Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis

Detalhes bibliográficos
Autor(a) principal: Giavina-Bianchi, Pedro
Data de Publicação: 2018
Outros Autores: Arruda, Luisa Karla, Aun, Marcelo V., Campos, Regis A., Chong-Neto, Herberto J., Constantino-Silva, Rosemeire N., Fernandes, Fátima R., Ferraro, Maria F., Ferriani, Mariana P.L., França, Alfeu T., Fusaro, Gustavo, Garcia, Juliana F.B., Komninakis, Shirley, Maia, Luana S.M., Mansour, Eli, Moreno, Adriana S., Motta, Antonio A., Pesquero, João B., Portilho, Nathalia, Rosário, Nelson A., Serpa, Faradiba S., Solé, Dirceu, Takejima, Priscila, Toledo, Eliana, Valle, Solange O.R., Veronez, Camila L., Grumach, Anete S.
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Clinics
Texto Completo: https://www.revistas.usp.br/clinics/article/view/146277
Resumo: Hereditary angioedema is an autosomal dominant disease characterized by recurrent angioedema attacks with the involvement of multiple organs. The disease is unknown to many health professionals and is therefore underdiagnosed. Patients who are not adequately diagnosed and treated have an estimated mortality rate ranging from 25% to 40% due to asphyxiation by laryngeal angioedema. Intestinal angioedema is another important and incapacitating presentation that may be the main or only manifestation during an attack. In this article, a group of experts from the “Associação Brasileira de Alergia e Imunologia (ASBAI)” and the “Grupo de Estudos Brasileiro em Angioedema Hereditário (GEBRAEH)” has updated the Brazilian guidelines for the diagnosis and treatment of hereditary angioedema.
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spelling Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and DiagnosisHereditary AngioedemaAngioedemaC1 Inhibitor DeficiencyCoagulation Factor XII MutationsManagementGuidelinesHereditary angioedema is an autosomal dominant disease characterized by recurrent angioedema attacks with the involvement of multiple organs. The disease is unknown to many health professionals and is therefore underdiagnosed. Patients who are not adequately diagnosed and treated have an estimated mortality rate ranging from 25% to 40% due to asphyxiation by laryngeal angioedema. Intestinal angioedema is another important and incapacitating presentation that may be the main or only manifestation during an attack. In this article, a group of experts from the “Associação Brasileira de Alergia e Imunologia (ASBAI)” and the “Grupo de Estudos Brasileiro em Angioedema Hereditário (GEBRAEH)” has updated the Brazilian guidelines for the diagnosis and treatment of hereditary angioedema.Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo2018-01-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://www.revistas.usp.br/clinics/article/view/14627710.6061/clinics/2018/e310Clinics; Vol. 73 (2018); e310Clinics; v. 73 (2018); e310Clinics; Vol. 73 (2018); e3101980-53221807-5932reponame:Clinicsinstname:Universidade de São Paulo (USP)instacron:USPenghttps://www.revistas.usp.br/clinics/article/view/146277/139967Copyright (c) 2018 Clinicsinfo:eu-repo/semantics/openAccessGiavina-Bianchi, PedroArruda, Luisa KarlaAun, Marcelo V.Campos, Regis A.Chong-Neto, Herberto J.Constantino-Silva, Rosemeire N.Fernandes, Fátima R.Ferraro, Maria F.Ferriani, Mariana P.L.França, Alfeu T.Fusaro, GustavoGarcia, Juliana F.B.Komninakis, ShirleyMaia, Luana S.M.Mansour, EliMoreno, Adriana S.Motta, Antonio A.Pesquero, João B.Portilho, NathaliaRosário, Nelson A.Serpa, Faradiba S.Solé, DirceuTakejima, PriscilaToledo, ElianaValle, Solange O.R.Veronez, Camila L.Grumach, Anete S.2019-05-14T11:48:50Zoai:revistas.usp.br:article/146277Revistahttps://www.revistas.usp.br/clinicsPUBhttps://www.revistas.usp.br/clinics/oai||clinics@hc.fm.usp.br1980-53221807-5932opendoar:2019-05-14T11:48:50Clinics - Universidade de São Paulo (USP)false
dc.title.none.fl_str_mv Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
title Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
spellingShingle Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
Giavina-Bianchi, Pedro
Hereditary Angioedema
Angioedema
C1 Inhibitor Deficiency
Coagulation Factor XII Mutations
Management
Guidelines
title_short Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
title_full Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
title_fullStr Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
title_full_unstemmed Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
title_sort Brazilian Guidelines for Hereditary Angioedema Management - 2017 Update Part 1: Definition, Classification and Diagnosis
author Giavina-Bianchi, Pedro
author_facet Giavina-Bianchi, Pedro
Arruda, Luisa Karla
Aun, Marcelo V.
Campos, Regis A.
Chong-Neto, Herberto J.
Constantino-Silva, Rosemeire N.
Fernandes, Fátima R.
Ferraro, Maria F.
Ferriani, Mariana P.L.
França, Alfeu T.
Fusaro, Gustavo
Garcia, Juliana F.B.
Komninakis, Shirley
Maia, Luana S.M.
Mansour, Eli
Moreno, Adriana S.
Motta, Antonio A.
Pesquero, João B.
Portilho, Nathalia
Rosário, Nelson A.
Serpa, Faradiba S.
Solé, Dirceu
Takejima, Priscila
Toledo, Eliana
Valle, Solange O.R.
Veronez, Camila L.
Grumach, Anete S.
author_role author
author2 Arruda, Luisa Karla
Aun, Marcelo V.
Campos, Regis A.
Chong-Neto, Herberto J.
Constantino-Silva, Rosemeire N.
Fernandes, Fátima R.
Ferraro, Maria F.
Ferriani, Mariana P.L.
França, Alfeu T.
Fusaro, Gustavo
Garcia, Juliana F.B.
Komninakis, Shirley
Maia, Luana S.M.
Mansour, Eli
Moreno, Adriana S.
Motta, Antonio A.
Pesquero, João B.
Portilho, Nathalia
Rosário, Nelson A.
Serpa, Faradiba S.
Solé, Dirceu
Takejima, Priscila
Toledo, Eliana
Valle, Solange O.R.
Veronez, Camila L.
Grumach, Anete S.
author2_role author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Giavina-Bianchi, Pedro
Arruda, Luisa Karla
Aun, Marcelo V.
Campos, Regis A.
Chong-Neto, Herberto J.
Constantino-Silva, Rosemeire N.
Fernandes, Fátima R.
Ferraro, Maria F.
Ferriani, Mariana P.L.
França, Alfeu T.
Fusaro, Gustavo
Garcia, Juliana F.B.
Komninakis, Shirley
Maia, Luana S.M.
Mansour, Eli
Moreno, Adriana S.
Motta, Antonio A.
Pesquero, João B.
Portilho, Nathalia
Rosário, Nelson A.
Serpa, Faradiba S.
Solé, Dirceu
Takejima, Priscila
Toledo, Eliana
Valle, Solange O.R.
Veronez, Camila L.
Grumach, Anete S.
dc.subject.por.fl_str_mv Hereditary Angioedema
Angioedema
C1 Inhibitor Deficiency
Coagulation Factor XII Mutations
Management
Guidelines
topic Hereditary Angioedema
Angioedema
C1 Inhibitor Deficiency
Coagulation Factor XII Mutations
Management
Guidelines
description Hereditary angioedema is an autosomal dominant disease characterized by recurrent angioedema attacks with the involvement of multiple organs. The disease is unknown to many health professionals and is therefore underdiagnosed. Patients who are not adequately diagnosed and treated have an estimated mortality rate ranging from 25% to 40% due to asphyxiation by laryngeal angioedema. Intestinal angioedema is another important and incapacitating presentation that may be the main or only manifestation during an attack. In this article, a group of experts from the “Associação Brasileira de Alergia e Imunologia (ASBAI)” and the “Grupo de Estudos Brasileiro em Angioedema Hereditário (GEBRAEH)” has updated the Brazilian guidelines for the diagnosis and treatment of hereditary angioedema.
publishDate 2018
dc.date.none.fl_str_mv 2018-01-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://www.revistas.usp.br/clinics/article/view/146277
10.6061/clinics/2018/e310
url https://www.revistas.usp.br/clinics/article/view/146277
identifier_str_mv 10.6061/clinics/2018/e310
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://www.revistas.usp.br/clinics/article/view/146277/139967
dc.rights.driver.fl_str_mv Copyright (c) 2018 Clinics
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2018 Clinics
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo
publisher.none.fl_str_mv Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo
dc.source.none.fl_str_mv Clinics; Vol. 73 (2018); e310
Clinics; v. 73 (2018); e310
Clinics; Vol. 73 (2018); e310
1980-5322
1807-5932
reponame:Clinics
instname:Universidade de São Paulo (USP)
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instname_str Universidade de São Paulo (USP)
instacron_str USP
institution USP
reponame_str Clinics
collection Clinics
repository.name.fl_str_mv Clinics - Universidade de São Paulo (USP)
repository.mail.fl_str_mv ||clinics@hc.fm.usp.br
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