Neuromyelitis optica: phenotypic characteristics in a Brazilian case series
Autor(a) principal: | |
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Data de Publicação: | 2017 |
Outros Autores: | , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Arquivos de neuro-psiquiatria (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017000200002 |
Resumo: | ABSTRACT The definition of neuromyelitis optica (NMO) is still evolving. In 2015, the International Panel for NMO Diagnosis was convened to develop revised diagnostic criteria. There have been few studies on NMO in the Brazilian population. Objective To describe the characteristics of 34 Brazilian NMO patients. To evaluate the contribution of the 2015 criteria to the diagnosis of NMO spectrum disorders (NMOSD) in 40 patients with longitudinal extensive transverse myelitis (LEMT). Methods This is a retrospective, descriptive and analytic study. Results Among NMO patients, there was a predominance of women, with onset in the fourth decade of life, and AQP4-IgG seropositivity in 73.5%. The diagnosis of NMOSD was established in 37.5% of LETM patients according to AQP4-IgG positivity and in 5% of LETM patients if the AQP4-IgG result was unknown. Conclusions The characteristics of this series are similar to those of other Western populations. The AQP4-IgG testing assists in the diagnosis of NMOSD. |
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Arquivos de neuro-psiquiatria (Online) |
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Neuromyelitis optica: phenotypic characteristics in a Brazilian case seriesneuromyelitis opticaepidemiologycross-sectional studiesenzyme-linked immunosorbent assayABSTRACT The definition of neuromyelitis optica (NMO) is still evolving. In 2015, the International Panel for NMO Diagnosis was convened to develop revised diagnostic criteria. There have been few studies on NMO in the Brazilian population. Objective To describe the characteristics of 34 Brazilian NMO patients. To evaluate the contribution of the 2015 criteria to the diagnosis of NMO spectrum disorders (NMOSD) in 40 patients with longitudinal extensive transverse myelitis (LEMT). Methods This is a retrospective, descriptive and analytic study. Results Among NMO patients, there was a predominance of women, with onset in the fourth decade of life, and AQP4-IgG seropositivity in 73.5%. The diagnosis of NMOSD was established in 37.5% of LETM patients according to AQP4-IgG positivity and in 5% of LETM patients if the AQP4-IgG result was unknown. Conclusions The characteristics of this series are similar to those of other Western populations. The AQP4-IgG testing assists in the diagnosis of NMOSD.Academia Brasileira de Neurologia - ABNEURO2017-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017000200002Arquivos de Neuro-Psiquiatria v.75 n.2 2017reponame:Arquivos de neuro-psiquiatria (Online)instname:Academia Brasileira de Neurologiainstacron:ABNEURO10.1590/0004-282x20160193info:eu-repo/semantics/openAccessDel Negro,Maria CristinaMarinho,Patricia Beatriz ChristinoPapais-Alvarenga,Regina Mariaeng2017-02-17T00:00:00Zoai:scielo:S0004-282X2017000200002Revistahttp://www.scielo.br/anphttps://old.scielo.br/oai/scielo-oai.php||revista.arquivos@abneuro.org1678-42270004-282Xopendoar:2017-02-17T00:00Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologiafalse |
dc.title.none.fl_str_mv |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
title |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
spellingShingle |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series Del Negro,Maria Cristina neuromyelitis optica epidemiology cross-sectional studies enzyme-linked immunosorbent assay |
title_short |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
title_full |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
title_fullStr |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
title_full_unstemmed |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
title_sort |
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series |
author |
Del Negro,Maria Cristina |
author_facet |
Del Negro,Maria Cristina Marinho,Patricia Beatriz Christino Papais-Alvarenga,Regina Maria |
author_role |
author |
author2 |
Marinho,Patricia Beatriz Christino Papais-Alvarenga,Regina Maria |
author2_role |
author author |
dc.contributor.author.fl_str_mv |
Del Negro,Maria Cristina Marinho,Patricia Beatriz Christino Papais-Alvarenga,Regina Maria |
dc.subject.por.fl_str_mv |
neuromyelitis optica epidemiology cross-sectional studies enzyme-linked immunosorbent assay |
topic |
neuromyelitis optica epidemiology cross-sectional studies enzyme-linked immunosorbent assay |
description |
ABSTRACT The definition of neuromyelitis optica (NMO) is still evolving. In 2015, the International Panel for NMO Diagnosis was convened to develop revised diagnostic criteria. There have been few studies on NMO in the Brazilian population. Objective To describe the characteristics of 34 Brazilian NMO patients. To evaluate the contribution of the 2015 criteria to the diagnosis of NMO spectrum disorders (NMOSD) in 40 patients with longitudinal extensive transverse myelitis (LEMT). Methods This is a retrospective, descriptive and analytic study. Results Among NMO patients, there was a predominance of women, with onset in the fourth decade of life, and AQP4-IgG seropositivity in 73.5%. The diagnosis of NMOSD was established in 37.5% of LETM patients according to AQP4-IgG positivity and in 5% of LETM patients if the AQP4-IgG result was unknown. Conclusions The characteristics of this series are similar to those of other Western populations. The AQP4-IgG testing assists in the diagnosis of NMOSD. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-02-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017000200002 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2017000200002 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/0004-282x20160193 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
dc.source.none.fl_str_mv |
Arquivos de Neuro-Psiquiatria v.75 n.2 2017 reponame:Arquivos de neuro-psiquiatria (Online) instname:Academia Brasileira de Neurologia instacron:ABNEURO |
instname_str |
Academia Brasileira de Neurologia |
instacron_str |
ABNEURO |
institution |
ABNEURO |
reponame_str |
Arquivos de neuro-psiquiatria (Online) |
collection |
Arquivos de neuro-psiquiatria (Online) |
repository.name.fl_str_mv |
Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologia |
repository.mail.fl_str_mv |
||revista.arquivos@abneuro.org |
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1754212781753630720 |