The importance of central auditory evaluation in Friedreich's ataxia

• Autor(a) principal: Zeigelboim,Bianca Simone
• Data de Publicação: 2018
• Outros Autores: Teive,Hélio A. G., Rosa,Michèlli Rodrigues da, Malisky,Jéssica Spricigo, Fonseca,Vinicius Ribas, Marques,Jair Mendes, Liberalesso,Paulo Breno
• Tipo de documento: Artigo
• Idioma: eng
• Título da fonte: Arquivos de neuro-psiquiatria (Online)
• Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2018000300170
• topic: spinocerebellar degenerations; hearing disorders; Friedreich ataxia; evoked potentials, auditory; ataxic gait

ABSTRACT Objective To assess central auditory function in Friedreich's ataxia. Methods A cross-sectional, retrospective study was carried out. Thirty patients underwent the anamnesis, otorhinolaryngology examination, pure tone audiometry, acoustic immittance measures and brainstem auditory evoked potential (BAEP) assessments. Results The observed alterations were: 43.3% in the pure tone audiometry, bilateral in 36.7%; 56.6% in the BAEP test, bilateral in 50%; and 46.6% in the acoustic immittance test. There was a significant difference (p < 0.05) in the comparison between the tests performed. Conclusion In the audiological screening, there was a prevalence of the descending audiometric configuration at the frequency of 4kHz, and absence of the acoustic reflex at the same frequency. In the BAEP test, there was a prevalence of an increase of the latencies in waves I, III and V, and in the intervals of interpeaks I-III, I-V and III-V. In 13.3% of the patients, wave V was absent, and all waves were absent in 3.3% of patients.