Moyamoya disease: report of three cases in Brazilian patients

• Autor(a) principal: FRANCO,CLÉLIA MARIA RIBEIRO
• Data de Publicação: 1999
• Outros Autores: FUKUJIMA,MARCIA MAIUMI, OLIVEIRA,ROBERTO DE MAGALHÃES CARNEIRO DE, GABBAI,ALBERTO ALAIN
• Tipo de documento: Relatório
• Idioma: eng
• Título da fonte: Arquivos de neuro-psiquiatria (Online)
• Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1999000300005
• topic: moyamoya disease; adult; chronic occlusive cerebrovascular disorder; stroke

Moyamoya disease (MMD) is a chronic occlusive cerebrovascular disease of unknown etiology reported mainly in the Japanese. Most cases occur in children. The disease is rare in non-Oriental adults manifesting itself mostly as intracerebral hemorrhages. We describe MMD in 2 non-Oriental young adults and one adolescent that developed cerebral infarctions. The adults were medicated with aspirin and no medication was given to the adolescent. All patients did not deteriorate in a follow-up period from 1 to 4 years. Although rare, MMD is an important cause of stroke in young individuals and may well be underreported: only 18 patients have been reported till 1997 in Brazil. Neurologists should include MMD in differential diagnosis of ischemic and hemorrhagic strokes in young adults.