Síndrome de Peutz-Jeghers: relato de caso

Detalhes bibliográficos
Autor(a) principal: Andrade,Aderivaldo Coelho de
Data de Publicação: 2008
Outros Autores: Carvalho Júnior,Edílson, Dantas,Karoline da Silva, Sousa,Jocerlano Santos de, Morais,Ricardo Keyson Paiva de
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista do Colégio Brasileiro de Cirurgiões
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-69912008000300015
Resumo: Peutz-Jeghers syndrome (PJS) is a dominant autosomal inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous melanocytic maculae. This syndrome is rare, and the frequency reaches from 1 in 60,000 to 1 in 300,000 people in the USA. The symptom presentations vary greatly in this disease. Some patients require minor clinical treatment while others undergo many hospitalizations and surgical treatments. In addition, patients with PJS have an increased risk for developing a variety of malignant tumors. The aim of the present study was to report one case studied of Peutz-Jeghers syndrome.
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spelling Síndrome de Peutz-Jeghers: relato de casoPeutz-Jeghers syndromeHamartomaColonic polypsMelanocytesPeutz-Jeghers syndrome (PJS) is a dominant autosomal inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous melanocytic maculae. This syndrome is rare, and the frequency reaches from 1 in 60,000 to 1 in 300,000 people in the USA. The symptom presentations vary greatly in this disease. Some patients require minor clinical treatment while others undergo many hospitalizations and surgical treatments. In addition, patients with PJS have an increased risk for developing a variety of malignant tumors. The aim of the present study was to report one case studied of Peutz-Jeghers syndrome.Colégio Brasileiro de Cirurgiões2008-06-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-69912008000300015Revista do Colégio Brasileiro de Cirurgiões v.35 n.3 2008reponame:Revista do Colégio Brasileiro de Cirurgiõesinstname:Colégio Brasileiro de Cirurgiões (CBC)instacron:CBC10.1590/S0100-69912008000300015info:eu-repo/semantics/openAccessAndrade,Aderivaldo Coelho deCarvalho Júnior,EdílsonDantas,Karoline da SilvaSousa,Jocerlano Santos deMorais,Ricardo Keyson Paiva depor2008-07-28T00:00:00Zoai:scielo:S0100-69912008000300015Revistahttp://www.scielo.br/rcbcONGhttps://old.scielo.br/oai/scielo-oai.php||revistacbc@cbc.org.br1809-45460100-6991opendoar:2008-07-28T00:00Revista do Colégio Brasileiro de Cirurgiões - Colégio Brasileiro de Cirurgiões (CBC)false
dc.title.none.fl_str_mv Síndrome de Peutz-Jeghers: relato de caso
title Síndrome de Peutz-Jeghers: relato de caso
spellingShingle Síndrome de Peutz-Jeghers: relato de caso
Andrade,Aderivaldo Coelho de
Peutz-Jeghers syndrome
Hamartoma
Colonic polyps
Melanocytes
title_short Síndrome de Peutz-Jeghers: relato de caso
title_full Síndrome de Peutz-Jeghers: relato de caso
title_fullStr Síndrome de Peutz-Jeghers: relato de caso
title_full_unstemmed Síndrome de Peutz-Jeghers: relato de caso
title_sort Síndrome de Peutz-Jeghers: relato de caso
author Andrade,Aderivaldo Coelho de
author_facet Andrade,Aderivaldo Coelho de
Carvalho Júnior,Edílson
Dantas,Karoline da Silva
Sousa,Jocerlano Santos de
Morais,Ricardo Keyson Paiva de
author_role author
author2 Carvalho Júnior,Edílson
Dantas,Karoline da Silva
Sousa,Jocerlano Santos de
Morais,Ricardo Keyson Paiva de
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Andrade,Aderivaldo Coelho de
Carvalho Júnior,Edílson
Dantas,Karoline da Silva
Sousa,Jocerlano Santos de
Morais,Ricardo Keyson Paiva de
dc.subject.por.fl_str_mv Peutz-Jeghers syndrome
Hamartoma
Colonic polyps
Melanocytes
topic Peutz-Jeghers syndrome
Hamartoma
Colonic polyps
Melanocytes
description Peutz-Jeghers syndrome (PJS) is a dominant autosomal inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous melanocytic maculae. This syndrome is rare, and the frequency reaches from 1 in 60,000 to 1 in 300,000 people in the USA. The symptom presentations vary greatly in this disease. Some patients require minor clinical treatment while others undergo many hospitalizations and surgical treatments. In addition, patients with PJS have an increased risk for developing a variety of malignant tumors. The aim of the present study was to report one case studied of Peutz-Jeghers syndrome.
publishDate 2008
dc.date.none.fl_str_mv 2008-06-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-69912008000300015
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-69912008000300015
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv 10.1590/S0100-69912008000300015
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Colégio Brasileiro de Cirurgiões
publisher.none.fl_str_mv Colégio Brasileiro de Cirurgiões
dc.source.none.fl_str_mv Revista do Colégio Brasileiro de Cirurgiões v.35 n.3 2008
reponame:Revista do Colégio Brasileiro de Cirurgiões
instname:Colégio Brasileiro de Cirurgiões (CBC)
instacron:CBC
instname_str Colégio Brasileiro de Cirurgiões (CBC)
instacron_str CBC
institution CBC
reponame_str Revista do Colégio Brasileiro de Cirurgiões
collection Revista do Colégio Brasileiro de Cirurgiões
repository.name.fl_str_mv Revista do Colégio Brasileiro de Cirurgiões - Colégio Brasileiro de Cirurgiões (CBC)
repository.mail.fl_str_mv ||revistacbc@cbc.org.br
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