibromatosis syndrome: Cutaneous manifestations
title_full_unstemmed Hyaline fibromatosis syndrome: Cutaneous manifestations
title_sort Hyaline fibromatosis syndrome: Cutaneous manifestations
author Marques, Silvio Alencar [UNESP]
author_facet Marques, Silvio Alencar [UNESP]
Stolf, Hamilton Ometto [UNESP]
Polizel, Juliana Ocanha [UNESP]
Munhoz, Tânia [UNESP]
Brandão, Marcela Calixto [UNESP]
Marques, Mariangela Esther Alencar [UNESP]
author_role author
author2 Stolf, Hamilton Ometto [UNESP]
Polizel, Juliana Ocanha [UNESP]
Munhoz, Tânia [UNESP]
Brandão, Marcela Calixto [UNESP]
Marques, Mariangela Esther Alencar [UNESP]
author2_role author
author
author
author
author
dc.contributor.none.fl_str_mv Universidade Estadual Paulista (Unesp)
dc.contributor.author.fl_str_mv Marques, Silvio Alencar [UNESP]
Stolf, Hamilton Ometto [UNESP]
Polizel, Juliana Ocanha [UNESP]
Munhoz, Tânia [UNESP]
Brandão, Marcela Calixto [UNESP]
Marques, Mariangela Esther Alencar [UNESP]
dc.subject.por.fl_str_mv Fibroma
Gingival hypertrophy
Mutation
Skin: Skin manifestations
topic Fibroma
Gingival hypertrophy
Mutation
Skin: Skin manifestations
description Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.
publishDate 2016
dc.date.none.fl_str_mv 2016-03-01
2018-12-11T17:28:16Z
2018-12-11T17:28:16Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://dx.doi.org/10.1590/abd1806-4841.20163799
Anais Brasileiros de Dermatologia, v. 91, n. 2, p. 226-229, 2016.
1806-4841
0365-0596
http://hdl.handle.net/11449/178021
10.1590/abd1806-4841.20163799
S0365-05962016000200226
2-s2.0-84967262072
S0365-05962016000200226.pdf
7528116925519142
url http://dx.doi.org/10.1590/abd1806-4841.20163799
http://hdl.handle.net/11449/178021
identifier_str_mv Anais Brasileiros de Dermatologia, v. 91, n. 2, p. 226-229, 2016.
1806-4841
0365-0596
10.1590/abd1806-4841.20163799
S0365-05962016000200226
2-s2.0-84967262072
S0365-05962016000200226.pdf
7528116925519142
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv Anais Brasileiros de Dermatologia
0,520
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv 226-229
application/pdf
dc.source.none.fl_str_mv Scopus
reponame:Repositório Institucional da UNESP
instname:Universidade Estadual Paulista (UNESP)
instacron:UNESP
instname_str Universidade Estadual Paulista (UNESP)
instacron_str UNESP
institution UNESP
reponame_str Repositório Institucional da UNESP
collection Repositório Institucional da UNESP
repository.name.fl_str_mv Repositório Institucional da UNESP - Universidade Estadual Paulista (UNESP)
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