Independent walk in osteogenesis imperfecta

Detalhes bibliográficos
Autor(a) principal: Moreira, Carmem Lia Martins
Data de Publicação: 2011
Outros Autores: Lima, Maria Agelica de Faria Domingues, Cardoso, Maria Helena Cabral de Almeida, Gomes Junior, Saint Clair dos Santos, Lopes, Paula Bacellar, Llerena Junior, Juan Clinton
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da FIOCRUZ (ARCA)
Texto Completo: https://www.arca.fiocruz.br/handle/icict/9373
Resumo: Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.
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spelling Moreira, Carmem Lia MartinsLima, Maria Agelica de Faria DominguesCardoso, Maria Helena Cabral de AlmeidaGomes Junior, Saint Clair dos SantosLopes, Paula BacellarLlerena Junior, Juan Clinton2015-01-13T12:45:07Z2015-01-13T12:45:07Z2011MOREIRA, Carmem Lia Martins et al. Independent walk in osteogensis imperfecta. Acta ortop. bras., Sao Paulo, v. 19, n. 5, p. 312-315, 2011.1413-7852https://www.arca.fiocruz.br/handle/icict/9373engSociedade Brasileira de Ortopedia e TraumatologiaIndependent walk in osteogenesis imperfectainfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleFundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.Instituto Nacional do Câncer. Genética Médica. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.Objectives: investigation of the locomotion process in patients with osteogenesis imperfecta (OI), and the factors that influence it, with special attention to clinical aspects relating to motor rehabilitation. Methods: a retrospective, cross-sectional study was carried out at the physical therapy outpatient clinic of the Instituto Fernandes Figueira. All patients with a clinical diagnosis of OI were included. Patients with other diseases, and those aged under two years, old were excluded. Epi-Info version 3.4 was used to construct the database, and SPSS version 15 for the statistical analysis. Results: The odds-ratio was used to measure the association between independent walking and clinical characteristics, adopting a level of significance of 5% for the analysis. Results: 69 patients were included. Of these, 43.5% were classified as OI type I; 37.7% as type III and 18.8% as type IV. 76.8% presented long bone deformities. A negative association was observed between hypotonia, number of fractures, and independent walking. A positive association was observed between independent walking and OI type I. Conclusions: physical therapy, as a complementary approach to orthopedics, and the administration of medications of the biophosphonates class, are of fundamental importance for the rehabilitation of motor capacity of individuals with OI. Level of Evidence, cross sectional.Physical TherapyOsteogenesis ImperfectaGaitMobility LimitationCross-Sectional StudiesFisioterapiaOsteogênese ImperfeitaMarchaLimitação da MobilidadeEstudos Transversaisinfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da FIOCRUZ (ARCA)instname:Fundação Oswaldo Cruz (FIOCRUZ)instacron:FIOCRUZLICENSElicense.txtlicense.txttext/plain; charset=utf-81914https://www.arca.fiocruz.br/bitstream/icict/9373/1/license.txt7d48279ffeed55da8dfe2f8e81f3b81fMD51ORIGINALIndependent walk in osteogenesis imperfecta.pdfIndependent walk in osteogenesis imperfecta.pdfapplication/pdf208285https://www.arca.fiocruz.br/bitstream/icict/9373/2/Independent%20walk%20in%20osteogenesis%20imperfecta.pdfaed3252af5081c2351a78aaac7e5d382MD52TEXTIndependent walk in osteogenesis imperfecta.pdf.txtIndependent walk in osteogenesis imperfecta.pdf.txtExtracted texttext/plain21919https://www.arca.fiocruz.br/bitstream/icict/9373/3/Independent%20walk%20in%20osteogenesis%20imperfecta.pdf.txt0177e6589a9ffd1b7b5e4996684d96a7MD53icict/93732020-05-26 14:05:28.071oai:www.arca.fiocruz.br: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ório InstitucionalPUBhttps://www.arca.fiocruz.br/oai/requestrepositorio.arca@fiocruz.bropendoar:21352020-05-26T17:05:28Repositório Institucional da FIOCRUZ (ARCA) - Fundação Oswaldo Cruz (FIOCRUZ)false
dc.title.pt_BR.fl_str_mv Independent walk in osteogenesis imperfecta
title Independent walk in osteogenesis imperfecta
spellingShingle Independent walk in osteogenesis imperfecta
Moreira, Carmem Lia Martins
Physical Therapy
Osteogenesis Imperfecta
Gait
Mobility Limitation
Cross-Sectional Studies
Fisioterapia
Osteogênese Imperfeita
Marcha
Limitação da Mobilidade
Estudos Transversais
title_short Independent walk in osteogenesis imperfecta
title_full Independent walk in osteogenesis imperfecta
title_fullStr Independent walk in osteogenesis imperfecta
title_full_unstemmed Independent walk in osteogenesis imperfecta
title_sort Independent walk in osteogenesis imperfecta
author Moreira, Carmem Lia Martins
author_facet Moreira, Carmem Lia Martins
Lima, Maria Agelica de Faria Domingues
Cardoso, Maria Helena Cabral de Almeida
Gomes Junior, Saint Clair dos Santos
Lopes, Paula Bacellar
Llerena Junior, Juan Clinton
author_role author
author2 Lima, Maria Agelica de Faria Domingues
Cardoso, Maria Helena Cabral de Almeida
Gomes Junior, Saint Clair dos Santos
Lopes, Paula Bacellar
Llerena Junior, Juan Clinton
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Moreira, Carmem Lia Martins
Lima, Maria Agelica de Faria Domingues
Cardoso, Maria Helena Cabral de Almeida
Gomes Junior, Saint Clair dos Santos
Lopes, Paula Bacellar
Llerena Junior, Juan Clinton
dc.subject.en.pt_BR.fl_str_mv Physical Therapy
Osteogenesis Imperfecta
Gait
Mobility Limitation
Cross-Sectional Studies
topic Physical Therapy
Osteogenesis Imperfecta
Gait
Mobility Limitation
Cross-Sectional Studies
Fisioterapia
Osteogênese Imperfeita
Marcha
Limitação da Mobilidade
Estudos Transversais
dc.subject.decs.pt_BR.fl_str_mv Fisioterapia
Osteogênese Imperfeita
Marcha
Limitação da Mobilidade
Estudos Transversais
description Fundação Oswaldo Cruz. Instituto Nacional da Saúde da Mulher e da Criança Fernandes Figueira. Departamento de Genética Médica. Rio de Janeiro, RJ, Brasil.
publishDate 2011
dc.date.issued.fl_str_mv 2011
dc.date.accessioned.fl_str_mv 2015-01-13T12:45:07Z
dc.date.available.fl_str_mv 2015-01-13T12:45:07Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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status_str publishedVersion
dc.identifier.citation.fl_str_mv MOREIRA, Carmem Lia Martins et al. Independent walk in osteogensis imperfecta. Acta ortop. bras., Sao Paulo, v. 19, n. 5, p. 312-315, 2011.
dc.identifier.uri.fl_str_mv https://www.arca.fiocruz.br/handle/icict/9373
dc.identifier.issn.none.fl_str_mv 1413-7852
identifier_str_mv MOREIRA, Carmem Lia Martins et al. Independent walk in osteogensis imperfecta. Acta ortop. bras., Sao Paulo, v. 19, n. 5, p. 312-315, 2011.
1413-7852
url https://www.arca.fiocruz.br/handle/icict/9373
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dc.publisher.none.fl_str_mv Sociedade Brasileira de Ortopedia e Traumatologia
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