Herlyn-Werner-Wunderlich syndrome: a case report

Detalhes bibliográficos
Autor(a) principal: Piccinini,Pedro Salomao
Data de Publicação: 2015
Outros Autores: Doski,John
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Revista brasileira de ginecologia e obstetrícia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032015000400192
Resumo: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disorder of the Müllerian ducts in which there is uterus didelphys, obstructed hemivagina and unilateral renal agenesis. The most common presentation is an abdominal mass secondary to hematocolpos, pain and dysmenorrhea. However, in some cases, such as the one we present here, menses are normal due to an obstructed hemivagina, and diagnosis can be delayed. We describe evaluation and surgical management of a 13-year-old girl with this condition who was diagnosed by computed tomography (CT) scan and confirmed by pelvic ultrasound and surgical exploration, as well as a review of the literature.
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spelling Herlyn-Werner-Wunderlich syndrome: a case reportMüllerian ductsVaginaUterusKidneyHerlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disorder of the Müllerian ducts in which there is uterus didelphys, obstructed hemivagina and unilateral renal agenesis. The most common presentation is an abdominal mass secondary to hematocolpos, pain and dysmenorrhea. However, in some cases, such as the one we present here, menses are normal due to an obstructed hemivagina, and diagnosis can be delayed. We describe evaluation and surgical management of a 13-year-old girl with this condition who was diagnosed by computed tomography (CT) scan and confirmed by pelvic ultrasound and surgical exploration, as well as a review of the literature.Federação Brasileira das Sociedades de Ginecologia e Obstetrícia2015-04-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032015000400192Revista Brasileira de Ginecologia e Obstetrícia v.37 n.4 2015reponame:Revista brasileira de ginecologia e obstetrícia (Online)instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)instacron:FEBRASGO10.1590/SO100-720320150005077info:eu-repo/semantics/openAccessPiccinini,Pedro SalomaoDoski,Johneng2015-09-10T00:00:00Zoai:scielo:S0100-72032015000400192Revistahttp://www.scielo.br/rbgohttps://old.scielo.br/oai/scielo-oai.phppublicações@febrasgo.org.br||rbgo@fmrp.usp.br1806-93390100-7203opendoar:2015-09-10T00:00Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)false
dc.title.none.fl_str_mv Herlyn-Werner-Wunderlich syndrome: a case report
title Herlyn-Werner-Wunderlich syndrome: a case report
spellingShingle Herlyn-Werner-Wunderlich syndrome: a case report
Piccinini,Pedro Salomao
Müllerian ducts
Vagina
Uterus
Kidney
title_short Herlyn-Werner-Wunderlich syndrome: a case report
title_full Herlyn-Werner-Wunderlich syndrome: a case report
title_fullStr Herlyn-Werner-Wunderlich syndrome: a case report
title_full_unstemmed Herlyn-Werner-Wunderlich syndrome: a case report
title_sort Herlyn-Werner-Wunderlich syndrome: a case report
author Piccinini,Pedro Salomao
author_facet Piccinini,Pedro Salomao
Doski,John
author_role author
author2 Doski,John
author2_role author
dc.contributor.author.fl_str_mv Piccinini,Pedro Salomao
Doski,John
dc.subject.por.fl_str_mv Müllerian ducts
Vagina
Uterus
Kidney
topic Müllerian ducts
Vagina
Uterus
Kidney
description Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disorder of the Müllerian ducts in which there is uterus didelphys, obstructed hemivagina and unilateral renal agenesis. The most common presentation is an abdominal mass secondary to hematocolpos, pain and dysmenorrhea. However, in some cases, such as the one we present here, menses are normal due to an obstructed hemivagina, and diagnosis can be delayed. We describe evaluation and surgical management of a 13-year-old girl with this condition who was diagnosed by computed tomography (CT) scan and confirmed by pelvic ultrasound and surgical exploration, as well as a review of the literature.
publishDate 2015
dc.date.none.fl_str_mv 2015-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032015000400192
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032015000400192
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/SO100-720320150005077
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Federação Brasileira das Sociedades de Ginecologia e Obstetrícia
publisher.none.fl_str_mv Federação Brasileira das Sociedades de Ginecologia e Obstetrícia
dc.source.none.fl_str_mv Revista Brasileira de Ginecologia e Obstetrícia v.37 n.4 2015
reponame:Revista brasileira de ginecologia e obstetrícia (Online)
instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
instacron:FEBRASGO
instname_str Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
instacron_str FEBRASGO
institution FEBRASGO
reponame_str Revista brasileira de ginecologia e obstetrícia (Online)
collection Revista brasileira de ginecologia e obstetrícia (Online)
repository.name.fl_str_mv Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
repository.mail.fl_str_mv publicações@febrasgo.org.br||rbgo@fmrp.usp.br
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