Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report

Detalhes bibliográficos
Autor(a) principal: Cihan,Yasemin Benderli
Data de Publicação: 2019
Outros Autores: Kut,Engin, Koç,Ali
Tipo de documento: Relatório
Idioma: eng
Título da fonte: São Paulo medical journal (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802019000200206
Resumo: ABSTRACT CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa.
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spelling Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case reportPerivascular epithelioid cell neoplasmsRetroperitoneal neoplasmsAntineoplastic protocolsABSTRACT CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa.Associação Paulista de Medicina - APM2019-04-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802019000200206Sao Paulo Medical Journal v.137 n.2 2019reponame:São Paulo medical journal (Online)instname:Associação Paulista de Medicinainstacron:APM10.1590/1516-3180.2017.0120050717info:eu-repo/semantics/openAccessCihan,Yasemin BenderliKut,EnginKoç,Alieng2019-07-10T00:00:00Zoai:scielo:S1516-31802019000200206Revistahttp://www.scielo.br/spmjhttps://old.scielo.br/oai/scielo-oai.phprevistas@apm.org.br1806-94601516-3180opendoar:2019-07-10T00:00São Paulo medical journal (Online) - Associação Paulista de Medicinafalse
dc.title.none.fl_str_mv Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
spellingShingle Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
Cihan,Yasemin Benderli
Perivascular epithelioid cell neoplasms
Retroperitoneal neoplasms
Antineoplastic protocols
title_short Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_full Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_fullStr Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_full_unstemmed Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
title_sort Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
author Cihan,Yasemin Benderli
author_facet Cihan,Yasemin Benderli
Kut,Engin
Koç,Ali
author_role author
author2 Kut,Engin
Koç,Ali
author2_role author
author
dc.contributor.author.fl_str_mv Cihan,Yasemin Benderli
Kut,Engin
Koç,Ali
dc.subject.por.fl_str_mv Perivascular epithelioid cell neoplasms
Retroperitoneal neoplasms
Antineoplastic protocols
topic Perivascular epithelioid cell neoplasms
Retroperitoneal neoplasms
Antineoplastic protocols
description ABSTRACT CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa.
publishDate 2019
dc.date.none.fl_str_mv 2019-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802019000200206
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802019000200206
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1516-3180.2017.0120050717
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Associação Paulista de Medicina - APM
publisher.none.fl_str_mv Associação Paulista de Medicina - APM
dc.source.none.fl_str_mv Sao Paulo Medical Journal v.137 n.2 2019
reponame:São Paulo medical journal (Online)
instname:Associação Paulista de Medicina
instacron:APM
instname_str Associação Paulista de Medicina
instacron_str APM
institution APM
reponame_str São Paulo medical journal (Online)
collection São Paulo medical journal (Online)
repository.name.fl_str_mv São Paulo medical journal (Online) - Associação Paulista de Medicina
repository.mail.fl_str_mv revistas@apm.org.br
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