Spinal cord compression in b-thalassemia: follow-up after radiotherapy
Autor(a) principal: | |
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Data de Publicação: | 1998 |
Outros Autores: | , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | São Paulo medical journal (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000600009 |
Resumo: | CONTEXT: Spinal cord compression due to extramedullary hematopoiesis is a well-described but rare syndrome encountered in several clinical hematologic disorders, including <FONT FACE="Symbol">b</font>-thalassemia. CASE REPORT: We report the case of a patient with intermediate <FONT FACE="Symbol">b</font>-thalassemia and crural paraparesis due to spinal cord compression by a paravertebral extramedullary mass. She was successfully treated with low-dose radiotherapy and transfusions. After splenectomy, she was regularly followed up for over four years without transfusion or recurrence of spinal cord compression. DISCUSSION: Extramedullary hematopoiesis should be investigated in patients with hematologic disorders and spinal cord symptoms. The rapid recognition and treatment with radiotherapy can dramatically alleviate symptoms. |
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Spinal cord compression in b-thalassemia: follow-up after radiotherapyExtramedullary hematopoiesisSpinal cord compressionIntermediate <FONT FACE=Symbol>b</font>-thalassemiaCONTEXT: Spinal cord compression due to extramedullary hematopoiesis is a well-described but rare syndrome encountered in several clinical hematologic disorders, including <FONT FACE="Symbol">b</font>-thalassemia. CASE REPORT: We report the case of a patient with intermediate <FONT FACE="Symbol">b</font>-thalassemia and crural paraparesis due to spinal cord compression by a paravertebral extramedullary mass. She was successfully treated with low-dose radiotherapy and transfusions. After splenectomy, she was regularly followed up for over four years without transfusion or recurrence of spinal cord compression. DISCUSSION: Extramedullary hematopoiesis should be investigated in patients with hematologic disorders and spinal cord symptoms. The rapid recognition and treatment with radiotherapy can dramatically alleviate symptoms.Associação Paulista de Medicina - APM1998-11-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000600009Sao Paulo Medical Journal v.116 n.6 1998reponame:São Paulo medical journal (Online)instname:Associação Paulista de Medicinainstacron:APM10.1590/S1516-31801998000600009info:eu-repo/semantics/openAccessFonseca,Silvana Fahel daFigueiredo,Maria StellaCançado,Rodolfo DelfiniNakandakare,FernandoSegreto,RobertoKerbauy,Joséeng1999-12-17T00:00:00Zoai:scielo:S1516-31801998000600009Revistahttp://www.scielo.br/spmjhttps://old.scielo.br/oai/scielo-oai.phprevistas@apm.org.br1806-94601516-3180opendoar:1999-12-17T00:00São Paulo medical journal (Online) - Associação Paulista de Medicinafalse |
dc.title.none.fl_str_mv |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
title |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
spellingShingle |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy Fonseca,Silvana Fahel da Extramedullary hematopoiesis Spinal cord compression Intermediate <FONT FACE=Symbol>b</font>-thalassemia |
title_short |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
title_full |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
title_fullStr |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
title_full_unstemmed |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
title_sort |
Spinal cord compression in b-thalassemia: follow-up after radiotherapy |
author |
Fonseca,Silvana Fahel da |
author_facet |
Fonseca,Silvana Fahel da Figueiredo,Maria Stella Cançado,Rodolfo Delfini Nakandakare,Fernando Segreto,Roberto Kerbauy,José |
author_role |
author |
author2 |
Figueiredo,Maria Stella Cançado,Rodolfo Delfini Nakandakare,Fernando Segreto,Roberto Kerbauy,José |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Fonseca,Silvana Fahel da Figueiredo,Maria Stella Cançado,Rodolfo Delfini Nakandakare,Fernando Segreto,Roberto Kerbauy,José |
dc.subject.por.fl_str_mv |
Extramedullary hematopoiesis Spinal cord compression Intermediate <FONT FACE=Symbol>b</font>-thalassemia |
topic |
Extramedullary hematopoiesis Spinal cord compression Intermediate <FONT FACE=Symbol>b</font>-thalassemia |
description |
CONTEXT: Spinal cord compression due to extramedullary hematopoiesis is a well-described but rare syndrome encountered in several clinical hematologic disorders, including <FONT FACE="Symbol">b</font>-thalassemia. CASE REPORT: We report the case of a patient with intermediate <FONT FACE="Symbol">b</font>-thalassemia and crural paraparesis due to spinal cord compression by a paravertebral extramedullary mass. She was successfully treated with low-dose radiotherapy and transfusions. After splenectomy, she was regularly followed up for over four years without transfusion or recurrence of spinal cord compression. DISCUSSION: Extramedullary hematopoiesis should be investigated in patients with hematologic disorders and spinal cord symptoms. The rapid recognition and treatment with radiotherapy can dramatically alleviate symptoms. |
publishDate |
1998 |
dc.date.none.fl_str_mv |
1998-11-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000600009 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000600009 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S1516-31801998000600009 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Associação Paulista de Medicina - APM |
publisher.none.fl_str_mv |
Associação Paulista de Medicina - APM |
dc.source.none.fl_str_mv |
Sao Paulo Medical Journal v.116 n.6 1998 reponame:São Paulo medical journal (Online) instname:Associação Paulista de Medicina instacron:APM |
instname_str |
Associação Paulista de Medicina |
instacron_str |
APM |
institution |
APM |
reponame_str |
São Paulo medical journal (Online) |
collection |
São Paulo medical journal (Online) |
repository.name.fl_str_mv |
São Paulo medical journal (Online) - Associação Paulista de Medicina |
repository.mail.fl_str_mv |
revistas@apm.org.br |
_version_ |
1754209259953848320 |