Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report
Autor(a) principal: | |
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Data de Publicação: | 2007 |
Outros Autores: | , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Revista brasileira de terapia intensiva (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-507X2007000400018 |
Resumo: | BACKGROUND AND OBJECTIVES: Cryptogenic fibrosing pleuritis is an extremely rare disease, which can affect both lungs from a very young age. The most common finding is severe lung restriction resulting in both hypoxemic and ventilatory failure. CASE REPORT: Male patient, 26 year old with acute deterioration of chronic respiratory failure. Following admission prolonged mechanical ventilation was necessary. An atypical clinical presentation made the diagnosis difficult, but eventually cryptogenic fibrosing pleuritis and lung fibrosis were established. CONCLUSIONS: The prognostic outcome of patients with the final diagnosis of cryptogenic fibrosing pleuritis is extremely poor, especially in an advanced phase of this disease. We recommend early treatment with corticosteroids or surgical pleural decortication. |
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Revista brasileira de terapia intensiva (Online) |
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Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case reportcryptogenicFibrothoraxlungfibrosispleural decorticationpleural fibrosisBACKGROUND AND OBJECTIVES: Cryptogenic fibrosing pleuritis is an extremely rare disease, which can affect both lungs from a very young age. The most common finding is severe lung restriction resulting in both hypoxemic and ventilatory failure. CASE REPORT: Male patient, 26 year old with acute deterioration of chronic respiratory failure. Following admission prolonged mechanical ventilation was necessary. An atypical clinical presentation made the diagnosis difficult, but eventually cryptogenic fibrosing pleuritis and lung fibrosis were established. CONCLUSIONS: The prognostic outcome of patients with the final diagnosis of cryptogenic fibrosing pleuritis is extremely poor, especially in an advanced phase of this disease. We recommend early treatment with corticosteroids or surgical pleural decortication.Associação de Medicina Intensiva Brasileira - AMIB2007-12-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-507X2007000400018Revista Brasileira de Terapia Intensiva v.19 n.4 2007reponame:Revista brasileira de terapia intensiva (Online)instname:Associação de Medicina Intensiva Brasileira (AMIB)instacron:AMIB10.1590/S0103-507X2007000400018info:eu-repo/semantics/openAccessVerweel,ElsemiekNoble,Jos leZoelen,Christine Groeninx-vanMaat,AlexThijsse,WillyGerritsen,PatriciaBakker,Janeng2008-01-22T00:00:00Zoai:scielo:S0103-507X2007000400018Revistahttp://www.scielo.br/rbtihttps://old.scielo.br/oai/scielo-oai.phpdiretoria@amib.org.br||rbti.artigos@amib.org.br1982-43350103-507Xopendoar:2008-01-22T00:00Revista brasileira de terapia intensiva (Online) - Associação de Medicina Intensiva Brasileira (AMIB)false |
dc.title.none.fl_str_mv |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
title |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
spellingShingle |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report Verweel,Elsemiek cryptogenic Fibrothorax lungfibrosis pleural decortication pleural fibrosis |
title_short |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
title_full |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
title_fullStr |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
title_full_unstemmed |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
title_sort |
Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report |
author |
Verweel,Elsemiek |
author_facet |
Verweel,Elsemiek Noble,Jos le Zoelen,Christine Groeninx-van Maat,Alex Thijsse,Willy Gerritsen,Patricia Bakker,Jan |
author_role |
author |
author2 |
Noble,Jos le Zoelen,Christine Groeninx-van Maat,Alex Thijsse,Willy Gerritsen,Patricia Bakker,Jan |
author2_role |
author author author author author author |
dc.contributor.author.fl_str_mv |
Verweel,Elsemiek Noble,Jos le Zoelen,Christine Groeninx-van Maat,Alex Thijsse,Willy Gerritsen,Patricia Bakker,Jan |
dc.subject.por.fl_str_mv |
cryptogenic Fibrothorax lungfibrosis pleural decortication pleural fibrosis |
topic |
cryptogenic Fibrothorax lungfibrosis pleural decortication pleural fibrosis |
description |
BACKGROUND AND OBJECTIVES: Cryptogenic fibrosing pleuritis is an extremely rare disease, which can affect both lungs from a very young age. The most common finding is severe lung restriction resulting in both hypoxemic and ventilatory failure. CASE REPORT: Male patient, 26 year old with acute deterioration of chronic respiratory failure. Following admission prolonged mechanical ventilation was necessary. An atypical clinical presentation made the diagnosis difficult, but eventually cryptogenic fibrosing pleuritis and lung fibrosis were established. CONCLUSIONS: The prognostic outcome of patients with the final diagnosis of cryptogenic fibrosing pleuritis is extremely poor, especially in an advanced phase of this disease. We recommend early treatment with corticosteroids or surgical pleural decortication. |
publishDate |
2007 |
dc.date.none.fl_str_mv |
2007-12-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-507X2007000400018 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-507X2007000400018 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S0103-507X2007000400018 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Associação de Medicina Intensiva Brasileira - AMIB |
publisher.none.fl_str_mv |
Associação de Medicina Intensiva Brasileira - AMIB |
dc.source.none.fl_str_mv |
Revista Brasileira de Terapia Intensiva v.19 n.4 2007 reponame:Revista brasileira de terapia intensiva (Online) instname:Associação de Medicina Intensiva Brasileira (AMIB) instacron:AMIB |
instname_str |
Associação de Medicina Intensiva Brasileira (AMIB) |
instacron_str |
AMIB |
institution |
AMIB |
reponame_str |
Revista brasileira de terapia intensiva (Online) |
collection |
Revista brasileira de terapia intensiva (Online) |
repository.name.fl_str_mv |
Revista brasileira de terapia intensiva (Online) - Associação de Medicina Intensiva Brasileira (AMIB) |
repository.mail.fl_str_mv |
diretoria@amib.org.br||rbti.artigos@amib.org.br |
_version_ |
1754212856710037504 |