Audiological characteristics in mucopolysaccharidosis: a systematic literature review

Detalhes bibliográficos
Autor(a) principal: Chimelo,Flávia Teixeira
Data de Publicação: 2019
Outros Autores: Silva,Liliane Aparecida Fagundes, Kim,Chong Ae, Matas,Carla Gentile
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Revista CEFAC (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-18462019000500604
Resumo: ABSTRACT Purpose: to describe the audiological characteristics of patients with mucopolysaccharidosis. Methods: after formulating the research question, three databases were considered for the search (Science Direct, Virtual Health Library and Web of Science); the following descriptors were used: mucopolysaccharidoses, hearing loss, and audiology. Articles were included that were original and complete, presenting audiological evaluation data in patients with mucopolysaccharidosis. Each study was classified according to the degree of recommendation and the level of scientific evidence, based on the criteria established by the Oxford Center for Evidence-based Medicine, and the results obtained from the evaluations were analyzed. Results: of the 499 articles found, eight met the inclusion criteria. Pure tone audiometry and tympanometry were performed in all studies. The incidence of hearing loss in patients with MPS ranged from 54% to 100% of the cases, with conductive hearing loss corresponding to 30% and 58.33%, mixed hearing loss corresponding to 28.5% and 66.66% and sensorineural hearing loss corresponding to less than 14%. None of the studies described the responses of otoacoustic emissions and auditory evoked potentials. Conclusion: the prevalence of hearing loss among individuals with MPS is higher than 54% of the cases, of which conductive and mixed are predominant.
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spelling Audiological characteristics in mucopolysaccharidosis: a systematic literature reviewHearing LossMucopolysaccharidosesAudiologyABSTRACT Purpose: to describe the audiological characteristics of patients with mucopolysaccharidosis. Methods: after formulating the research question, three databases were considered for the search (Science Direct, Virtual Health Library and Web of Science); the following descriptors were used: mucopolysaccharidoses, hearing loss, and audiology. Articles were included that were original and complete, presenting audiological evaluation data in patients with mucopolysaccharidosis. Each study was classified according to the degree of recommendation and the level of scientific evidence, based on the criteria established by the Oxford Center for Evidence-based Medicine, and the results obtained from the evaluations were analyzed. Results: of the 499 articles found, eight met the inclusion criteria. Pure tone audiometry and tympanometry were performed in all studies. The incidence of hearing loss in patients with MPS ranged from 54% to 100% of the cases, with conductive hearing loss corresponding to 30% and 58.33%, mixed hearing loss corresponding to 28.5% and 66.66% and sensorineural hearing loss corresponding to less than 14%. None of the studies described the responses of otoacoustic emissions and auditory evoked potentials. Conclusion: the prevalence of hearing loss among individuals with MPS is higher than 54% of the cases, of which conductive and mixed are predominant.ABRAMO Associação Brasileira de Motricidade Orofacial2019-01-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-18462019000500604Revista CEFAC v.21 n.5 2019reponame:Revista CEFAC (Online)instname:Centro de Especialização em Fonoaudiologia Clínica (CEFAC)instacron:CEFAC10.1590/1982-0216/201921516218info:eu-repo/semantics/openAccessChimelo,Flávia TeixeiraSilva,Liliane Aparecida FagundesKim,Chong AeMatas,Carla Gentileeng2019-10-07T00:00:00Zoai:scielo:S1516-18462019000500604Revistahttp://www.revistacefac.com.br/https://old.scielo.br/oai/scielo-oai.php||revistacefac@cefac.br1982-02161516-1846opendoar:2019-10-07T00:00Revista CEFAC (Online) - Centro de Especialização em Fonoaudiologia Clínica (CEFAC)false
dc.title.none.fl_str_mv Audiological characteristics in mucopolysaccharidosis: a systematic literature review
title Audiological characteristics in mucopolysaccharidosis: a systematic literature review
spellingShingle Audiological characteristics in mucopolysaccharidosis: a systematic literature review
Chimelo,Flávia Teixeira
Hearing Loss
Mucopolysaccharidoses
Audiology
title_short Audiological characteristics in mucopolysaccharidosis: a systematic literature review
title_full Audiological characteristics in mucopolysaccharidosis: a systematic literature review
title_fullStr Audiological characteristics in mucopolysaccharidosis: a systematic literature review
title_full_unstemmed Audiological characteristics in mucopolysaccharidosis: a systematic literature review
title_sort Audiological characteristics in mucopolysaccharidosis: a systematic literature review
author Chimelo,Flávia Teixeira
author_facet Chimelo,Flávia Teixeira
Silva,Liliane Aparecida Fagundes
Kim,Chong Ae
Matas,Carla Gentile
author_role author
author2 Silva,Liliane Aparecida Fagundes
Kim,Chong Ae
Matas,Carla Gentile
author2_role author
author
author
dc.contributor.author.fl_str_mv Chimelo,Flávia Teixeira
Silva,Liliane Aparecida Fagundes
Kim,Chong Ae
Matas,Carla Gentile
dc.subject.por.fl_str_mv Hearing Loss
Mucopolysaccharidoses
Audiology
topic Hearing Loss
Mucopolysaccharidoses
Audiology
description ABSTRACT Purpose: to describe the audiological characteristics of patients with mucopolysaccharidosis. Methods: after formulating the research question, three databases were considered for the search (Science Direct, Virtual Health Library and Web of Science); the following descriptors were used: mucopolysaccharidoses, hearing loss, and audiology. Articles were included that were original and complete, presenting audiological evaluation data in patients with mucopolysaccharidosis. Each study was classified according to the degree of recommendation and the level of scientific evidence, based on the criteria established by the Oxford Center for Evidence-based Medicine, and the results obtained from the evaluations were analyzed. Results: of the 499 articles found, eight met the inclusion criteria. Pure tone audiometry and tympanometry were performed in all studies. The incidence of hearing loss in patients with MPS ranged from 54% to 100% of the cases, with conductive hearing loss corresponding to 30% and 58.33%, mixed hearing loss corresponding to 28.5% and 66.66% and sensorineural hearing loss corresponding to less than 14%. None of the studies described the responses of otoacoustic emissions and auditory evoked potentials. Conclusion: the prevalence of hearing loss among individuals with MPS is higher than 54% of the cases, of which conductive and mixed are predominant.
publishDate 2019
dc.date.none.fl_str_mv 2019-01-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-18462019000500604
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-18462019000500604
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1982-0216/201921516218
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv ABRAMO Associação Brasileira de Motricidade Orofacial
publisher.none.fl_str_mv ABRAMO Associação Brasileira de Motricidade Orofacial
dc.source.none.fl_str_mv Revista CEFAC v.21 n.5 2019
reponame:Revista CEFAC (Online)
instname:Centro de Especialização em Fonoaudiologia Clínica (CEFAC)
instacron:CEFAC
instname_str Centro de Especialização em Fonoaudiologia Clínica (CEFAC)
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reponame_str Revista CEFAC (Online)
collection Revista CEFAC (Online)
repository.name.fl_str_mv Revista CEFAC (Online) - Centro de Especialização em Fonoaudiologia Clínica (CEFAC)
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