Angiossarcoma do couro cabeludo: relato de caso

Detalhes bibliográficos
Autor(a) principal: Martinez, Daniela de Abreu e Silva
Data de Publicação: 2017
Outros Autores: Lyra, Marcelo Rosandiski, Cuzzi, Tullia, Macedo, Priscila Marques de, Lima, Ricardo Barbosa, Martins, Carlos José
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Institucional da FIOCRUZ (ARCA)
Texto Completo: https://www.arca.fiocruz.br/handle/icict/34446
Resumo: Angiosarcoma of the head and neck is a rare vascular sarcoma associated with high rates of local recurrence and distant metastasis and a poor prognosis. The diagnosis of cutaneous angiosarcoma can be challenging because it often presents insidiously as a bruiselike lesion or a purplish papule that may be mistaken for a benign lesion such as hemangioma. The tumor size is a important prognostic factor and a multi modality treatment approach is imperative for successful outcomes. This study reports the case of 58-years-man with angiosarcoma of the scalp aggressive and a poor prognosis.
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spelling Martinez, Daniela de Abreu e SilvaLyra, Marcelo RosandiskiCuzzi, TulliaMacedo, Priscila Marques deLima, Ricardo BarbosaMartins, Carlos José2019-07-26T14:55:49Z2019-07-26T14:55:49Z2017MATINEZ, Daniela de Abreu e Silva et al. Angiossarcoma do couro cabeludo: relato de caso. Medicina, v. 50, n. 2, p. 134-138, 2017.0076-6046https://www.arca.fiocruz.br/handle/icict/3444610.11606/issn.2176-7262.v50i2p134-1382176-7262Angiosarcoma of the head and neck is a rare vascular sarcoma associated with high rates of local recurrence and distant metastasis and a poor prognosis. The diagnosis of cutaneous angiosarcoma can be challenging because it often presents insidiously as a bruiselike lesion or a purplish papule that may be mistaken for a benign lesion such as hemangioma. The tumor size is a important prognostic factor and a multi modality treatment approach is imperative for successful outcomes. This study reports the case of 58-years-man with angiosarcoma of the scalp aggressive and a poor prognosis.O angiossarcoma é uma rara neoplasia vascular originada das células endoteliais. É muito agressivo com alta taxa de recorrência, metástases precoces e mau prognóstico. O diagnóstico precoce do angiossarcoma é um desafio, pois muitas vezes apresenta-se como uma equimose ou pápula violácea que pode ser confundida com lesão benigna como um hemangioma. O tamanho do tumor é um fator prognóstico importante e o diagnóstico precoce e tratamento combinado são fundamentais para aumentar a sobrevida desses pacientes. Esse estudo relata o caso de um homem de 58 anos de idade com angiossarcoma de couro cabeludo altamente agressivo e prognóstico reservado.Universidade Federal do Estado do Rio de Janeiro. Hospital Universitário Gaffrée e Guinle. Setor de Dermatologia. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto de Infectologia Evandro Chagas. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto de Infectologia Evandro Chagas. Rio de Janeiro, RJ, Brasil.Fundação Oswaldo Cruz. Instituto de Infectologia Evandro Chagas. Rio de Janeiro, RJ, Brasil.Universidade Federal do Estado do Rio de Janeiro. Hospital Universitário Gaffrée e Guinle. Setor de Dermatologia. Rio de Janeiro, RJ, Brasil.Universidade Federal do Estado do Rio de Janeiro. Hospital Universitário Gaffrée e Guinle. Setor de Dermatologia. Rio de Janeiro, RJ, Brasil.porAngiossarcomaNeoplasiasNeoplasias de tecido vascularAngiosarcomaNeoplasmsVascular tissue neoplasmsAngiossarcoma do couro cabeludo: relato de casoAngiosarcoma of the scalp: case reportinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleinfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da FIOCRUZ (ARCA)instname:Fundação Oswaldo Cruz (FIOCRUZ)instacron:FIOCRUZLICENSElicense.txttext/plain1748https://www.arca.fiocruz.br/bitstream/icict/34446/1/license.txt8a4605be74aa9ea9d79846c1fba20a33MD51ORIGINALve_Martinez_Daniela_etal_INI_2017.pdfve_Martinez_Daniela_etal_INI_2017.pdfapplication/pdf698200https://www.arca.fiocruz.br/bitstream/icict/34446/2/ve_Martinez_Daniela_etal_INI_2017.pdf89518c4b830e8a4632597668bbf4d80cMD52TEXTve_Martinez_Daniela_etal_INI_2017.pdf.txtve_Martinez_Daniela_etal_INI_2017.pdf.txtExtracted texttext/plain9073https://www.arca.fiocruz.br/bitstream/icict/34446/3/ve_Martinez_Daniela_etal_INI_2017.pdf.txt1b32c897fb9b1a5f3a703018b51c10b6MD53icict/344462019-07-27 02:03:02.89oai:www.arca.fiocruz.br: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Repositório InstitucionalPUBhttps://www.arca.fiocruz.br/oai/requestrepositorio.arca@fiocruz.bropendoar:21352019-07-27T05:03:02Repositório Institucional da FIOCRUZ (ARCA) - Fundação Oswaldo Cruz (FIOCRUZ)false
dc.title.pt_BR.fl_str_mv Angiossarcoma do couro cabeludo: relato de caso
dc.title.alternative.pt_BR.fl_str_mv Angiosarcoma of the scalp: case report
title Angiossarcoma do couro cabeludo: relato de caso
spellingShingle Angiossarcoma do couro cabeludo: relato de caso
Martinez, Daniela de Abreu e Silva
Angiossarcoma
Neoplasias
Neoplasias de tecido vascular
Angiosarcoma
Neoplasms
Vascular tissue neoplasms
title_short Angiossarcoma do couro cabeludo: relato de caso
title_full Angiossarcoma do couro cabeludo: relato de caso
title_fullStr Angiossarcoma do couro cabeludo: relato de caso
title_full_unstemmed Angiossarcoma do couro cabeludo: relato de caso
title_sort Angiossarcoma do couro cabeludo: relato de caso
author Martinez, Daniela de Abreu e Silva
author_facet Martinez, Daniela de Abreu e Silva
Lyra, Marcelo Rosandiski
Cuzzi, Tullia
Macedo, Priscila Marques de
Lima, Ricardo Barbosa
Martins, Carlos José
author_role author
author2 Lyra, Marcelo Rosandiski
Cuzzi, Tullia
Macedo, Priscila Marques de
Lima, Ricardo Barbosa
Martins, Carlos José
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Martinez, Daniela de Abreu e Silva
Lyra, Marcelo Rosandiski
Cuzzi, Tullia
Macedo, Priscila Marques de
Lima, Ricardo Barbosa
Martins, Carlos José
dc.subject.other.pt_BR.fl_str_mv Angiossarcoma
Neoplasias
Neoplasias de tecido vascular
topic Angiossarcoma
Neoplasias
Neoplasias de tecido vascular
Angiosarcoma
Neoplasms
Vascular tissue neoplasms
dc.subject.en.pt_BR.fl_str_mv Angiosarcoma
Neoplasms
Vascular tissue neoplasms
description Angiosarcoma of the head and neck is a rare vascular sarcoma associated with high rates of local recurrence and distant metastasis and a poor prognosis. The diagnosis of cutaneous angiosarcoma can be challenging because it often presents insidiously as a bruiselike lesion or a purplish papule that may be mistaken for a benign lesion such as hemangioma. The tumor size is a important prognostic factor and a multi modality treatment approach is imperative for successful outcomes. This study reports the case of 58-years-man with angiosarcoma of the scalp aggressive and a poor prognosis.
publishDate 2017
dc.date.issued.fl_str_mv 2017
dc.date.accessioned.fl_str_mv 2019-07-26T14:55:49Z
dc.date.available.fl_str_mv 2019-07-26T14:55:49Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.citation.fl_str_mv MATINEZ, Daniela de Abreu e Silva et al. Angiossarcoma do couro cabeludo: relato de caso. Medicina, v. 50, n. 2, p. 134-138, 2017.
dc.identifier.uri.fl_str_mv https://www.arca.fiocruz.br/handle/icict/34446
dc.identifier.issn.pt_BR.fl_str_mv 0076-6046
dc.identifier.doi.pt_BR.fl_str_mv 10.11606/issn.2176-7262.v50i2p134-138
dc.identifier.eissn.none.fl_str_mv 2176-7262
identifier_str_mv MATINEZ, Daniela de Abreu e Silva et al. Angiossarcoma do couro cabeludo: relato de caso. Medicina, v. 50, n. 2, p. 134-138, 2017.
0076-6046
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